Cholesterol accumulation and liver cell death in mice with Niemann-Pick type C disease

Hepatology

Volumn 42, Issue 4, 2005, Pages 886-893

  Beltroy, Eduardo P ^a   Richardson, James A ^a   Horton, Jay D ^a   Turley, Stephen D ^a   Dietschy, John M ^a,b  

^a UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

^b UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALKALINE PHOSPHATASE; BILE ACID; CASPASE 6; CHOLESTEROL; COLLAGEN; GLYCOGEN; INTERLEUKIN 1BETA CONVERTING ENZYME; MESSENGER RNA; STEROL;

ALKALINE PHOSPHATASE BLOOD LEVEL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BILE ACID SYNTHESIS; CELL DEATH; CELL INCLUSION; CHOLESTEROL TRANSPORT; CONTROLLED STUDY; CYTOSOL; ENDOSOME; FAT CONTENT; GENE; GENE EXPRESSION; GENE MUTATION; HEPATOMEGALY; HISTOPATHOLOGY; LIPID STORAGE; LIVER CELL; LIVER DYSFUNCTION; LYSOSOME; MACROPHAGE; MOUSE; NERVE DEGENERATION; NIEMANN PICK DISEASE; NONHUMAN; NPC1 GENE; PRIORITY JOURNAL; STEROL SYNTHESIS;

ALANINE TRANSAMINASE; ANIMALS; ASPARTATE AMINOTRANSFERASES; BRAIN; CASPASE 1; CASPASE 6; CASPASES; CHOLESTEROL; DIETARY FATS; DISEASE MODELS, ANIMAL; FEMALE; LIVER; MALE; MICE; MICE, INBRED BALB C; MICE, MUTANT STRAINS; NIEMANN-PICK DISEASES; ORGAN SIZE; PROTEINS; RNA, MESSENGER; TUMOR NECROSIS FACTOR-ALPHA;

EID: 25844483845     PISSN: 02709139     EISSN: None     Source Type: Journal    
DOI: 10.1002/hep.20868     Document Type: Article

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