Sulfite and base for the treatment of familial amyloidotic polyneuropathy: Two additive approaches to stabilize the conformation of human amyloidogenic transthyretin

Neurogenetics

Volumn 5, Issue 1, 2004, Pages 61-67

  Altland, Klaus ^a   Winter, Pia ^a   Saraiva, Maria Joao M ^b   Suhr, Ole ^c  

^a JUSTUS LIEBIG UNIVERSITY   (Germany)

^b UNIVERSITY OF PORTO   (Portugal)

^c UMEÅ UNIVERSITY HOSPITAL   (Sweden)

Author keywords

Acidosis; Familial amyloidotic polyneuropathy; Sulfite; Transthyretin

Indexed keywords

BASE; DIMER; DODECYL SULFATE SODIUM; MONOMER; PREALBUMIN; SULFITE;

ACIDIFICATION; ACIDITY; ARTICLE; CONTROLLED STUDY; DISEASE COURSE; DRUG EFFECT; DRUG MECHANISM; DRUG POTENTIATION; FAMILIAL AMYLOID POLYNEUROPATHY; HOMOZYGOSITY; HUMAN; MUTATION; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRIORITY JOURNAL; PROTEIN CONFORMATION; PROTEIN STABILITY; RISK; SULFONATION;

ACIDOSIS; ALKALIES; AMYLOID NEUROPATHIES, FAMILIAL; BLOOD PROTEIN ELECTROPHORESIS; DIMERIZATION; HUMANS; HYDROGEN-ION CONCENTRATION; PREALBUMIN; PROTEIN CONFORMATION; SULFITES;

EID: 1542320018     PISSN: 13646745     EISSN: None     Source Type: Journal    
DOI: 10.1007/s10048-003-0160-1     Document Type: Article

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