Cell type-specific modulation of respiratory chain supercomplex organization

International Journal of Molecular Sciences

Volumn 17, Issue 6, 2016, Pages

  Sun, Dayan ^a   Li, Bin ^a   Qiu, Ruyi ^a   Fang, Hezhi ^a   Lyu, Jianxin ^a  

^a WENZHOU MEDICAL UNIVERSITY   (China)

Author keywords

Leigh s disease; Mitochondrial dysfunction; Mitochondrial supercomplex; Nuclear genetic background; Respiratory chain

Indexed keywords

REACTIVE OXYGEN METABOLITE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE; ADENOSINE TRIPHOSPHATE; SUCCINATE DEHYDROGENASE (UBIQUINONE); UBIQUINOL CYTOCHROME C REDUCTASE;

ARTICLE; CASE REPORT; CHILD; COPY NUMBER VARIATION; FEMALE; GENE SEQUENCE; HUMAN; IMMUNOBLOTTING; LEIGH DISEASE; MALE; MITOCHONDRIAL MEMBRANE POTENTIAL; MUTATIONAL ANALYSIS; OXYGEN CONSUMPTION; POLYMERASE CHAIN REACTION; PRESCHOOL CHILD; REAL TIME POLYMERASE CHAIN REACTION; RESPIRATORY CHAIN; RESTRICTION FRAGMENT LENGTH POLYMORPHISM; SCHOOL CHILD; WESTERN BLOTTING; ANIMAL; ANTIBODY SPECIFICITY; CELL CULTURE; GENETICS; LIVER MITOCHONDRION; METABOLISM; MOUSE; MUTATION; PATHOLOGY; PROTEIN MULTIMERIZATION; TUMOR CELL LINE;

ADENOSINE TRIPHOSPHATE; ANIMALS; CELL LINE, TUMOR; CELLS, CULTURED; CHILD; CHILD, PRESCHOOL; ELECTRON TRANSPORT COMPLEX II; ELECTRON TRANSPORT COMPLEX III; FEMALE; HUMANS; LEIGH DISEASE; MALE; MICE; MITOCHONDRIA, LIVER; MUTATION; NADH DEHYDROGENASE; ORGAN SPECIFICITY; PROTEIN MULTIMERIZATION;

EID: 84975847279     PISSN: 16616596     EISSN: 14220067     Source Type: Journal    
DOI: 10.3390/ijms17060926     Document Type: Article

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