Aberrations of ammonia metabolism in ornithine carbamoyltransferase-deficient spf-ash mice and their prevention by treatment with urea cycle intermediate amino acids and an ornithine aminotransferase inactivator

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1455, Issue 1, 1999, Pages 1-11

  Li, Meng Xian ^a   Nakajima, Toshihiro ^b   Fukushige, Tomoko ^a   Kobayashi, Keiko ^a   Seiler, Nikolaus ^c   Saheki, Takeyori ^a  

^a KAGOSHIMA UNIVERSITY   (Japan)

^b KYOTO PREFECTURAL UNIVERSITY OF MEDICINE   (Japan)

^c IRCAD   (France)

Author keywords

5 (Fluoromethyl)ornithine; Hyperammonemia; Ornithine aminotransferase; Ornithine carbamoyltransferase; Sparse fur with abnormal skin and hair mouse

Indexed keywords

5 FLUOROMETHYLORNITHINE; AMMONIA; ARGININE; CITRULLINE; ORNITHINE; ORNITHINE CARBAMOYLTRANSFERASE; ORNITHINE OXOACID AMINOTRANSFERASE; UREA;

AMMONIA BLOOD LEVEL; AMMONIA FORMATION; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; ENZYME DEFICIENCY; HYPERAMMONEMIA; MALE; MOUSE; NONHUMAN; PRIORITY JOURNAL;

AMINO ACID METABOLISM, INBORN ERRORS; AMMONIA; AMMONIUM CHLORIDE; ANIMALS; ARGININE; CITRULLINE; ENZYME INHIBITORS; INJECTIONS, INTRAPERITONEAL; LIVER; MALE; MICE; MICE, TRANSGENIC; ORNITHINE; ORNITHINE CARBAMOYLTRANSFERASE; PERFUSION; UREA;

EID: 0032791144     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0925-4439(99)00048-4     Document Type: Article

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