Absence of ventral cell populations in the developing brain in a rat model of the Smith-Lemli-Opitz syndrome

American Journal of Medical Genetics

Volumn 87, Issue 3, 1999, Pages 207-216

  Gofflot, Françoise ^a   Kolf Clauw, Martine ^b,c   Clotman, Frederic ^a,d   Roux, Charles ^b   Picard, Jacques J ^a  

^a UNIVERSITÉ CATHOLIQUE DE LOUVAIN   (Belgium)

^b HÔPITAL SAINT ANTOINE   (France)

^c ECOLE NATIONALE VÉTÉRINAIRE D ALFORT   (France)

^d DEPARTMENT OF PLANT SYSTEMS BIOLOGY   (Belgium)

Author keywords

Cholesterol; Holoprosencephaly; Otx2; Pax6; Shh

Indexed keywords

1,4 BIS(2 CHLOROBENZYLAMINOMETHYL)CYCLOHEXANE; 4 [2 [1 (4 CHLOROCINNAMYL) 4 PIPERAZINYL]ETHYL]BENZOIC ACID; 7 DEHYDROCHOLESTEROL; OXIDOREDUCTASE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BRAIN DEVELOPMENT; CELL POPULATION; CENTRAL NERVOUS SYSTEM MALFORMATION; CHOLESTEROL SYNTHESIS; CONTROLLED STUDY; CRANIOFACIAL MALFORMATION; EMBRYO; GENE EXPRESSION; GENE FUNCTION; HOLOPROSENCEPHALY; NONHUMAN; PRIORITY JOURNAL; RAT; SMITH LEMLI OPITZ SYNDROME; VENTRAL ROOT;

ANIMALS; BRAIN; CHOLESTEROL; DISEASE MODELS, ANIMAL; DNA-BINDING PROTEINS; EMBRYONIC AND FETAL DEVELOPMENT; ENZYME INHIBITORS; EYE PROTEINS; FEMALE; FETAL DISEASES; FETAL PROTEINS; GESTATIONAL AGE; HEDGEHOG PROTEINS; HOMEODOMAIN PROTEINS; IN SITU HYBRIDIZATION; MALE; NERVE TISSUE PROTEINS; NEURAL TUBE DEFECTS; NEURONS; OTX TRANSCRIPTION FACTORS; OXIDOREDUCTASES; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS; PAIRED BOX TRANSCRIPTION FACTORS; PREGNANCY; PROSENCEPHALON; PROTEIN BIOSYNTHESIS; PROTEINS; RATS; RATS, WISTAR; REPRESSOR PROTEINS; RHOMBENCEPHALON; SIGNAL TRANSDUCTION; SMITH-LEMLI-OPITZ SYNDROME; TRANS-1,4-BIS(2-CHLOROBENZAMINOMETHYL)CYCLOHEXANE DIHYDROCHLORIDE; TRANS-ACTIVATORS;

ANIMALIA; ERINACEIDAE;

EID: 0033607623     PISSN: 01487299     EISSN: None     Source Type: Journal    
DOI: 10.1002/(SICI)1096-8628(19991126)87:3<207::AID-AJMG3>3.0.CO;2-5     Document Type: Article

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