-
1
-
-
67650712233
-
Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening
-
Sly PD, Brennan S, Gangell C, de Klerk N, Murray C, Mott L, Stick SM, Robinson PJ, Robertson CF, Ranganathan SC; Australian Respiratory Early Surveillance Team for Cystic Fibrosis (AREST-CF). Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening. Am J Respir Crit Care Med 2009;180:146-152.
-
(2009)
Am J Respir Crit Care Med
, vol.180
, pp. 146-152
-
-
Australian Respiratory Early Surveillance Team for Cystic Fibrosis (AREST-CF)1
Sly, P.D.2
Brennan, S.3
Gangell, C.4
De Klerk, N.5
Murray, C.6
Mott, L.7
Stick, S.M.8
Robinson, P.J.9
Robertson, C.F.10
Ranganathan, S.C.11
-
2
-
-
79958142002
-
The ENaC-overexpressing mouse as a model of cystic fibrosis lung disease
-
Zhou Z, Duerr J, Johannesson B, Schubert SC, Treis D, Harm M, Graeber SY, Dalpke A, Schultz C, Mall MA. The ENaC-overexpressing mouse as a model of cystic fibrosis lung disease. J Cyst Fibros 2011; 10:S172-S182.
-
(2011)
J Cyst Fibros
, vol.10
, pp. S172-S182
-
-
Zhou, Z.1
Duerr, J.2
Johannesson, B.3
Schubert, S.C.4
Treis, D.5
Harm, M.6
Graeber, S.Y.7
Dalpke, A.8
Schultz, C.9
Mall, M.A.10
-
3
-
-
84927792201
-
Hypoxic epithelial necrosis triggers neutrophilic inflammation via IL-1 receptor signaling in cystic fibrosis lung disease
-
Fritzsching B, Zhou-Suckow Z, Trojanek JB, Schubert SC, Schatterny J, Hirtz S, Agrawal R, Muley T, Kahn N, Sticht C, et al. Hypoxic epithelial necrosis triggers neutrophilic inflammation via IL-1 receptor signaling in cystic fibrosis lung disease. Am J Respir Crit Care Med 2015;191: 902-913.
-
(2015)
Am J Respir Crit Care Med
, vol.191
, pp. 902-913
-
-
Fritzsching, B.1
Zhou-Suckow, Z.2
Trojanek, J.B.3
Schubert, S.C.4
Schatterny, J.5
Hirtz, S.6
Agrawal, R.7
Muley, T.8
Kahn, N.9
Sticht, C.10
-
4
-
-
84905992903
-
A neutrophil intrinsic impairment affecting Rab27a and degranulation in cystic fibrosis is corrected by CFTR potentiator therapy
-
Pohl K, Hayes E, Keenan J, Henry M, Meleady P, Molloy K, Jundi B, Bergin DA, McCarthy C, McElvaney OJ, et al. A neutrophil intrinsic impairment affecting Rab27a and degranulation in cystic fibrosis is corrected by CFTR potentiator therapy. Blood 2014;124: 999-1009.
-
(2014)
Blood
, vol.124
, pp. 999-1009
-
-
Pohl, K.1
Hayes, E.2
Keenan, J.3
Henry, M.4
Meleady, P.5
Molloy, K.6
Jundi, B.7
Bergin, D.A.8
McCarthy, C.9
McElvaney, O.J.10
-
5
-
-
84884736892
-
Impaired functions of macrophage from cystic fibrosis patients: CD11b, TLR-5 decrease and sCD14, inflammatory cytokines increase
-
Simonin-Le Jeune K, Le Jeune A, Jouneau S, Belleguic C, Roux PF, Jaguin M, Dimanche-Boitre MT, Lecureur V, Leclercq C, Desrues B, et al. Impaired functions of macrophage from cystic fibrosis patients: CD11b, TLR-5 decrease and sCD14, inflammatory cytokines increase. PLoS One 2013;8:e75667.
-
(2013)
PLoS One
, vol.8
, pp. e75667
-
-
Simonin-Le Jeune, K.1
Le Jeune, A.2
Jouneau, S.3
Belleguic, C.4
Roux, P.F.5
Jaguin, M.6
Dimanche-Boitre, M.T.7
Lecureur, V.8
Leclercq, C.9
Desrues, B.10
-
6
-
-
0030768159
-
Lower airway inflammation in infants and young children with cystic fibrosis
-
Armstrong DS, Grimwood K, Carlin JB, Carzino R, Gutiè rrez JP, Hull J, Olinsky A, Phelan EM, Robertson CF, Phelan PD. Lower airway inflammation in infants and young children with cystic fibrosis. Am J Respir Crit Care Med 1997;156:1197-1204.
-
(1997)
Am J Respir Crit Care Med
, vol.156
, pp. 1197-1204
-
-
Armstrong, D.S.1
Grimwood, K.2
Carlin, J.B.3
Carzino, R.4
Gutièrrez, J.P.5
Hull, J.6
Olinsky, A.7
Phelan, E.M.8
Robertson, C.F.9
Phelan, P.D.10
-
7
-
-
84878000440
-
Risk factors for bronchiectasis in children with cystic fibrosis
-
Sly PD, Gangell CL, Chen L, Ware RS, Ranganathan S, Mott LS, Murray CP, Stick SM; AREST CF Investigators. Risk factors for bronchiectasis in children with cystic fibrosis. N Engl J Med 2013;368:1963-1970.
-
(2013)
N Engl J Med
, vol.368
, pp. 1963-1970
-
-
AREST CF Investigators1
Sly, P.D.2
Gangell, C.L.3
Chen, L.4
Ware, R.S.5
Ranganathan, S.6
Mott, L.S.7
Murray, C.P.8
Stick, S.M.9
-
8
-
-
84992436652
-
Newborn cystic fibrosis pigs have a blunted early response to an inflammatory stimulus
-
Bartlett JA, Ramachandran S, Wohlford-Lenane CL, Barker CK, Pezzulo AA, Zabner J, Welsh MJ, Meyerholz DK, Stoltz DA, McCray PB Jr. Newborn cystic fibrosis pigs have a blunted early response to an inflammatory stimulus. Am J Respir Crit Care Med 2016;194: 845-854.
-
(2016)
Am J Respir Crit Care Med
, vol.194
, pp. 845-854
-
-
Bartlett, J.A.1
Ramachandran, S.2
Wohlford-Lenane, C.L.3
Barker, C.K.4
Pezzulo, A.A.5
Zabner, J.6
Welsh, M.J.7
Meyerholz, D.K.8
Stoltz, D.A.9
McCray, P.B.10
-
9
-
-
48949101838
-
Inflammatory responses to specific pathogens in the lungs of children with cystic fibrosis
-
Gard S, Brennan S, Winfield K, Sturges N, Gangell C, Sly P. Inflammatory responses to specific pathogens in the lungs of children with cystic fibrosis. Respirology 2007;12:22.
-
(2007)
Respirology
, vol.12
, pp. 22
-
-
Gard, S.1
Brennan, S.2
Winfield, K.3
Sturges, N.4
Gangell, C.5
Sly, P.6
-
10
-
-
84923930953
-
Early respiratory infection is associated with reduced spirometry in children with cystic fibrosis
-
Ramsey KA, Ranganathan S, Park J, Skoric B, Adams AM, Simpson SJ, Robins-Browne RM, Franklin PJ, de Klerk NH, Sly PD, et al.; AREST CF. Early respiratory infection is associated with reduced spirometry in children with cystic fibrosis. Am J Respir Crit Care Med 2014;190:1111-1116.
-
(2014)
Am J Respir Crit Care Med
, vol.190
, pp. 1111-1116
-
-
AREST CF1
Ramsey, K.A.2
Ranganathan, S.3
Park, J.4
Skoric, B.5
Adams, A.M.6
Simpson, S.J.7
Robins-Browne, R.M.8
Franklin, P.J.9
De Klerk, N.H.10
Sly, P.D.11
-
11
-
-
84948971137
-
Progressive ventilation inhomogeneity in infants with cystic fibrosis after pulmonary infection
-
Simpson SJ, Ranganathan S, Park J, Turkovic L, Robins-Browne RM, Skoric B, et al. Progressive ventilation inhomogeneity in infants with cystic fibrosis after pulmonary infection. Eur Respir J 2015;46:1680-1690.
-
(2015)
Eur Respir J
, vol.46
, pp. 1680-1690
-
-
Simpson, S.J.1
Ranganathan, S.2
Park, J.3
Turkovic, L.4
Robins-Browne, R.M.5
Skoric, B.6
-
12
-
-
58149512622
-
Impact of Pseudomonas and Staphylococcus infection on inflammation and clinical status in young children with cystic fibrosis
-
Sagel SD, Gibson RL, Emerson J, McNamara S, Burns JL, Wagener JS, Ramsey BW; Inhaled Tobramycin in Young Children Study Group; Cystic Fibrosis Foundation Therapeutics Development Network. Impact of Pseudomonas and Staphylococcus infection on inflammation and clinical status in young children with cystic fibrosis. J Pediatr 2009;154:183-188.
-
(2009)
J Pediatr
, vol.154
, pp. 183-188
-
-
Inhaled Tobramycin in Young Children Study Group1
Cystic Fibrosis Foundation Therapeutics Development Network2
Sagel, S.D.3
Gibson, R.L.4
Emerson, J.5
McNamara, S.6
Burns, J.L.7
Wagener, J.S.8
Ramsey, B.W.9
-
13
-
-
46349106358
-
Lung function from infancy to the preschool years after clinical diagnosis of cystic fibrosis
-
Kozlowska WJ, Bush A, Wade A, Aurora P, Carr SB, Castle RA, Hoo AF, Lum S, Price J, Ranganathan S, et al.; London Cystic Fibrosis Collaboration. Lung function from infancy to the preschool years after clinical diagnosis of cystic fibrosis. Am J Respir Crit Care Med 2008;178:42-49.
-
(2008)
Am J Respir Crit Care Med
, vol.178
, pp. 42-49
-
-
Kozlowska, W.J.1
Bush, A.2
Wade, A.3
Aurora, P.4
Carr, S.B.5
Castle, R.A.6
Hoo, A.F.7
Lum, S.8
Price, J.9
Ranganathan, S.10
-
14
-
-
84872735966
-
Rescue of dysfunctional autophagy attenuates hyperinflammatory responses from cystic fibrosis cells
-
Mayer ML, Blohmke CJ, Falsafi R, Fjell CD, Madera L, Turvey SE, Hancock RE. Rescue of dysfunctional autophagy attenuates hyperinflammatory responses from cystic fibrosis cells. J Immunol 2013;190:1227-1238.
-
(2013)
J Immunol
, vol.190
, pp. 1227-1238
-
-
Mayer, M.L.1
Blohmke, C.J.2
Falsafi, R.3
Fjell, C.D.4
Madera, L.5
Turvey, S.E.6
Hancock, R.E.7
-
15
-
-
79955489997
-
Innate inflammatory responses of pediatric cystic fibrosis airway epithelial cells: Effects of nonviral and viral stimulation
-
Sutanto EN, Kicic A, Foo CJ, Stevens PT, Mullane D, Knight DA, Stick SM; Australian Respiratory Early Surveillance Team for Cystic Fibrosis. Innate inflammatory responses of pediatric cystic fibrosis airway epithelial cells: effects of nonviral and viral stimulation. Am J Respir Cell Mol Biol 2011;44:761-767.
-
(2011)
Am J Respir Cell Mol Biol
, vol.44
, pp. 761-767
-
-
Australian Respiratory Early Surveillance Team for Cystic Fibrosis1
Sutanto, E.N.2
Kicic, A.3
Foo, C.J.4
Stevens, P.T.5
Mullane, D.6
Knight, D.A.7
Stick, S.M.8
-
16
-
-
84879410271
-
Distribution of early structural lung changes due to cystic fibrosis detected with chest computed tomography
-
Mott LS, Park J, Gangell CL, de Klerk NH, Sly PD, Murray CP, Stick SM; Australian Respiratory Early Surveillance Team for Cystic Fibrosis Study Group. Distribution of early structural lung changes due to cystic fibrosis detected with chest computed tomography. J Pediatr 2013;163:243-248.
-
(2013)
J Pediatr
, vol.163
, pp. 243-248
-
-
Australian Respiratory Early Surveillance Team for Cystic Fibrosis Study Group1
Mott, L.S.2
Park, J.3
Gangell, C.L.4
De Klerk, N.H.5
Sly, P.D.6
Murray, C.P.7
Stick, S.M.8
-
17
-
-
84880070930
-
Differences in the pattern of structural abnormalities on CT scan in patients with cystic fibrosis and pancreatic sufficiency or insufficiency
-
Simanovsky N, Cohen-Cymberknoh M, Shoseyov D, Gileles-Hillel A, Wilschanski M, Kerem E, Hiller N. Differences in the pattern of structural abnormalities on CT scan in patients with cystic fibrosis and pancreatic sufficiency or insufficiency. Chest 2013;144:208-214.
-
(2013)
Chest
, vol.144
, pp. 208-214
-
-
Simanovsky, N.1
Cohen-Cymberknoh, M.2
Shoseyov, D.3
Gileles-Hillel, A.4
Wilschanski, M.5
Kerem, E.6
Hiller, N.7
-
18
-
-
84862776813
-
Progression of early structural lung disease in young children with cystic fibrosis assessed using CT
-
Mott LS, Park J, Murray CP, Gangell CL, de Klerk NH, Robinson PJ, Robertson CF, Ranganathan SC, Sly PD, Stick SM; AREST CF. Progression of early structural lung disease in young children with cystic fibrosis assessed using CT. Thorax 2012;67:509-516.
-
(2012)
Thorax
, vol.67
, pp. 509-516
-
-
AREST CF1
Mott, L.S.2
Park, J.3
Murray, C.P.4
Gangell, C.L.5
De Klerk, N.H.6
Robinson, P.J.7
Robertson, C.F.8
Ranganathan, S.C.9
Sly, P.D.10
Stick, S.M.11
-
19
-
-
77956240072
-
Airway surface liquid volume regulation determines different airway phenotypes in liddle compared with betaENaC-overexpressing mice
-
Mall MA, Button B, Johannesson B, Zhou Z, Livraghi A, Caldwell RA, Schubert SC, Schultz C, O'Neal WK, Pradervand S, et al. Airway surface liquid volume regulation determines different airway phenotypes in liddle compared with betaENaC-overexpressing mice. J Biol Chem 2010;285:26945-26955.
-
(2010)
J Biol Chem
, vol.285
, pp. 26945-26955
-
-
Mall, M.A.1
Button, B.2
Johannesson, B.3
Zhou, Z.4
Livraghi, A.5
Caldwell, R.A.6
Schubert, S.C.7
Schultz, C.8
O'neal, W.K.9
Pradervand, S.10
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