Schnitzler's syndrome: Lessons from 281 cases

Clinical and Translational Allergy

Volumn 4, Issue 1, 2014, Pages

  De Koning, Heleen D ^a,b,c  

^a RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^b RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^c N4i Centre for Immunodeficiency and Autoinflammation   (Netherlands)

Author keywords

Autoinflammation; Chronic urticaria; Interleukin 1 beta; Monoclonal gammopathy; Paraprotein; Schnitzler's syndrome

Indexed keywords

ALKALINE PHOSPHATASE BONE ISOENZYME; ALPHA INTERFERON; BENCE JONES PROTEIN; C REACTIVE PROTEIN; CANAKINUMAB; COLCHICINE; CORTICOSTEROID; CRYOPYRIN; IMMUNOGLOBULIN G; IMMUNOGLOBULIN M; IMMUNOGLOBULIN M KAPPA; INTERLEUKIN 1BETA; INTERLEUKIN 6; OSTEOCALCIN; OSTEOCLAST DIFFERENTIATION FACTOR; OSTEOPROTEGERIN; PEFLOXACIN; RECOMBINANT INTERLEUKIN 1 RECEPTOR BLOCKING AGENT; RILONACEPT; RITUXIMAB; THALIDOMIDE; TOCILIZUMAB; TUMOR NECROSIS FACTOR ALPHA; UNCLASSIFIED DRUG; VASCULOTROPIN;

ADULT ONSET STILL DISEASE; ARTHRALGIA; BONE MARROW BIOPSY; BONE RADIOGRAPHY; BONE SCINTISCANNING; CHRONIC URTICARIA; CINCA SYNDROME; CLINICAL EFFECTIVENESS; CLINICAL FEATURE; CYTOKINE PRODUCTION; CYTOKINE RELEASE; CYTOKINE RESPONSE; DIFFERENTIAL DIAGNOSIS; DRUG MEGADOSE; DRUG WITHDRAWAL; ERYTHROCYTE SEDIMENTATION RATE; FEVER; FOLLOW UP; GAMMOPATHY; GENE; GENE MUTATION; HEMATOLOGIC MALIGNANCY; HISTOPATHOLOGY; HUMAN; IMMUNOPATHOGENESIS; INCIDENCE; INJECTION SITE ERYTHEMA; LABORATORY TEST; MOLECULAR PATHOLOGY; MONOCLONAL IMMUNOGLOBULINEMIA; NEUTROPENIA; NLRP3 GENE; OUTCOME ASSESSMENT; PLASMACYTOSIS; POEMS SYNDROME; POLYNEUROPATHY; PREVALENCE; PRIORITY JOURNAL; PROGNOSIS; PROTEIN BLOOD LEVEL; PROTEIN FUNCTION; RASH; REVIEW; SCHNITZLER SYNDROME; SENSORY NEUROPATHY; SEX RATIO; SKIN BIOPSY; SURVIVAL TIME; SYSTEMIC LUPUS ERYTHEMATOSUS; UPPER RESPIRATORY TRACT INFECTION; WALDENSTROEM MACROGLOBULINEMIA; WEIGHT REDUCTION;

EID: 84978022581     PISSN: None     EISSN: 20457022     Source Type: Journal    
DOI: 10.1186/2045-7022-4-41     Document Type: Review

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