Neuropathology in respiratory-related motoneurons in young Pompe (Gaa−/−) mice

Respiratory Physiology and Neurobiology

Volumn 227, Issue , 2016, Pages 48-55

  Turner, Sara M F ^a   Hoyt, Aaron K ^a   ElMallah, Mai K ^b   Falk, Darin J ^a,b   Byrne, Barry J ^a,b   Fuller, David D ^a  

^a UNIVERSITY OF FLORIDA   (United States)

^b UNIVERSITY OF FLORIDA COLLEGE OF MEDICINE   (United States)

Author keywords

Glycogen; Hypoglossal; Intercostal; Lysosomal storage disease; Neurodegeneration; Phrenic

Indexed keywords

ALPHA GLUCOSIDASE; CASPASE 3; GLIAL FIBRILLARY ACIDIC PROTEIN; IONIZED CALCIUM BINDING ADAPTOR MOLECULE 1; PROTEIN; UNCLASSIFIED DRUG; ACTIN BINDING PROTEIN; AIF1 PROTEIN, MOUSE; CALCIUM BINDING PROTEIN; CASP3 PROTEIN, MOUSE; GLIAL FIBRILLARY ASTROCYTIC PROTEIN, MOUSE; GLYCOGEN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CERVICAL SPINAL CORD; DNA DAMAGE; GLYCOGEN STORAGE DISEASE TYPE 2; IMMUNOREACTIVITY; MOTONEURON; MOUSE; NERVE DEGENERATION; NEUROPATHOLOGY; NONHUMAN; PERIODIC ACID SCHIFF STAIN; PRIORITY JOURNAL; PROTEIN CLEAVAGE; RESPIRATORY TRACT DISEASE; SOLITARY TRACT NUCLEUS; SPINAL CORD DORSAL HORN; TUNEL ASSAY; 129 MOUSE; ANIMAL; APOPTOSIS; CERVICAL VERTEBRA; COHORT ANALYSIS; DISEASE MODEL; IMMUNOMODULATION; KNOCKOUT MOUSE; MEDULLA OBLONGATA; METABOLISM; PATHOLOGY; SPINAL CORD; THORACIC VERTEBRA;

ANIMALS; APOPTOSIS; CALCIUM-BINDING PROTEINS; CASPASE 3; CERVICAL VERTEBRAE; COHORT STUDIES; DISEASE MODELS, ANIMAL; DNA DAMAGE; GLIAL FIBRILLARY ACIDIC PROTEIN; GLYCOGEN; GLYCOGEN STORAGE DISEASE TYPE II; MEDULLA OBLONGATA; MICE, 129 STRAIN; MICE, KNOCKOUT; MICROFILAMENT PROTEINS; MOTOR NEURONS; NEUROIMMUNOMODULATION; SPINAL CORD; THORACIC VERTEBRAE;

EID: 85013702147     PISSN: 15699048     EISSN: 18781519     Source Type: Journal    
DOI: 10.1016/j.resp.2016.02.007     Document Type: Article

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