Cystic fibrosis: Channel, catalytic, and folding properties of the CFTR protein

Journal of Bioenergetics and Biomembranes

Volumn 29, Issue 5, 1997, Pages 429-442

  Seibert, Fabian S ^b   Loo, Tip W ^b   Clarke, David M ^b   Riordan, John R ^a  

^a MAYO CLINIC COLLEGE OF MEDICINE   (United States)

^b UNIVERSITY OF TORONTO   (Canada)

Author keywords

CFTR; Chloride channel; Cystic fibrosis; ER quality control; Phosphorylation ATPase; Proteasome; Protein folding; Proteolysis

Indexed keywords

TRANSMEMBRANE CONDUCTANCE REGULATOR;

CHANNEL GATING; CYSTIC FIBROSIS; ENDOPLASMIC RETICULUM; HUMAN; PATHOPHYSIOLOGY; PROTEIN FOLDING; PROTEIN TRANSPORT; SHORT SURVEY;

CATALYSIS; CHLORIDE CHANNELS; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; HUMANS; PROTEIN FOLDING;

EID: 0031417142     PISSN: 0145479X     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1022478822214     Document Type: Short Survey

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