Surgical Treatment of Progressive Familial Intrahepatic Cholestasis: Comparison of Partial External Biliary Diversion and Ileal Bypass

European Journal of Pediatric Surgery

Volumn 13, Issue 5, 2003, Pages 307-311

  Kaliciński, Piotr J ^a   Ismail, H ^a   Jankowska, I ^a   Kaminski A ^a   Pawlowska J ^a   Drewniak, T ^a   Markiewicz, M ^a   Szymczak, M ^a  

^a CHILDREN'S MEMORIAL HEALTH INSTITUTE   (Poland)

Author keywords

Biliary diversion; Byler's disease; Progressive familial intrahepatic cholestasis; Surgical treatment

Indexed keywords

BILE ACID;

ARTICLE; BIOCHEMISTRY; CHILD; CLINICAL ARTICLE; COMPARATIVE STUDY; CONTROLLED STUDY; FEMALE; FOLLOW UP; HUMAN; ILEUM BYPASS; INTRAHEPATIC CHOLESTASIS; LIVER FUNCTION TEST; MALE; MEDICAL ASSESSMENT; PARTIAL EXTERNAL BILIARY DIVERSION; STATISTICAL SIGNIFICANCE; SURGICAL TECHNIQUE; SURVIVAL RATE; SYMPTOM; TRANSPLANTATION; TREATMENT OUTCOME;

ADOLESCENT; BILIARY TRACT SURGICAL PROCEDURES; CHILD; CHILD, PRESCHOOL; CHOLESTASIS, INTRAHEPATIC; FEMALE; FOLLOW-UP STUDIES; HUMANS; INFANT; MALE; TREATMENT OUTCOME;

EID: 0344876490     PISSN: 09397248     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2003-43570     Document Type: Article

References (17)

1. Alonso EM, Snover DC, Montag A, Freese D, Whitington PF. Histologic pathology of the liver in progressive familial intrahepatic cholestasis. J Pediatr Gastroenterol Nutr 1994; 18: 128-133
2. Chorbert MN, Bernard O, Bulle F, Lemonnier A, Guellaen G, Alagille D. High hepatic gamma-glutamyl-transferase (GGTP) activity with normal serum GGTP in children with progressive idiopathic cholestasis. J Hepatol 1989; 8: 22-25
3. Clayton RJ, Iber FL, Ruchner BH, McKusick VA. Byler's disease: Fatal familial intrahepatic cholestasis in an Amish kindred. J Pediatr 1965; 67: 1025-1028 (abstract)
4. Clayton RJ, Iber FL, Ruchner BH, McKusick VA. Byler's disease - fatal intrahepatic cholestasis in an Amish kindred. Amer J Dis Child 1969; 117: 112-124
5. Emond JC, Whitington PF. Selective surgical management of progressive familial intrahepatic cholestasis (Byler's disease). J Pediatr Surg 1995; 30: 1635-1641
6. Hollands CM, Rivera-Pedrogo FJ, Gonzalez-Vallina R, Loret-de-Mola O, Nahmad M, Burnweit CA. Ileal exclusion for Byler's disease: an alternative surgical approach with promising early results for pruritus. J Pediatr Surg 1998; 33: 220-224
7. Ismail H, Kaliciński P, Markiewicz M, Jankowska I, Pawłowska J, Kaminski A, Szymczak M, Drewniak T. Treatment of progressive familial intrahepatic cholestasis in children. Liver transplantation or partial external biliary diversion? Pediatric Transpl 1999; 3: 219-224
8. Jacquemin E, Dumont M, Bernard O et al. Evidence for defective primary bile acid secretion in children with progressive familial intrahepatic cholestasis (Byler's disease). Eur J Pediatr 1994; 153: 424-428
9. Jacquemin E, Hermans D, Myara A, Habes D, Debray D, Handchouel M, Sokal EM, Bernard O. Ursodeoxycholic acid therapy in pediatric patients with progressive familial intrahepatic cholestasis. Hepatology 1997; 25: 519
10. Knisley AS et al. Pancreatic dysfunction in Byler's disease. J Pediatr Gastroenterol Nutr (NASPGN abstracts) 1995; 21: 3
11. Lee H, Vacanti J. Liver transplantation and its long term management in children. Pediatr Clin N Amer 1996; 43: 99-124
12. Maggiore G, Bernard O, Handchouel M, Lemonnier A, Alagille D. Diagnostic value of serum gamma-glutamyl transpeptidase activity in liver diseases in children. J Pediatr Gastroenterol Nutr 1991; 12: 1-21
13. Maggiore G, Bernard O, Riely C et al. Normal serum g-glutamyl-transpeptidase activity identifies groups of infants with idiopathic cholestasis with poor diagnosis. J Pediatr 1987; 111: 251-252
14. Siebert JR. Small-intestine length in infants and children. Am J Dis Childh 1980; 134: 593-595
15. Soubrane O, Gauthier F, DeVictor D, Bernard O, Valayer J, Houssin D, Chapnis Y. Orthotopic liver transplantation for Byler's disease. Transplantation 1990; 50: 804-806
16. Whitington PF. Chronic cholestasis of infancy. Pediatr Clin N Amer 1996; 43: 1-25
17. Whitington PF, Whitington GL. Partial external diversion of bile for the treatment of intractable pruritus associated with intrahepatic cholestasis. Gastroenterology 1988; 95: 130-136