The survival of motor neurons (SMN) protein interacts with the snoRNP proteins fibrillarin and GAR1

Current Biology

Volumn 11, Issue 14, 2001, Pages 1079-1088

  Pellizzoni, Livio ^a   Baccon, Jennifer ^a   Charroux, Bernard ^a   Dreyfuss, Gideon ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MAMMALIA;

EID: 0035943003     PISSN: 09609822     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0960-9822(01)00316-5     Document Type: Article

References (57)

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8. A mouse model for spinal muscular atrophy
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10. A novel nuclear structure containing the survival of motor neurons protein
11. The spinal muscular atrophy disease gene product, SMN, and its associated protein SIP1 are in a complex with spliceosomal snRNP proteins
12. Gemin3, a novel DEAD box protein that interacts with SMN, the spinal muscular atrophy gene product, and is a component of gems
13. Gemin4: A novel component of the SMN complex that is found in both gems and nucleoli
14. The SMN-SIP1 complex has an essential role in spliceosomal snRNP biogenesis
15. A novel function for SMN, the spinal muscular atrophy disease gene product, in pre-mRNA splicing
16. Essential role for the tudor domain of SMN in spliceosomal U snRNP assembly: Implications for spinal muscular atrophy
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18. A functional interaction between the survival motor neuron complex and RNA polymerase II
19. SMN oligomerization defect correlates with spinal muscular atrophy severity
20. SMN mutants of spinal muscular atrophy patients are defective in binding to snRNP proteins
21. Specific sequences of the Sm and Sm-like (Lsm) proteins mediate their interaction with the spinal muscular atrophy disease gene product (SMN)
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25. The RNA world of the nucleolus: Two major families of small RNAs defined by different box elements with related functions
26. The small nucleolar RNP protein NOP1 (fibrillarin) is required for pre-rRNA processing in yeast
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34. U3, U8 and U13 comprise a new class of mammalian snRNPs localized in the cell nucleolus
35. GAR1 is an essential small nucleolar RNP protein required for pre-rRNA processing in yeast
36. In vitro assembly of human H/ACA small nucleolar RNPs reveals unique features of U17 and telomerase RNAs
37. Gar1p binds to the small nucleolar RNAs snR10 and snR30 in vitro through a nontypical RNA binding element
38. Fibrillarin binds directly and specifically to U16 box C/D snoRNA
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40. The domain encoded by exon 2 of the survival motor neuron protein mediates nucleic acid binding
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44. Human H/ACA small nucleolar RNPs and telomerase share evolutionarily conserved proteins NHP2 and NOP10
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51. The small nucleolar RNAs
52. The snoRNA box CID motif directs nucleolar targeting and also couples snoRNA synthesis and localization
53. Newly assembled snRNPs associate with coiled bodies before speckles, suggesting a nuclear snRNP maturation pathway
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55. High mobility of proteins in the mammalian cell nucleus
56. Monoclonal autoantibody from a (New Zealand black × New Zealand white) F1 mouse and some human scleroderma sera target an Mr 34,000 nucleolar protein of the U3 RNP particle
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