Molecular basis of cholestatic diseases of surgical interest

Seminars in Pediatric Surgery

Volumn 14, Issue 4, 2005, Pages 200-205

  Alvarez, Luis ^a,b   Jara, Paloma ^a   Hierro, Loreto ^a   Sánchez Sabaté, Elena ^a   Martínez Fernández, Pilar ^a   López Santamaría, Manuel ^a  

^a HOSPITAL INFANTIL LA PAZ   (Spain)

^b HOSPITAL UNIVERSITARIO LA PAZ   (Spain)

Author keywords

Alagille syndrome; Biliary atresia; JAG1; Progressive familial intrahepatic cholestasis

Indexed keywords

FARNESOID X RECEPTOR; GAMMA INTERFERON; INTERLEUKIN 2; JAGGED1; NOTCH RECEPTOR; PROTEIN; PROTEIN ABCB11; TUMOR NECROSIS FACTOR ALPHA; UNCLASSIFIED DRUG; URSODEOXYCHOLIC ACID;

ALAGILLE SYNDROME; ASPLENIA; BILE DUCT ATRESIA; BILE SALT EXPORT PUMP DISEASE; BILIARY ATRESIA SPLENIC MALFORMATION SYNDROME; BILIARY TRACT DRAINAGE; BILIARY TRACT SURGERY; CHOLESTASIS; CONGENITAL MALFORMATION; DRUG TARGETING; GENE MUTATION; HUMAN; INTRAHEPATIC CHOLESTASIS; LIVER FIBROSIS; LIVER TRANSPLANTATION; PEDIATRIC SURGERY; PHENOTYPE; PORTOENTEROSTOMY; PRIORITY JOURNAL; PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS; REVIEW; SIGNAL TRANSDUCTION;

EID: 26644452988     PISSN: 10558586     EISSN: None     Source Type: Journal    
DOI: 10.1053/j.sempedsurg.2005.06.002     Document Type: Article

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