Partial restoration of cAMP-stimulated CFTR chloride channel activity in ΔF508 cells by deoxyspergualin

American Journal of Physiology - Cell Physiology

Volumn 275, Issue 1 44-1, 1998, Pages

  Jiang, Canwen ^a   Fang, Shaona L ^a   Xiao, Yong Fu ^b   O'Connor, Sean P ^a   Nadler, Steven G ^c   Lee, Des W ^d   Jefferson, Douglas M ^d   Kaplan, Johanne M ^a   Smith, Alan E ^a   Cheng, Seng H ^a  

^a GENZYME CORPORATION   (United States)

^b HARVARD MEDICAL SCHOOL   (United States)

^c BRISTOL MYERS SQUIBB   (United States)

^d TUFTS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

6 methoxy N (3 sulfopropyl)quinolinium fluorescence; Cellular chaperones; Cystic fibrosis; Whole cell patch clamp

Indexed keywords

15 DEOXYSPERGUALIN; 6 METHOXY N (3 SULFOPROPYL)QUINOLIUM; CALNEXIN; CHAPERONE; CHLORIDE CHANNEL; CYCLIC AMP; HEAT SHOCK PROTEIN 70; TRANSMEMBRANE CONDUCTANCE REGULATOR; UNCLASSIFIED DRUG;

ARTICLE; CELL MEMBRANE; CYSTIC FIBROSIS; ENDOPLASMIC RETICULUM; GENE MUTATION; HUMAN; HUMAN CELL; PATCH CLAMP; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN TRANSPORT;

EID: 0031853136     PISSN: 03636143     EISSN: None     Source Type: Journal    
DOI: 10.1152/ajpcell.1998.275.1.c171     Document Type: Article

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