Decreased thermodynamic stability as a crucial factor for familial amyloidotic polyneuropathy

Journal of Molecular Biology

Volumn 320, Issue 2, 2002, Pages 333-342

  Niraula, Tara Nath ^a   Haraoka, Katsuki ^b   Ando, Yukio ^b   Li, Hua ^a   Yamada, Hiroaki ^a   Akasaka, Kazuyuki ^a  

^a KOBE UNIVERSITY   (Japan)

^b KUMAMOTO UNIVERSITY   (Japan)

Author keywords

Familial amyloidotic polyneuropathy; High pressure NMR; Thermodynamic stability; Transthyretin; Unfolded monomer

Indexed keywords

MONOMER; PREALBUMIN; TETRAMER;

AMYLOID NEUROPATHY; ARTICLE; CONTROLLED STUDY; CRYSTAL STRUCTURE; DIFFUSION; DISSOCIATION; FAMILIAL AMYLOID POLYNEUROPATHY; HUMAN; PH; PRESSURE; PRIORITY JOURNAL; PROTEIN FOLDING; PROTEIN STABILITY; PROTEIN STRUCTURE; PROTON NUCLEAR MAGNETIC RESONANCE; THERMODYNAMICS; THERMOSTABILITY;

EID: 0036295569     PISSN: 00222836     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0022-2836(02)00425-4     Document Type: Article

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