Neurofilaments and orthograde transport are reduced in ventral root axons of transgenic mice that express human SOD1 with a G93A mutation

Journal of Cell Biology

Volumn 139, Issue 5, 1997, Pages 1307-1315

  Zhang, Bin ^a   Tu, Pang Hsien ^a   Abtahian, Farhad ^a   Trojanowski, John Q ^a   Lee, Virginia M Y ^a,b  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b HOSPITAL OF THE UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALANINE; COPPER ZINC SUPEROXIDE DISMUTASE; GLYCINE;

AMINO ACID SUBSTITUTION; AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL INCLUSION; CELL VACUOLE; CONTROLLED STUDY; GENE EXPRESSION; GENE MUTATION; GENETIC ENGINEERING; GOLGI COMPLEX; MOTOR NEURON DISEASE; MUSCLE WEAKNESS; NERVE FIBER TRANSPORT; NEUROFILAMENT; NONHUMAN; PRIORITY JOURNAL; SPINAL CORD MOTONEURON; TRANSGENIC MOUSE; VENTRAL ROOT;

AGE OF ONSET; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; AXONAL TRANSPORT; AXONS; BIOLOGICAL TRANSPORT; CYTOSKELETAL PROTEINS; DISEASE MODELS, ANIMAL; GENE DOSAGE; HUMANS; INTERMEDIATE FILAMENTS; MICE; MICE, TRANSGENIC; MOTOR NEURON DISEASE; MUTATION; SPINAL CORD; SPINAL NERVE ROOTS; SUPEROXIDE DISMUTASE;

ANIMALIA; MUS MUSCULUS;

EID: 0030817291     PISSN: 00219525     EISSN: None     Source Type: Journal    
DOI: 10.1083/jcb.139.5.1307     Document Type: Article

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