Limited rescue of osteoclast-poor osteopetrosis after successful engraftment by cord blood from an unrelated donor

Journal of Bone and Mineral Research

Volumn 20, Issue 12, 2005, Pages 2264-2270

  Nicholls, Brian M ^a   Bredius, Robbert G M ^b   Hamdy, Neveen A T ^b   Gerritsen, Egbert J A ^c   Lankester, Arjan C ^b   Hogendoorn, Pancras C W ^b   Nesbitt, Stephen A ^a   Horton, Michael A ^a   Flanagan, Adrienne M ^a,d  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

^b LEIDEN UNIVERSITY MEDICAL CENTER   (Netherlands)

^c Stichting Oosterschelde Ziekenhuizen   (Netherlands)

^d ROYAL NATIONAL ORTHOPAEDIC HOSPITAL   (United Kingdom)

Author keywords

Bone resorption; Hematopoietic stem cell transplant; Osteoclast; Osteopetrosis

Indexed keywords

BETA3 INTEGRIN; CARBOXY TERMINAL TELOPEPTIDE; COLLAGEN; COLONY STIMULATING FACTOR 1; OSTEOCLAST DIFFERENTIATION FACTOR; VITRONECTIN RECEPTOR;

ALBERS SCHOENBERG DISEASE; ARTICLE; BLOOD DONOR; BONE DEFECT; CASE REPORT; CHILD; ENZYME LINKED IMMUNOSORBENT ASSAY; EXTRAMEDULLARY HEMATOPOIESIS; FEMALE; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HIGH RISK PATIENT; HISTOPATHOLOGY; HUMAN; MICROENVIRONMENT; OSTEOCLAST; OSTEOLYSIS; PERIPHERAL BLOOD MONONUCLEAR CELL; STEM CELL; TISSUE SLICE; UMBILICAL CORD BLOOD;

ACID PHOSPHATASE; ANTIGENS, CD11C; ANTIGENS, CD18; BIOPSY; CARRIER PROTEINS; CARTILAGE; CELL DIFFERENTIATION; CHILD; COLLAGEN; COLLAGEN TYPE I; CORD BLOOD STEM CELL TRANSPLANTATION; DNA MUTATIONAL ANALYSIS; FEMALE; FEMUR; GLYCOPROTEINS; HEMATOLOGIC DISEASES; HUMANS; HUMERUS; INTEGRIN ALPHAVBETA3; ISOENZYMES; LEUKOCYTES, MONONUCLEAR; MACROPHAGE COLONY-STIMULATING FACTOR; MEMBRANE GLYCOPROTEINS; OSTEOCLASTS; OSTEOPETROSIS; OSTEOPROTEGERIN; PEPTIDES; RANK LIGAND; RECEPTOR ACTIVATOR OF NUCLEAR FACTOR-KAPPA B; RECEPTORS, CYTOPLASMIC AND NUCLEAR; RECEPTORS, TUMOR NECROSIS FACTOR; TRANSPLANTATION, HOMOLOGOUS; TREATMENT OUTCOME;

EID: 28144449934     PISSN: 08840431     EISSN: None     Source Type: Journal    
DOI: 10.1359/JBMR.050807     Document Type: Article

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