Reduced ornithine transcarbamylase activity does not impair ureagenesis in Otcspf-ash mice

Journal of Nutrition

Volumn 136, Issue 4, 2006, Pages 1017-1020

  Marini, Juan C ^a   Lee, Brendan ^b   Garlick, Peter J ^a  

^a UNIVERSITY OF ILLINOIS AT URBANA CHAMPAIGN   (United States)

^b BAYLOR COLLEGE OF MEDICINE   (United States)

Author keywords

Mouse models; Ornithine transcarbamylase deficiency; Spf ash mouse; Urea cycle disorders; Urea kinetics

Indexed keywords

ALANINE; AMINO ACID; CARBAMOYLTRANSFERASE; GLUCOSE; GLYCINE; NITROGEN; ORNITHINE; UREA;

ACUTE HEPATITIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BODY WEIGHT; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME DEFICIENCY; GENOTYPE; GLUCOSE BLOOD LEVEL; HYPERAMMONEMIA; IN VIVO STUDY; INFUSION RATE; KINETICS; LIVER WEIGHT; MOUSE; NONHUMAN; STOMACH CONTENT; UREA BLOOD LEVEL; UREA CYCLE;

ANIMALIA;

EID: 33645526443     PISSN: 00223166     EISSN: 15416100     Source Type: Journal    
DOI: 10.1093/jn/136.4.1017     Document Type: Article

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