Neuromuscular accumulation of mutant superoxide dismutase 1 aggregates in a transgenic mouse model of familial amyotrophic lateral sclerosis

Neuroscience Letters

Volumn 350, Issue 2, 2003, Pages 132-136

  Turner, Bradley J ^a,b   Lopes, Elizabeth C ^a,b   Cheema, Surindar S ^a,b  

^a UNIVERSITY OF MELBOURNE   (Australia)

^b MONASH UNIVERSITY   (Australia)

Author keywords

Aggregates; Familial amyotrophic lateral sclerosis; Muscle; Oligomers; Spinal cord; Superoxide dismutase 1

Indexed keywords

DIMER; MONOMER; MUTANT PROTEIN; SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN STEM; CERVICAL SPINAL CORD; CONTROLLED STUDY; DIAPHRAGM MUSCLE; DISEASE COURSE; FAMILIAL DISEASE; GASTROCNEMIUS MUSCLE; IMMUNOBLOTTING; LUMBAR SPINAL CORD; MODEL; MOLECULAR WEIGHT; MOUSE; MUSCLE TISSUE; NERVOUS TISSUE; NEUROMUSCULAR SYSTEM; NONHUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN ANALYSIS; PROTEIN DETERMINATION; PROTEIN STABILITY; SCIATIC NERVE; TRANSGENIC MOUSE; VISCERA; ZYMOGRAPHY;

EID: 0042827316     PISSN: 03043940     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0304-3940(03)00893-0     Document Type: Article

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