Airway surface liquid volume regulation determines different airway phenotypes in liddle compared with βENaC-overexpressing mice

Journal of Biological Chemistry

Volumn 285, Issue 35, 2010, Pages 26945-26955

  Mall, Marcus A ^a   Button, Brian ^c   Johannesson, Bjarki ^a   Zhou, Zhe ^a   Livraghi, Alessandra ^c   Caldwell, Ray A ^c   Schubert, Susanne C ^a   Schultz, Carsten ^a,b   O'Neal, Wanda K ^c   Pradervand, Sylvain ^d   Hummler, Edith ^d   Rossier, Bernard C ^d   Grubb, Barbara R ^c   Boucher, Richard C ^c  

^a UNIVERSITY OF HEIDELBERG   (Germany)

^b EUROPEAN MOLECULAR BIOLOGY LABORATORY   (Germany)

^c UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

^d UNIVERSITY OF LAUSANNE   (Switzerland)

Author keywords

[No Author keywords available]

Indexed keywords

AIRWAY SURFACE LIQUID; CYSTIC FIBROSIS; DOUBLE MUTANTS; HUMAN AIRWAY; HYPER-FUNCTION; IN-VIVO; LOW LEVEL; LUNG DISEASE; MUTANT MICE; PHYSIOLOGIC FUNCTION; TRANSPORT RATE;

BIOLOGICAL ORGANS; LIQUIDS;

SODIUM;

APROTININ; CHLORIDE ION; EPITHELIAL SODIUM CHANNEL; EPITHELIAL SODIUM CHANNEL ALPHA SUBUNIT; EPITHELIAL SODIUM CHANNEL BETA SUBUNIT; EPITHELIAL SODIUM CHANNEL GAMMA SUBUNIT; SERINE PROTEINASE; SERUM AND GLUCOCORTICOID REGULATED KINASE 1; TRANSMEMBRANE CONDUCTANCE REGULATOR; TRYPSIN; UBIQUITIN PROTEIN LIGASE NEDD4; UNCLASSIFIED DRUG;

AIRWAY; AIRWAY SURFACE LIQUID VOLUME; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; GAIN OF FUNCTION MUTATION; GENE MUTATION; GENE OVEREXPRESSION; HISTOLOGY; IN VIVO STUDY; LIDDLE SYNDROME; LUNG DISEASE; MOUSE; MOUSE STRAIN; MUTANT; NONHUMAN; NOSE MUCOSA; PHENOTYPE; PRIORITY JOURNAL; SODIUM ABSORPTION; SODIUM TRANSPORT; TRACHEA MUCOSA;

ANIMALS; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EPITHELIAL SODIUM CHANNEL; GENE EXPRESSION REGULATION; HUMANS; ION TRANSPORT; LIDDLE SYNDROME; MICE; MICE, KNOCKOUT; MUTATION; NASAL MUCOSA; ORGAN CULTURE TECHNIQUES; SODIUM; TRACHEA;

MUS;

EID: 77956240072     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M110.151803     Document Type: Article

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