The Fanconi syndrome of cystinosis: Insights into the pathophysiology

Pediatric Nephrology

Volumn 12, Issue 6, 1998, Pages 492-497

  Baum, Michel ^a  

^a UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

Author keywords

Cystine dimethyl ester; Cystine loaded tubule; Intracellular phosphate; Na K ATPase; Proximal tubule

Indexed keywords

ADENOSINE TRIPHOSPHATASE (POTASSIUM SODIUM); ADENOSINE TRIPHOSPHATE; CYSTINE; PHOSPHATE;

ACTIVE TRANSPORT; ARTICLE; CELL LEVEL; CELL MEMBRANE PERMEABILITY; CYSTINOSIS; ENZYME ACTIVITY; FANCONI RENOTUBULAR SYNDROME; HUMAN; KIDNEY PROXIMAL TUBULE; LYSOSOME STORAGE DISEASE; PATHOPHYSIOLOGY; PERMEABILITY; PRIORITY JOURNAL;

CYSTINOSIS; FANCONI SYNDROME; HUMANS; PHOSPHATES;

EID: 0031854963     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004670050495     Document Type: Article

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