메뉴 건너뛰기




Volumn 46, Issue 6, 2015, Pages 1680-1690

Progressive ventilation inhomogeneity in infants with cystic fibrosis after pulmonary infection

Author keywords

[No Author keywords available]

Indexed keywords

IL8 PROTEIN, HUMAN; INTERLEUKIN 8;

EID: 84948971137     PISSN: 09031936     EISSN: 13993003     Source Type: Journal    
DOI: 10.1183/13993003.00622-2015     Document Type: Article
Times cited : (45)

References (60)
  • 1
    • 0028015883 scopus 로고
    • Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation
    • Konstan MW, Hilliard KA, Norvell TM, et al. Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation. Am J Respir Crit Care Med 1994; 150: 448-454.
    • (1994) Am J Respir Crit Care Med , vol.150 , pp. 448-454
    • Konstan, M.W.1    Hilliard, K.A.2    Norvell, T.M.3
  • 2
    • 0032770489 scopus 로고    scopus 로고
    • Quantitation of inflammatory responses to bacteria in young cystic fibrosis and control patients
    • Muhlebach MS, Stewart PW, Leigh MW, et al. Quantitation of inflammatory responses to bacteria in young cystic fibrosis and control patients. Am J Respir Crit Care Med 1999; 160: 186-191.
    • (1999) Am J Respir Crit Care Med , vol.160 , pp. 186-191
    • Muhlebach, M.S.1    Stewart, P.W.2    Leigh, M.W.3
  • 3
    • 0036529046 scopus 로고    scopus 로고
    • Inflammation, infection, and pulmonary function in infants and young children with cystic fibrosis
    • Dakin CJ, Numa AH, Wang H, et al. Inflammation, infection, and pulmonary function in infants and young children with cystic fibrosis. Am J Respir Crit Care Med 2002; 165: 904-910.
    • (2002) Am J Respir Crit Care Med , vol.165 , pp. 904-910
    • Dakin, C.J.1    Numa, A.H.2    Wang, H.3
  • 4
    • 0030768159 scopus 로고    scopus 로고
    • Lower airway inflammation in infants and young children with cystic fibrosis
    • Armstrong DS, Grimwood K, Carlin JB, et al. Lower airway inflammation in infants and young children with cystic fibrosis. Am J Respir Crit Care Med 1997; 156: 1197-1204.
    • (1997) Am J Respir Crit Care Med , vol.156 , pp. 1197-1204
    • Armstrong, D.S.1    Grimwood, K.2    Carlin, J.B.3
  • 5
    • 70349831005 scopus 로고    scopus 로고
    • Bronchiectasis in infants and preschool children diagnosed with cystic fibrosis after newborn screening
    • Stick SM, Brennan S, Murray C, et al. Bronchiectasis in infants and preschool children diagnosed with cystic fibrosis after newborn screening. J Pediatr 2009; 155: 623-628.
    • (2009) J Pediatr , vol.155 , pp. 623-628
    • Stick, S.M.1    Brennan, S.2    Murray, C.3
  • 6
    • 67650712233 scopus 로고    scopus 로고
    • Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening
    • Sly PD, Brennan S, Gangell C, et al. Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening. Am J Respir Crit Care Med 2009; 180: 146-152.
    • (2009) Am J Respir Crit Care Med , vol.180 , pp. 146-152
    • Sly, P.D.1    Brennan, S.2    Gangell, C.3
  • 7
    • 67649476123 scopus 로고    scopus 로고
    • Bronchiectasis in an asymptomatic infant with cystic fibrosis diagnosed following newborn screening
    • Mott LS, Gangell CL, Murray CP, et al. Bronchiectasis in an asymptomatic infant with cystic fibrosis diagnosed following newborn screening. J Cyst Fibros 2009; 8: 285-287.
    • (2009) J Cyst Fibros , vol.8 , pp. 285-287
    • Mott, L.S.1    Gangell, C.L.2    Murray, C.P.3
  • 8
    • 57149116921 scopus 로고    scopus 로고
    • Lung function in infants with cystic fibrosis diagnosed by newborn screening
    • Linnane BM, Hall GL, Nolan G, et al. Lung function in infants with cystic fibrosis diagnosed by newborn screening. Am J Respir Crit Care Med 2008; 178: 1238-1244.
    • (2008) Am J Respir Crit Care Med , vol.178 , pp. 1238-1244
    • Linnane, B.M.1    Hall, G.L.2    Nolan, G.3
  • 9
    • 80051572617 scopus 로고    scopus 로고
    • Infection, inflammation, and lung function decline in infants with cystic fibrosis
    • Pillarisetti N, Williamson E, Linnane B, et al. Infection, inflammation, and lung function decline in infants with cystic fibrosis. Am J Respir Crit Care Med 2011; 184: 75-81.
    • (2011) Am J Respir Crit Care Med , vol.184 , pp. 75-81
    • Pillarisetti, N.1    Williamson, E.2    Linnane, B.3
  • 10
    • 34247167236 scopus 로고    scopus 로고
    • Early detection of cystic fibrosis lung disease: Multiple-breath washout versus raised volume tests
    • Lum S, Gustafsson P, Ljungberg H, et al. Early detection of cystic fibrosis lung disease: multiple-breath washout versus raised volume tests. Thorax 2007; 62: 341-347.
    • (2007) Thorax , vol.62 , pp. 341-347
    • Lum, S.1    Gustafsson, P.2    Ljungberg, H.3
  • 11
    • 0035830289 scopus 로고    scopus 로고
    • Airway function in infants newly diagnosed with cystic fibrosis
    • Ranganathan SC, Dezateux C, Bush A, et al. Airway function in infants newly diagnosed with cystic fibrosis. Lancet 2001; 358: 1964-1965.
    • (2001) Lancet , vol.358 , pp. 1964-1965
    • Ranganathan, S.C.1    Dezateux, C.2    Bush, A.3
  • 12
    • 11144355490 scopus 로고    scopus 로고
    • The evolution of airway function in early childhood following clinical diagnosis of cystic fibrosis
    • Ranganathan SC, Stocks J, Dezateux C, et al. The evolution of airway function in early childhood following clinical diagnosis of cystic fibrosis. Am J Respir Crit Care Med 2004; 169: 928-933.
    • (2004) Am J Respir Crit Care Med , vol.169 , pp. 928-933
    • Ranganathan, S.C.1    Stocks, J.2    Dezateux, C.3
  • 13
    • 77951983616 scopus 로고    scopus 로고
    • Multiple-breath inert gas washout test and early cystic fibrosis lung disease
    • Aurora P. Multiple-breath inert gas washout test and early cystic fibrosis lung disease. Thorax 2010; 65: 373-374.
    • (2010) Thorax , vol.65 , pp. 373-374
    • Aurora, P.1
  • 14
    • 77955288385 scopus 로고    scopus 로고
    • Comparison of the utility of multiple breath inert gas washout parameters in cystic fibrosis
    • Robinson PD, Lindblad A, Gustafsson PM. Comparison of the utility of multiple breath inert gas washout parameters in cystic fibrosis. Thorax 2010; 65: 659.
    • (2010) Thorax , vol.65 , pp. 659
    • Robinson, P.D.1    Lindblad, A.2    Gustafsson, P.M.3
  • 15
    • 23644454805 scopus 로고    scopus 로고
    • Gas mixing efficiency from birth to adulthood measured by multiple-breath washout
    • Aurora P, Kozlowska W, Stocks J. Gas mixing efficiency from birth to adulthood measured by multiple-breath washout. Respir Physiol Neurobiol 2005; 148: 125-139.
    • (2005) Respir Physiol Neurobiol , vol.148 , pp. 125-139
    • Aurora, P.1    Kozlowska, W.2    Stocks, J.3
  • 16
    • 12744277962 scopus 로고    scopus 로고
    • Multiple-breath washout as a marker of lung disease in preschool children with cystic fibrosis
    • Aurora P, Bush A, Gustafsson P, et al. Multiple-breath washout as a marker of lung disease in preschool children with cystic fibrosis. Am J Respir Crit Care Med 2005; 171: 249-256.
    • (2005) Am J Respir Crit Care Med , vol.171 , pp. 249-256
    • Aurora, P.1    Bush, A.2    Gustafsson, P.3
  • 17
    • 39049084491 scopus 로고    scopus 로고
    • Multiple-breath inert gas washout and spirometry versus structural lung disease in cystic fibrosis
    • Gustafsson PM, De Jong PA, Tiddens HA, et al. Multiple-breath inert gas washout and spirometry versus structural lung disease in cystic fibrosis. Thorax 2008; 63: 129-134.
    • (2008) Thorax , vol.63 , pp. 129-134
    • Gustafsson, P.M.1    De Jong, P.A.2    Tiddens, H.A.3
  • 18
    • 79952504576 scopus 로고    scopus 로고
    • Lung clearance index at 4 years predicts subsequent lung function in children with cystic fibrosis
    • Aurora P, Stanojevic S, Wade A, et al. Lung clearance index at 4 years predicts subsequent lung function in children with cystic fibrosis. Am J Respir Crit Care Med 2011; 183: 752-758.
    • (2011) Am J Respir Crit Care Med , vol.183 , pp. 752-758
    • Aurora, P.1    Stanojevic, S.2    Wade, A.3
  • 19
    • 79956360940 scopus 로고    scopus 로고
    • Lung Clearance Index and HRCT are complementary markers of lung abnormalities in young children with CF
    • Owens CM, Aurora P, Stanojevic S, et al. Lung Clearance Index and HRCT are complementary markers of lung abnormalities in young children with CF. Thorax 2011; 66: 481-488.
    • (2011) Thorax , vol.66 , pp. 481-488
    • Owens, C.M.1    Aurora, P.2    Stanojevic, S.3
  • 20
    • 13544250572 scopus 로고    scopus 로고
    • Ventilation inhomogeneities in relation to standard lung function in patients with cystic fibrosis
    • Kraemer R, Blum A, Schibler A, et al. Ventilation inhomogeneities in relation to standard lung function in patients with cystic fibrosis. Am J Respir Crit Care Med 2005; 171: 371-378.
    • (2005) Am J Respir Crit Care Med , vol.171 , pp. 371-378
    • Kraemer, R.1    Blum, A.2    Schibler, A.3
  • 21
    • 78650016662 scopus 로고    scopus 로고
    • Sensitivity of Lung Clearance Index and chest computed tomography in early CF lung disease
    • Ellemunter H, Fuchs SI, Unsinn KM, et al. Sensitivity of Lung Clearance Index and chest computed tomography in early CF lung disease. Respir Med 2010; 104: 1834-1842.
    • (2010) Respir Med , vol.104 , pp. 1834-1842
    • Ellemunter, H.1    Fuchs, S.I.2    Unsinn, K.M.3
  • 22
    • 81455154503 scopus 로고    scopus 로고
    • Long-term course of lung clearance index between infancy and school-age in cystic fibrosis subjects
    • Kieninger E, Singer F, Fuchs O, et al. Long-term course of lung clearance index between infancy and school-age in cystic fibrosis subjects. J Cyst Fibros 2011; 10: 487-490.
    • (2011) J Cyst Fibros , vol.10 , pp. 487-490
    • Kieninger, E.1    Singer, F.2    Fuchs, O.3
  • 23
    • 79953287790 scopus 로고    scopus 로고
    • The effect of dornase alfa on ventilation inhomogeneity in patients with cystic fibrosis
    • Amin R, Subbarao P, Lou W, et al. The effect of dornase alfa on ventilation inhomogeneity in patients with cystic fibrosis. Eur Respir J 2011; 37: 806-812.
    • (2011) Eur Respir J , vol.37 , pp. 806-812
    • Amin, R.1    Subbarao, P.2    Lou, W.3
  • 24
    • 77951988740 scopus 로고    scopus 로고
    • Hypertonic saline improves the LCI in paediatric patients with CF with normal lung function
    • Amin R, Subbarao P, Jabar A, et al. Hypertonic saline improves the LCI in paediatric patients with CF with normal lung function. Thorax 2010; 65: 379-383.
    • (2010) Thorax , vol.65 , pp. 379-383
    • Amin, R.1    Subbarao, P.2    Jabar, A.3
  • 25
    • 9644303188 scopus 로고    scopus 로고
    • Detecting early lung disease in cystic fibrosis: Are current techniques sufficient?
    • Sly PD, Brennan S. Detecting early lung disease in cystic fibrosis: are current techniques sufficient? Thorax 2004; 59: 1008-1010.
    • (2004) Thorax , vol.59 , pp. 1008-1010
    • Sly, P.D.1    Brennan, S.2
  • 26
    • 68049093796 scopus 로고    scopus 로고
    • Using index of ventilation to assess response to treatment for acute pulmonary exacerbation in children with cystic fibrosis
    • Robinson PD, Cooper P, Van Asperen P, et al. Using index of ventilation to assess response to treatment for acute pulmonary exacerbation in children with cystic fibrosis. Pediatr Pulmonol 2009; 44: 733-742.
    • (2009) Pediatr Pulmonol , vol.44 , pp. 733-742
    • Robinson, P.D.1    Cooper, P.2    Van Asperen, P.3
  • 27
    • 84911981936 scopus 로고    scopus 로고
    • Lung clearance index during hospital admission in school-age children with cystic fibrosis
    • Welsh L, Nesci C, Tran H, et al. Lung clearance index during hospital admission in school-age children with cystic fibrosis. J Cyst Fibros 2014; 13: 687-691.
    • (2014) J Cyst Fibros , vol.13 , pp. 687-691
    • Welsh, L.1    Nesci, C.2    Tran, H.3
  • 28
    • 84866070431 scopus 로고    scopus 로고
    • Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening
    • Hoo AF, Thia LP, Nguyen TT, et al. Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening. Thorax 2012; 67: 874-881.
    • (2012) Thorax , vol.67 , pp. 874-881
    • Hoo, A.F.1    Thia, L.P.2    Nguyen, T.T.3
  • 29
    • 80051850244 scopus 로고    scopus 로고
    • Air trapping on chest CT is associated with worse ventilation distribution in infants with cystic fibrosis diagnosed following newborn screening
    • Hall GL, Logie KM, Parsons F, et al. Air trapping on chest CT is associated with worse ventilation distribution in infants with cystic fibrosis diagnosed following newborn screening. PLoS One 2011; 6: e23932.
    • (2011) PLoS One , vol.6 , pp. e23932
    • Hall, G.L.1    Logie, K.M.2    Parsons, F.3
  • 30
    • 84860110054 scopus 로고    scopus 로고
    • Early cystic fibrosis lung disease detected by bronchoalveolar lavage and lung clearance index
    • Belessis Y, Dixon B, Hawkins G, et al. Early cystic fibrosis lung disease detected by bronchoalveolar lavage and lung clearance index. Am J Respir Crit Care Med 2012; 185: 862-873.
    • (2012) Am J Respir Crit Care Med , vol.185 , pp. 862-873
    • Belessis, Y.1    Dixon, B.2    Hawkins, G.3
  • 31
    • 0036800001 scopus 로고    scopus 로고
    • Measurement of lung volume and ventilation distribution with an ultrasonic flow meter in healthy infants
    • Schibler A, Hall GL, Businger F, et al. Measurement of lung volume and ventilation distribution with an ultrasonic flow meter in healthy infants. Eur Respir J 2002; 20: 912-918.
    • (2002) Eur Respir J , vol.20 , pp. 912-918
    • Schibler, A.1    Hall, G.L.2    Businger, F.3
  • 32
    • 77949487366 scopus 로고    scopus 로고
    • Lung volume and ventilation inhomogeneity in preterm infants at 15-18 months corrected age
    • Schulzke SM, Hall GL, Nathan EA, et al. Lung volume and ventilation inhomogeneity in preterm infants at 15-18 months corrected age. J Pediatr 2010; 156: 542-549.
    • (2010) J Pediatr , vol.156 , pp. 542-549
    • Schulzke, S.M.1    Hall, G.L.2    Nathan, E.A.3
  • 33
    • 35148862499 scopus 로고    scopus 로고
    • Optimized temperature and deadspace correction improve analysis of multiple breath washout measurements by ultrasonic flowmeter in infants
    • Latzin P, Sauteur L, Thamrin C, et al. Optimized temperature and deadspace correction improve analysis of multiple breath washout measurements by ultrasonic flowmeter in infants. Pediatr Pulmonol 2007; 42: 888-897.
    • (2007) Pediatr Pulmonol , vol.42 , pp. 888-897
    • Latzin, P.1    Sauteur, L.2    Thamrin, C.3
  • 35
    • 70349971436 scopus 로고    scopus 로고
    • Inert gas washout: Theoretical background and clinical utility in respiratory disease
    • Robinson PD, Goldman MD, Gustafsson PM. Inert gas washout: theoretical background and clinical utility in respiratory disease. Respiration 2009; 78: 339-355.
    • (2009) Respiration , vol.78 , pp. 339-355
    • Robinson, P.D.1    Goldman, M.D.2    Gustafsson, P.M.3
  • 36
    • 0033985571 scopus 로고    scopus 로고
    • Bronchoalveolar lavage in children. ERS Task Force on bronchoalveolar lavage in children
    • de Blic J, Midulla F, Barbato A, et al. Bronchoalveolar lavage in children. ERS Task Force on bronchoalveolar lavage in children. Eur Respir J 2000; 15: 217-231.
    • (2000) Eur Respir J , vol.15 , pp. 217-231
    • De Blic, J.1    Midulla, F.2    Barbato, A.3
  • 37
    • 13544260495 scopus 로고    scopus 로고
    • Correlation of forced oscillation technique in preschool children with cystic fibrosis with pulmonary inflammation
    • Brennan S, Hall GL, Horak F, et al. Correlation of forced oscillation technique in preschool children with cystic fibrosis with pulmonary inflammation. Thorax 2005; 60: 159-163.
    • (2005) Thorax , vol.60 , pp. 159-163
    • Brennan, S.1    Hall, G.L.2    Horak, F.3
  • 38
    • 80052014087 scopus 로고    scopus 로고
    • Inflammatory responses to individual microorganisms in the lungs of children with cystic fibrosis
    • Gangell C, Gard S, Douglas T, et al. Inflammatory responses to individual microorganisms in the lungs of children with cystic fibrosis. Clin Infect Dis 2011; 53: 425-432.
    • (2011) Clin Infect Dis , vol.53 , pp. 425-432
    • Gangell, C.1    Gard, S.2    Douglas, T.3
  • 39
    • 0141615605 scopus 로고    scopus 로고
    • The phenotypic consequences of CFTR mutations
    • Rowntree RK, Harris A. The phenotypic consequences of CFTR mutations. Ann Hum Genet 2003; 67: 471-485.
    • (2003) Ann Hum Genet , vol.67 , pp. 471-485
    • Rowntree, R.K.1    Harris, A.2
  • 40
    • 77957576131 scopus 로고    scopus 로고
    • Mutations that permit residual CFTR function delay acquisition of multiple respiratory pathogens in CF patients
    • Green DM, McDougal KE, Blackman SM, et al. Mutations that permit residual CFTR function delay acquisition of multiple respiratory pathogens in CF patients. Respir Res 2010; 11: 140.
    • (2010) Respir Res , vol.11 , pp. 140
    • Green, D.M.1    McDougal, K.E.2    Blackman, S.M.3
  • 41
    • 0034109607 scopus 로고    scopus 로고
    • Genotype and phenotype in cystic fibrosis
    • Zielenski J. Genotype and phenotype in cystic fibrosis. Respiration 2000; 67: 117-133.
    • (2000) Respiration , vol.67 , pp. 117-133
    • Zielenski, J.1
  • 42
    • 0029616734 scopus 로고
    • Cystic fibrosis: Genotypic and phenotypic variations
    • Zielenski J, Tsui LC. Cystic fibrosis: genotypic and phenotypic variations. Annu Rev Genet 1995; 29: 777-807.
    • (1995) Annu Rev Genet , vol.29 , pp. 777-807
    • Zielenski, J.1    Tsui, L.C.2
  • 43
    • 0346121620 scopus 로고    scopus 로고
    • Evaluation of ventilation maldistribution as an early indicator of lung disease in children with cystic fibrosis
    • Gustafsson PM, Aurora P, Lindblad A. Evaluation of ventilation maldistribution as an early indicator of lung disease in children with cystic fibrosis. Eur Respir J 2003; 22: 972-979.
    • (2003) Eur Respir J , vol.22 , pp. 972-979
    • Gustafsson, P.M.1    Aurora, P.2    Lindblad, A.3
  • 44
    • 79958013884 scopus 로고    scopus 로고
    • Is lung function diminished by 3 months of age in infants with cystic fibrosis (CF) diagnosed by newborn screening (NBS)?
    • Hoo A, Chudleigh J, Prasad A, et al. Is lung function diminished by 3 months of age in infants with cystic fibrosis (CF) diagnosed by newborn screening (NBS)? Eur Respir J 2010; 36: Suppl. 54, 1016s.
    • (2010) Eur Respir J , vol.36 , pp. 1016s
    • Hoo, A.1    Chudleigh, J.2    Prasad, A.3
  • 45
    • 84885071273 scopus 로고    scopus 로고
    • Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: A randomised controlled trial
    • Davies J, Sheridan H, Bell N, et al. Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: a randomised controlled trial. Lancet Respir Med 2013; 1: 630-638.
    • (2013) Lancet Respir Med , vol.1 , pp. 630-638
    • Davies, J.1    Sheridan, H.2    Bell, N.3
  • 46
    • 84923930953 scopus 로고    scopus 로고
    • Early respiratory infection is associated with reduced spirometry in children with cystic fibrosis
    • Ramsey KA, Ranganathan S, Park J, et al. Early respiratory infection is associated with reduced spirometry in children with cystic fibrosis. Am J Respir Crit Care Med 2014; 190: 1111-1116.
    • (2014) Am J Respir Crit Care Med , vol.190 , pp. 1111-1116
    • Ramsey, K.A.1    Ranganathan, S.2    Park, J.3
  • 47
    • 33745757955 scopus 로고    scopus 로고
    • Haemophilus influenzae forms biofilms on airway epithelia: Implications in cystic fibrosis
    • Starner TD, Zhang N, Kim G, et al. Haemophilus influenzae forms biofilms on airway epithelia: implications in cystic fibrosis. Am J Respir Crit Care Med 2006; 174: 213-220.
    • (2006) Am J Respir Crit Care Med , vol.174 , pp. 213-220
    • Starner, T.D.1    Zhang, N.2    Kim, G.3
  • 48
    • 84887236798 scopus 로고    scopus 로고
    • Staphylococcus aureus in early cystic fibrosis lung disease
    • Wong JK, Ranganathan SC, Hart E. Staphylococcus aureus in early cystic fibrosis lung disease. Pediatr Pulmonol 2013; 48: 1151-1159.
    • (2013) Pediatr Pulmonol , vol.48 , pp. 1151-1159
    • Wong, J.K.1    Ranganathan, S.C.2    Hart, E.3
  • 49
    • 77449133012 scopus 로고    scopus 로고
    • Cystic Fibrosis Foundation evidence-based guidelines for management of infants with cystic fibrosis
    • Borowitz D, Robinson KA, Rosenfeld M, et al. Cystic Fibrosis Foundation evidence-based guidelines for management of infants with cystic fibrosis. J Pediatr 2009; 155: Suppl. 6, S73-S93.
    • (2009) J Pediatr , vol.155 , pp. S73-S93
    • Borowitz, D.1    Robinson, K.A.2    Rosenfeld, M.3
  • 50
    • 46349106358 scopus 로고    scopus 로고
    • Lung function from infancy to the preschool years after clinical diagnosis of cystic fibrosis
    • Kozlowska WJ, Bush A, Wade A, et al. Lung function from infancy to the preschool years after clinical diagnosis of cystic fibrosis. Am J Respir Crit Care Med 2008; 178: 42-49.
    • (2008) Am J Respir Crit Care Med , vol.178 , pp. 42-49
    • Kozlowska, W.J.1    Bush, A.2    Wade, A.3
  • 51
    • 0029010510 scopus 로고
    • Lower respiratory infection and inflammation in infants with newly diagnosed cystic fibrosis
    • Armstrong DS, Grimwood K, Carzino R, et al. Lower respiratory infection and inflammation in infants with newly diagnosed cystic fibrosis. BMJ 1995; 310: 1571-1572.
    • (1995) BMJ , vol.310 , pp. 1571-1572
    • Armstrong, D.S.1    Grimwood, K.2    Carzino, R.3
  • 52
    • 0028914085 scopus 로고
    • Early pulmonary inflammation in infants with cystic fibrosis
    • Khan TZ, Wagener JS, Bost T, et al. Early pulmonary inflammation in infants with cystic fibrosis. Am J Respir Crit Care Med 1995; 151: 1075-1082.
    • (1995) Am J Respir Crit Care Med , vol.151 , pp. 1075-1082
    • Khan, T.Z.1    Wagener, J.S.2    Bost, T.3
  • 53
    • 59649123905 scopus 로고    scopus 로고
    • Acquisition and eradication of P. Aeruginosa in young children with cystic fibrosis
    • Douglas TA, Brennan S, Gard S, et al. Acquisition and eradication of P. aeruginosa in young children with cystic fibrosis. Eur Respir J 2009; 33: 305-311.
    • (2009) Eur Respir J , vol.33 , pp. 305-311
    • Douglas, T.A.1    Brennan, S.2    Gard, S.3
  • 54
    • 77957576131 scopus 로고    scopus 로고
    • Mutations that permit residual CFTR function delay acquisition of multiple respiratory pathogens in CF patients
    • Green DM, McDougal KE, Blackman SM, et al. Mutations that permit residual CFTR function delay acquisition of multiple respiratory pathogens in CF patients. Respir Res 2010; 11: 140.
    • (2010) Respir Res , vol.11 , pp. 140
    • Green, D.M.1    McDougal, K.E.2    Blackman, S.M.3
  • 55
    • 0031471090 scopus 로고    scopus 로고
    • Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis
    • Corey M, Edwards L, Levison H, et al. Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis. J Pediatr 1997; 131: 809-814.
    • (1997) J Pediatr , vol.131 , pp. 809-814
    • Corey, M.1    Edwards, L.2    Levison, H.3
  • 56
    • 0028806462 scopus 로고
    • Genetic and clinical features of patients with cystic fibrosis diagnosed after the age of 16 years
    • Gan KH, Geus WP, Bakker W, et al. Genetic and clinical features of patients with cystic fibrosis diagnosed after the age of 16 years. Thorax 1995; 50: 1301-1304.
    • (1995) Thorax , vol.50 , pp. 1301-1304
    • Gan, K.H.1    Geus, W.P.2    Bakker, W.3
  • 57
    • 0029003982 scopus 로고
    • A cystic fibrosis mutation associated with mild lung disease
    • Gan KH, Veeze HJ, van den Ouweland AM, et al. A cystic fibrosis mutation associated with mild lung disease. N Engl J Med 1995; 333: 95-99.
    • (1995) N Engl J Med , vol.333 , pp. 95-99
    • Gan, K.H.1    Veeze, H.J.2    Van Den Ouweland, A.M.3
  • 59
    • 84865285995 scopus 로고    scopus 로고
    • Direct sampling of cystic fibrosis lungs indicates that DNA-based analyses of upper-airway specimens can misrepresent lung microbiota
    • Goddard AF, Staudinger BJ, Dowd SE, et al. Direct sampling of cystic fibrosis lungs indicates that DNA-based analyses of upper-airway specimens can misrepresent lung microbiota. Proc Natl Acad Sci USA 2012; 109: 13769-13774.
    • (2012) Proc Natl Acad Sci USA , vol.109 , pp. 13769-13774
    • Goddard, A.F.1    Staudinger, B.J.2    Dowd, S.E.3
  • 60
    • 84859620802 scopus 로고    scopus 로고
    • Cystic fibrosis: A mucosal immunodeficiency syndrome
    • Cohen TS, Prince A. Cystic fibrosis: a mucosal immunodeficiency syndrome. Nat Med 2012; 18: 509-519.
    • (2012) Nat Med , vol.18 , pp. 509-519
    • Cohen, T.S.1    Prince, A.2


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.