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Volumn 44, Issue , 2001, Pages 225-231

18. Targeting the hexosaminidase genes: Mouse models of the GM2 gangliosidoses

Author keywords

[No Author keywords available]

Indexed keywords

BETA N ACETYLHEXOSAMINIDASE;

EID: 0035225852     PISSN: 00652660     EISSN: None     Source Type: Book Series    
DOI: 10.1016/s0065-2660(01)44082-x     Document Type: Article
Times cited : (3)

References (15)
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    • The GM2 gangliosidoses
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    • Gravel, R.A.1    Clarke, J.T.R.2    Kaback, M.M.3    Mahuran, D.4    Sandhoff, K.5    Suzuki, K.6
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    • 0033060380 scopus 로고    scopus 로고
    • Delayed symptom onset and increased life expectancy in Sandhoff disease mice treated with N-butyldeoxynojirimycin
    • M. Jeyakumar T.D. Butters M. Cortina-Borja V. Hunnam R.L. Proia H.V. Perry R.A. Dwek F.M. Platt Delayed symptom onset and increased life expectancy in Sandhoff disease mice treated with N-butyldeoxynojirimycin Proc. Natl. Acad. Sci. U.S.A. 96 1999 6388 6393
    • (1999) , pp. 6388-6393
    • Jeyakumar, M.1    Butters, T.D.2    Cortina-Borja, M.3    Hunnam, V.4    Proia, R.L.5    Perry, H.V.6    Dwek, R.A.7    Platt, F.M.8
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    • M. Jeyakumar F. Norflus C.J. Tifft M. Cortina-Borja T.D. Butters R.L. Proia V.H. Perry R. Dwek F.M. Platt Enhanced survival in Sandhoff disease mice receiving a combination of substrate deprivation therapy and bone marrow transplantation Blood 97 2001 327 329
    • (2001) Blood , vol.97 , pp. 327-329
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  • 6
    • 0026689409 scopus 로고
    • Altering genes in animals by gene targeting
    • B.H. Koller O. Smithies Altering genes in animals by gene targeting Annu. Rev. Immunol. 10 1992 705 730
    • (1992) Annu. Rev. Immunol. , vol.10 , pp. 705-730
    • Koller, B.H.1    Smithies, O.2
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    • The mucopolysaccharidoses
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    • (1998) , pp. 1883-1887
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* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.