Ornithine restores ureagenesis capacity and mitigates hyperammonemia in Otcspf-ash mice

Journal of Nutrition

Volumn 136, Issue 7, 2006, Pages 1834-1838

  Marini, Juan C ^a,b   Lee, Brendan ^b   Garlick, Peter J ^a  

^a UNIVERSITY OF ILLINOIS AT URBANA CHAMPAIGN   (United States)

^b BAYLOR COLLEGE OF MEDICINE   (United States)

Author keywords

Glutamine; Ornithine; OTCD; spf ash mouse; Urea cycle disorders

Indexed keywords

ALANINE; AMINO ACID MIXTURE; AMMONIA; GLUTAMINE; GLYCINE; NITROGEN 15; ORNITHINE; ORNITHINE CARBAMOYLTRANSFERASE; UREA;

AMMONIA BLOOD LEVEL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; ENZYME ACTIVITY; GENOTYPE; HEPATOMEGALY; HYPERAMMONEMIA; LIVER WEIGHT; MATHEMATICAL COMPUTING; MOUSE; NITROGEN METABOLISM; NONHUMAN; PROTEIN DEGRADATION; REDUCTION; SUPPLEMENTATION; UREA BLOOD LEVEL; UREA CYCLE;

EID: 33745677465     PISSN: 00223166     EISSN: 15416100     Source Type: Journal    
DOI: 10.1093/jn/136.7.1834     Document Type: Article

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