-
1
-
-
55949098781
-
Respiratory active mitochondrial supercomplexes
-
Acin-Perez R., Fernandez-Silva P., Peleato M.L., Perez-Martos A., Enriquez J.A. Respiratory active mitochondrial supercomplexes. Mol. Cell 2008, 32:529-539.
-
(2008)
Mol. Cell
, vol.32
, pp. 529-539
-
-
Acin-Perez, R.1
Fernandez-Silva, P.2
Peleato, M.L.3
Perez-Martos, A.4
Enriquez, J.A.5
-
2
-
-
0016369243
-
Isolation of rat liver peroxisomes
-
Baudhuin P. Isolation of rat liver peroxisomes. Methods Enzymol. 1974, 31:356-368.
-
(1974)
Methods Enzymol.
, vol.31
, pp. 356-368
-
-
Baudhuin, P.1
-
3
-
-
37849035983
-
Multiple pathways for sorting mitochondrial precursor proteins
-
Bolender N., Sickmann A., Wagner R., Meisinger C., Pfanner N. Multiple pathways for sorting mitochondrial precursor proteins. EMBO Rep. 2008, 9:42-49.
-
(2008)
EMBO Rep.
, vol.9
, pp. 42-49
-
-
Bolender, N.1
Sickmann, A.2
Wagner, R.3
Meisinger, C.4
Pfanner, N.5
-
4
-
-
0029876984
-
In vivo labeling and analysis of human mitochondrial translation products
-
Chomyn A. In vivo labeling and analysis of human mitochondrial translation products. Methods Enzymol. 1996, 264:197-211.
-
(1996)
Methods Enzymol.
, vol.264
, pp. 197-211
-
-
Chomyn, A.1
-
5
-
-
34447312250
-
Human CIA30 is involved in the early assembly of mitochondrial complex I and mutations in its gene cause disease
-
Dunning C.J., McKenzie M., Sugiana C., Lazarou M., Silke J., Connelly A., Fletcher J.M., Kirby D.M., Thorburn D.R., Ryan M.T. Human CIA30 is involved in the early assembly of mitochondrial complex I and mutations in its gene cause disease. Embo J. 2007, 26:3227-3237.
-
(2007)
Embo J.
, vol.26
, pp. 3227-3237
-
-
Dunning, C.J.1
McKenzie, M.2
Sugiana, C.3
Lazarou, M.4
Silke, J.5
Connelly, A.6
Fletcher, J.M.7
Kirby, D.M.8
Thorburn, D.R.9
Ryan, M.T.10
-
6
-
-
0029936438
-
Analysis of aminoacylation of human mitochondrial tRNAs
-
Enriquez J.A., Attardi G. Analysis of aminoacylation of human mitochondrial tRNAs. Methods Enzymol. 1996, 264:183-196.
-
(1996)
Methods Enzymol.
, vol.264
, pp. 183-196
-
-
Enriquez, J.A.1
Attardi, G.2
-
7
-
-
0029767729
-
Evidence for aminoacylation-induced conformational changes in human mitochondrial tRNAs
-
Enriquez J.A., Attardi G. Evidence for aminoacylation-induced conformational changes in human mitochondrial tRNAs. Proc. Natl. Acad. Sci. USA 1996, 93:8300-8305.
-
(1996)
Proc. Natl. Acad. Sci. USA
, vol.93
, pp. 8300-8305
-
-
Enriquez, J.A.1
Attardi, G.2
-
8
-
-
0344097294
-
Direct regulation of mitochondrial RNA synthesis by thyroid hormone
-
Enriquez J.A., Fernandez-Silva P., Garrido-Perez N., Lopez-Perez M.J., Perez-Martos A., Montoya J. Direct regulation of mitochondrial RNA synthesis by thyroid hormone. Mol. Cell. Biol. 1999, 19:657-670.
-
(1999)
Mol. Cell. Biol.
, vol.19
, pp. 657-670
-
-
Enriquez, J.A.1
Fernandez-Silva, P.2
Garrido-Perez, N.3
Lopez-Perez, M.J.4
Perez-Martos, A.5
Montoya, J.6
-
9
-
-
0345493790
-
Autonomous regulation in mammalian mitochondrial DNA transcription
-
Enriquez J.A., Fernandez-Silva P., Montoya J. Autonomous regulation in mammalian mitochondrial DNA transcription. Biol. Chem. 1999, 380:737-747.
-
(1999)
Biol. Chem.
, vol.380
, pp. 737-747
-
-
Enriquez, J.A.1
Fernandez-Silva, P.2
Montoya, J.3
-
10
-
-
0029974275
-
The synthesis of mRNA in isolated mitochondria can be maintained for several hours and is inhibited by high levels of ATP
-
Enriquez J.A., Fernandez-Silva P., Perez-Martos A., Lopez-Perez M.J., Montoya J. The synthesis of mRNA in isolated mitochondria can be maintained for several hours and is inhibited by high levels of ATP. Eur. J. Biochem. 1996, 237:601-610.
-
(1996)
Eur. J. Biochem.
, vol.237
, pp. 601-610
-
-
Enriquez, J.A.1
Fernandez-Silva, P.2
Perez-Martos, A.3
Lopez-Perez, M.J.4
Montoya, J.5
-
11
-
-
0029876982
-
In organello RNA synthesis system from mammalian liver and brain
-
Enriquez J.A., Perez-Martos A., Lopez-Perez M.J., Montoya J. In organello RNA synthesis system from mammalian liver and brain. Methods Enzymol. 1996, 264:50-57.
-
(1996)
Methods Enzymol.
, vol.264
, pp. 50-57
-
-
Enriquez, J.A.1
Perez-Martos, A.2
Lopez-Perez, M.J.3
Montoya, J.4
-
12
-
-
0028322165
-
Highly efficient DNA synthesis in isolated mitochondria from rat liver
-
Enriquez J.A., Ramos J., Perez-Martos A., Lopez-Perez M.J., Montoya J. Highly efficient DNA synthesis in isolated mitochondria from rat liver. Nucleic Acids Res. 1994, 22:1861-1865.
-
(1994)
Nucleic Acids Res.
, vol.22
, pp. 1861-1865
-
-
Enriquez, J.A.1
Ramos, J.2
Perez-Martos, A.3
Lopez-Perez, M.J.4
Montoya, J.5
-
13
-
-
0025647694
-
Rat brain synaptosomes prepared by phase partition
-
Enriquez J.A., Sanchez-Prieto J., Muino Blanco M.T., Hernandez-Yago J., Lopez-Perez M.J. Rat brain synaptosomes prepared by phase partition. J. Neurochem. 1990, 55:1841-1849.
-
(1990)
J. Neurochem.
, vol.55
, pp. 1841-1849
-
-
Enriquez, J.A.1
Sanchez-Prieto, J.2
Muino Blanco, M.T.3
Hernandez-Yago, J.4
Lopez-Perez, M.J.5
-
14
-
-
34147119553
-
In vivo and in organello analyses of mitochondrial translation
-
Fernandez-Silva P., Acin-Perez R., Fernandez-Vizarra E., Perez-Martos A., Enriquez J.A. In vivo and in organello analyses of mitochondrial translation. Methods Cell Biol. 2007, 80:571-588.
-
(2007)
Methods Cell Biol.
, vol.80
, pp. 571-588
-
-
Fernandez-Silva, P.1
Acin-Perez, R.2
Fernandez-Vizarra, E.3
Perez-Martos, A.4
Enriquez, J.A.5
-
15
-
-
0031048845
-
The human mitochondrial transcription termination factor (mTERF) is a multizipper protein but binds to DNA as a monomer, with evidence pointing to intramolecular leucine zipper interactions
-
Fernandez-Silva P., Martinez-Azorin F., Micol V., Attardi G. The human mitochondrial transcription termination factor (mTERF) is a multizipper protein but binds to DNA as a monomer, with evidence pointing to intramolecular leucine zipper interactions. Embo J. 1997, 16:1066-1079.
-
(1997)
Embo J.
, vol.16
, pp. 1066-1079
-
-
Fernandez-Silva, P.1
Martinez-Azorin, F.2
Micol, V.3
Attardi, G.4
-
16
-
-
34147144142
-
Nonsense mutation in pseudouridylate synthase 1 (PUS1) in two brothers affected by myopathy, lactic acidosis and sideroblastic anaemia (MLASA)
-
Fernandez-Vizarra E., Berardinelli A., Valente L., Tiranti V., Zeviani M. Nonsense mutation in pseudouridylate synthase 1 (PUS1) in two brothers affected by myopathy, lactic acidosis and sideroblastic anaemia (MLASA). J. Med. Genet. 2007, 44:173-180.
-
(2007)
J. Med. Genet.
, vol.44
, pp. 173-180
-
-
Fernandez-Vizarra, E.1
Berardinelli, A.2
Valente, L.3
Tiranti, V.4
Zeviani, M.5
-
17
-
-
34447336126
-
Impaired complex III assembly associated with BCS1L gene mutations in isolated mitochondrial encephalopathy
-
Fernandez-Vizarra E., Bugiani M., Goffrini P., Carrara F., Farina L., Procopio E., Donati A., Uziel G., Ferrero I., Zeviani M. Impaired complex III assembly associated with BCS1L gene mutations in isolated mitochondrial encephalopathy. Hum. Mol. Genet. 2007, 16:1241-1252.
-
(2007)
Hum. Mol. Genet.
, vol.16
, pp. 1241-1252
-
-
Fernandez-Vizarra, E.1
Bugiani, M.2
Goffrini, P.3
Carrara, F.4
Farina, L.5
Procopio, E.6
Donati, A.7
Uziel, G.8
Ferrero, I.9
Zeviani, M.10
-
18
-
-
47249148789
-
Mitochondrial gene expression is regulated at multiple levels and differentially in the heart and liver by thyroid hormones
-
Fernandez-Vizarra E., Enriquez J.A., Perez-Martos A., Montoya J., Fernandez-Silva P. Mitochondrial gene expression is regulated at multiple levels and differentially in the heart and liver by thyroid hormones. Curr. Genet. 2008, 54:13-22.
-
(2008)
Curr. Genet.
, vol.54
, pp. 13-22
-
-
Fernandez-Vizarra, E.1
Enriquez, J.A.2
Perez-Martos, A.3
Montoya, J.4
Fernandez-Silva, P.5
-
20
-
-
0036024971
-
Isolation of biogenetically competent mitochondria from mammalian tissues and cultured cells
-
Fernandez-Vizarra E., Lopez-Perez M.J., Enriquez J.A. Isolation of biogenetically competent mitochondria from mammalian tissues and cultured cells. Methods 2002, 26:292-297.
-
(2002)
Methods
, vol.26
, pp. 292-297
-
-
Fernandez-Vizarra, E.1
Lopez-Perez, M.J.2
Enriquez, J.A.3
-
21
-
-
34347236921
-
Organelle isolation: functional mitochondria from mouse liver, muscle and cultured fibroblasts
-
Frezza C., Cipolat S., Scorrano L. Organelle isolation: functional mitochondria from mouse liver, muscle and cultured fibroblasts. Nat. Protoc. 2007, 2:287-295.
-
(2007)
Nat. Protoc.
, vol.2
, pp. 287-295
-
-
Frezza, C.1
Cipolat, S.2
Scorrano, L.3
-
22
-
-
0021736980
-
Highly efficient RNA-synthesizing system that uses isolated human mitochondria: new initiation events and in vivo-like processing patterns
-
Gaines G., Attardi G. Highly efficient RNA-synthesizing system that uses isolated human mitochondria: new initiation events and in vivo-like processing patterns. Mol. Cell Biol. 1984, 4:1605-1617.
-
(1984)
Mol. Cell Biol.
, vol.4
, pp. 1605-1617
-
-
Gaines, G.1
Attardi, G.2
-
23
-
-
0023259258
-
Markedly different ATP requirements for rRNA synthesis and mtDNA light strand transcription versus mRNA synthesis in isolated human mitochondria
-
Gaines G., Rossi C., Attardi G. Markedly different ATP requirements for rRNA synthesis and mtDNA light strand transcription versus mRNA synthesis in isolated human mitochondria. J. Biol. Chem. 1987, 262:1907-1915.
-
(1987)
J. Biol. Chem.
, vol.262
, pp. 1907-1915
-
-
Gaines, G.1
Rossi, C.2
Attardi, G.3
-
24
-
-
0029986874
-
In organello RNA synthesis system from HeLa cells
-
Gaines G.L. In organello RNA synthesis system from HeLa cells. Methods Enzymol. 1996, 264:43-49.
-
(1996)
Methods Enzymol.
, vol.264
, pp. 43-49
-
-
Gaines, G.L.1
-
25
-
-
49649102090
-
Cisplatin-mediated impairment of mitochondrial DNA metabolism inversely correlates with glutathione levels
-
Garrido N., Perez-Martos A., Faro M., Lou-Bonafonte J.M., Fernandez-Silva P., Lopez-Perez M.J., Montoya J., Enriquez J.A. Cisplatin-mediated impairment of mitochondrial DNA metabolism inversely correlates with glutathione levels. Biochem. J. 2008, 414:93-102.
-
(2008)
Biochem. J.
, vol.414
, pp. 93-102
-
-
Garrido, N.1
Perez-Martos, A.2
Faro, M.3
Lou-Bonafonte, J.M.4
Fernandez-Silva, P.5
Lopez-Perez, M.J.6
Montoya, J.7
Enriquez, J.A.8
-
26
-
-
0344012456
-
Import of mitochondrial transcription factor A (TFAM) into rat liver mitochondria stimulates transcription of mitochondrial DNA
-
Garstka H.L., Schmitt W.E., Schultz J., Sogl B., Silakowski B., Perez-Martos A., Montoya J., Wiesner R.J. Import of mitochondrial transcription factor A (TFAM) into rat liver mitochondria stimulates transcription of mitochondrial DNA. Nucleic Acids Res. 2003, 31:5039-5047.
-
(2003)
Nucleic Acids Res.
, vol.31
, pp. 5039-5047
-
-
Garstka, H.L.1
Schmitt, W.E.2
Schultz, J.3
Sogl, B.4
Silakowski, B.5
Perez-Martos, A.6
Montoya, J.7
Wiesner, R.J.8
-
27
-
-
0035444293
-
Mechanism of mammalian mitochondrial DNA replication: import of mitochondrial transcription factor A into isolated mitochondria stimulates 7S DNA synthesis
-
Gensler S., Weber K., Schmitt W.E., Perez-Martos A., Enriquez J.A., Montoya J., Wiesner R.J. Mechanism of mammalian mitochondrial DNA replication: import of mitochondrial transcription factor A into isolated mitochondria stimulates 7S DNA synthesis. Nucleic Acids Res. 2001, 29:3657-3663.
-
(2001)
Nucleic Acids Res.
, vol.29
, pp. 3657-3663
-
-
Gensler, S.1
Weber, K.2
Schmitt, W.E.3
Perez-Martos, A.4
Enriquez, J.A.5
Montoya, J.6
Wiesner, R.J.7
-
28
-
-
50949096038
-
FASTKD2 nonsense mutation in an infantile mitochondrial encephalomyopathy associated with cytochrome C oxidase deficiency
-
Ghezzi D., Saada A., D'Adamo P., Fernandez-Vizarra E., Gasparini P., Tiranti V., Elpeleg O., Zeviani M. FASTKD2 nonsense mutation in an infantile mitochondrial encephalomyopathy associated with cytochrome C oxidase deficiency. Am. J. Hum. Genet. 2008, 83:415-423.
-
(2008)
Am. J. Hum. Genet.
, vol.83
, pp. 415-423
-
-
Ghezzi, D.1
Saada, A.2
D'Adamo, P.3
Fernandez-Vizarra, E.4
Gasparini, P.5
Tiranti, V.6
Elpeleg, O.7
Zeviani, M.8
-
29
-
-
34147164476
-
Biochemical assays of respiratory chain complex activity
-
Kirby D.M., Thorburn D.R., Turnbull D.M., Taylor R.W. Biochemical assays of respiratory chain complex activity. Methods Cell Biol. 2007, 80:93-119.
-
(2007)
Methods Cell Biol.
, vol.80
, pp. 93-119
-
-
Kirby, D.M.1
Thorburn, D.R.2
Turnbull, D.M.3
Taylor, R.W.4
-
30
-
-
33746906633
-
Mitochondria in cancer
-
Kroemer G. Mitochondria in cancer. Oncogene 2006, 25:4630-4632.
-
(2006)
Oncogene
, vol.25
, pp. 4630-4632
-
-
Kroemer, G.1
-
31
-
-
34250164233
-
Analysis of the assembly profiles for mitochondrial- and nuclear-DNA-encoded subunits into complex I
-
Lazarou M., McKenzie M., Ohtake A., Thorburn D.R., Ryan M.T. Analysis of the assembly profiles for mitochondrial- and nuclear-DNA-encoded subunits into complex I. Mol. Cell. Biol. 2007, 27:4228-4237.
-
(2007)
Mol. Cell. Biol.
, vol.27
, pp. 4228-4237
-
-
Lazarou, M.1
McKenzie, M.2
Ohtake, A.3
Thorburn, D.R.4
Ryan, M.T.5
-
32
-
-
0028356648
-
Preparation of synaptosomes and mitochondria from mammalian brain
-
Lopez-Perez M.J. Preparation of synaptosomes and mitochondria from mammalian brain. Methods Enzymol. 1994, 228:403-411.
-
(1994)
Methods Enzymol.
, vol.228
, pp. 403-411
-
-
Lopez-Perez, M.J.1
-
33
-
-
0019879101
-
Highly purified mitochondria from rat brain prepared by phase partition
-
Lopez-Perez M.J., Paris G., Larsson C. Highly purified mitochondria from rat brain prepared by phase partition. Biochim. Biophys. Acta 1981, 635:359-368.
-
(1981)
Biochim. Biophys. Acta
, vol.635
, pp. 359-368
-
-
Lopez-Perez, M.J.1
Paris, G.2
Larsson, C.3
-
34
-
-
3242860254
-
Genomic footprinting of mitochondrial DNA: I. In organello analysis of protein-mitochondrial DNA interactions in bovine mitochondria
-
Madsen C.S., Ghivizzani S.C., Ammini C.V., Nelen M.R., Hauswirth W.W. Genomic footprinting of mitochondrial DNA: I. In organello analysis of protein-mitochondrial DNA interactions in bovine mitochondria. Methods Enzymol. 1996, 264:12-22.
-
(1996)
Methods Enzymol.
, vol.264
, pp. 12-22
-
-
Madsen, C.S.1
Ghivizzani, S.C.2
Ammini, C.V.3
Nelen, M.R.4
Hauswirth, W.W.5
-
35
-
-
45449121006
-
Severe infantile encephalomyopathy caused by a mutation in COX6B1, a nucleus-encoded subunit of cytochrome c oxidase
-
Massa V., Fernandez-Vizarra E., Alshahwan S., Bakhsh E., Goffrini P., Ferrero I., Mereghetti P., D'Adamo P., Gasparini P., Zeviani M. Severe infantile encephalomyopathy caused by a mutation in COX6B1, a nucleus-encoded subunit of cytochrome c oxidase. Am. J. Hum. Genet. 2008, 82:1281-1289.
-
(2008)
Am. J. Hum. Genet.
, vol.82
, pp. 1281-1289
-
-
Massa, V.1
Fernandez-Vizarra, E.2
Alshahwan, S.3
Bakhsh, E.4
Goffrini, P.5
Ferrero, I.6
Mereghetti, P.7
D'Adamo, P.8
Gasparini, P.9
Zeviani, M.10
-
36
-
-
1842339276
-
Functional analysis of in vivo and in organello footprinting of HeLa cell mitochondrial DNA in relationship to ATP and ethidium bromide effects on transcription
-
Micol V., Fernandez-Silva P., Attardi G. Functional analysis of in vivo and in organello footprinting of HeLa cell mitochondrial DNA in relationship to ATP and ethidium bromide effects on transcription. J. Biol. Chem. 1997, 272:18896-18904.
-
(1997)
J. Biol. Chem.
, vol.272
, pp. 18896-18904
-
-
Micol, V.1
Fernandez-Silva, P.2
Attardi, G.3
-
37
-
-
33750428601
-
Differences in reactive oxygen species production explain the phenotypes associated with common mouse mitochondrial DNA variants
-
Moreno-Loshuertos R., Acin-Perez R., Fernandez-Silva P., Movilla N., Perez-Martos A., Rodriguez de Cordoba S., Gallardo M.E., Enriquez J.A. Differences in reactive oxygen species production explain the phenotypes associated with common mouse mitochondrial DNA variants. Nat. Genet. 2006, 38:1261-1268.
-
(2006)
Nat. Genet.
, vol.38
, pp. 1261-1268
-
-
Moreno-Loshuertos, R.1
Acin-Perez, R.2
Fernandez-Silva, P.3
Movilla, N.4
Perez-Martos, A.5
Rodriguez de Cordoba, S.6
Gallardo, M.E.7
Enriquez, J.A.8
-
38
-
-
77956998789
-
Isolation of golgi apparatus
-
Morre D.J. Isolation of golgi apparatus. Methods Enzymol. 1971, 31:130-148.
-
(1971)
Methods Enzymol.
, vol.31
, pp. 130-148
-
-
Morre, D.J.1
-
39
-
-
77949914150
-
Mitochondrial dysfunction in pancreatic beta-cells in Type 2 Diabetes
-
Mulder H., Ling C. Mitochondrial dysfunction in pancreatic beta-cells in Type 2 Diabetes. Mol. Cell. Endocrinol. 2008.
-
(2008)
Mol. Cell. Endocrinol.
-
-
Mulder, H.1
Ling, C.2
-
40
-
-
0014590212
-
Studies on 2′, 3′-cyclic nucleotide-3′-phosphohydrolase from brain
-
Olafson R.W., Drummond G.I., Lee J.F. Studies on 2′, 3′-cyclic nucleotide-3′-phosphohydrolase from brain. Can. J. Biochem. 1969, 47:961-966.
-
(1969)
Can. J. Biochem.
, vol.47
, pp. 961-966
-
-
Olafson, R.W.1
Drummond, G.I.2
Lee, J.F.3
-
41
-
-
0035227198
-
Isolation and subfractionation of mitochondria from animal cells and tissue culture lines
-
Pallotti F., Lenaz G. Isolation and subfractionation of mitochondria from animal cells and tissue culture lines. Methods Cell Biol. 2001, 65:1-35.
-
(2001)
Methods Cell Biol.
, vol.65
, pp. 1-35
-
-
Pallotti, F.1
Lenaz, G.2
-
42
-
-
34147143391
-
Isolation and subfractionation of mitochondria from animal cells and tissue culture lines
-
Pallotti F., Lenaz G. Isolation and subfractionation of mitochondria from animal cells and tissue culture lines. Methods Cell Biol. 2007, 80:3-44.
-
(2007)
Methods Cell Biol.
, vol.80
, pp. 3-44
-
-
Pallotti, F.1
Lenaz, G.2
-
43
-
-
57749093494
-
Restoration of electron transport without proton pumping in mammalian mitochondria
-
Perales-Clemente E., Bayona-Bafaluy M.P., Perez-Martos A., Barrientos A., Fernandez-Silva P., Enriquez J.A. Restoration of electron transport without proton pumping in mammalian mitochondria. Proc. Natl. Acad. Sci. USA 2008, 105:18735-18739.
-
(2008)
Proc. Natl. Acad. Sci. USA
, vol.105
, pp. 18735-18739
-
-
Perales-Clemente, E.1
Bayona-Bafaluy, M.P.2
Perez-Martos, A.3
Barrientos, A.4
Fernandez-Silva, P.5
Enriquez, J.A.6
-
44
-
-
34250656608
-
Mitochondria and neurodegeneration
-
Petrozzi L., Ricci G., Giglioli N.J., Siciliano G., Mancuso M. Mitochondria and neurodegeneration. Biosci. Rep. 2007, 27:87-104.
-
(2007)
Biosci. Rep.
, vol.27
, pp. 87-104
-
-
Petrozzi, L.1
Ricci, G.2
Giglioli, N.J.3
Siciliano, G.4
Mancuso, M.5
-
45
-
-
0032534869
-
Identification and characterization of human cDNAs specific to BCS1, PET 112, SCO1, COX15, and COX11, five genes involved in the formation and function of the mitochondrial respiratory chain
-
Petruzzella V., Tiranti V., Fernandez P., Ianna P., Carrozzo R., Zeviani M. Identification and characterization of human cDNAs specific to BCS1, PET 112, SCO1, COX15, and COX11, five genes involved in the formation and function of the mitochondrial respiratory chain. Genomics 1998, 54:494-504.
-
(1998)
Genomics
, vol.54
, pp. 494-504
-
-
Petruzzella, V.1
Tiranti, V.2
Fernandez, P.3
Ianna, P.4
Carrozzo, R.5
Zeviani, M.6
-
46
-
-
0001883657
-
Isolation and characteristics of intact mitochondria
-
IRL Press, Oxford, Washington, DC, V.M.R.D.W.M.T. Darley-Usmar (Ed.)
-
Rickwood D., Wilson M.T., Darley-Usmar V.M. Isolation and characteristics of intact mitochondria. Mitochondria: A Practical Approach 1987, 1-16. IRL Press, Oxford, Washington, DC. V.M.R.D.W.M.T. Darley-Usmar (Ed.).
-
(1987)
Mitochondria: A Practical Approach
, pp. 1-16
-
-
Rickwood, D.1
Wilson, M.T.2
Darley-Usmar, V.M.3
-
48
-
-
0029924286
-
Electrophoretic techniques for isolation and quantification of oxidative phosphorylation complexes from human tissues
-
Schagger H. Electrophoretic techniques for isolation and quantification of oxidative phosphorylation complexes from human tissues. Methods Enzymol. 1996, 264:555-566.
-
(1996)
Methods Enzymol.
, vol.264
, pp. 555-566
-
-
Schagger, H.1
-
49
-
-
33646376465
-
MPV17 encodes an inner mitochondrial membrane protein and is mutated in infantile hepatic mitochondrial DNA depletion
-
Spinazzola A., Viscomi C., Fernandez-Vizarra E., Carrara F., D'Adamo P., Calvo S., Marsano R.M., Donnini C., Weiher H., Strisciuglio P., Parini R., Sarzi E., Chan A., DiMauro S., Rotig A., Gasparini P., Ferrero I., Mootha V.K., Tiranti V., Zeviani M. MPV17 encodes an inner mitochondrial membrane protein and is mutated in infantile hepatic mitochondrial DNA depletion. Nat. Genet. 2006, 38:570-575.
-
(2006)
Nat. Genet.
, vol.38
, pp. 570-575
-
-
Spinazzola, A.1
Viscomi, C.2
Fernandez-Vizarra, E.3
Carrara, F.4
D'Adamo, P.5
Calvo, S.6
Marsano, R.M.7
Donnini, C.8
Weiher, H.9
Strisciuglio, P.10
Parini, R.11
Sarzi, E.12
Chan, A.13
DiMauro, S.14
Rotig, A.15
Gasparini, P.16
Ferrero, I.17
Mootha, V.K.18
Tiranti, V.19
Zeviani, M.20
more..
-
50
-
-
77957010982
-
Citrate synthase
-
Srere P.A. Citrate synthase. Methods Enzymol. 1969, 13:3-11.
-
(1969)
Methods Enzymol.
, vol.13
, pp. 3-11
-
-
Srere, P.A.1
-
51
-
-
0016370516
-
Isolation of modified liver lysosomes
-
Trouet A. Isolation of modified liver lysosomes. Methods Enzymol. 1974, 31:323-329.
-
(1974)
Methods Enzymol.
, vol.31
, pp. 323-329
-
-
Trouet, A.1
-
52
-
-
57649181749
-
Early-onset liver mtDNA depletion and late-onset proteinuric nephropathy in Mpv17 knockout mice
-
Viscomi C., Spinazzola A., Maggioni M., Fernandez-Vizarra E., Massa V., Pagano C., Vettor R., Mora M., Zeviani M. Early-onset liver mtDNA depletion and late-onset proteinuric nephropathy in Mpv17 knockout mice. Hum. Mol. Genet. 2009, 18:12-26.
-
(2009)
Hum. Mol. Genet.
, vol.18
, pp. 12-26
-
-
Viscomi, C.1
Spinazzola, A.2
Maggioni, M.3
Fernandez-Vizarra, E.4
Massa, V.5
Pagano, C.6
Vettor, R.7
Mora, M.8
Zeviani, M.9
-
53
-
-
27144528747
-
Human mitochondrial complex I assembly is mediated by NDUFAF1
-
Vogel R.O., Janssen R.J., Ugalde C., Grovenstein M., Huijbens R.J., Visch H.J., van den Heuvel L.P., Willems P.H., Zeviani M., Smeitink J.A., Nijtmans L.G. Human mitochondrial complex I assembly is mediated by NDUFAF1. FEBS J. 2005, 272:5317-5326.
-
(2005)
FEBS J.
, vol.272
, pp. 5317-5326
-
-
Vogel, R.O.1
Janssen, R.J.2
Ugalde, C.3
Grovenstein, M.4
Huijbens, R.J.5
Visch, H.J.6
van den Heuvel, L.P.7
Willems, P.H.8
Zeviani, M.9
Smeitink, J.A.10
Nijtmans, L.G.11
-
54
-
-
2042432480
-
Cytochrome oxidase from beef heart mitochondria
-
Wharton D.C., Tzagoloff A. Cytochrome oxidase from beef heart mitochondria. Methods Enzymol. 1967, 10:245-250.
-
(1967)
Methods Enzymol.
, vol.10
, pp. 245-250
-
-
Wharton, D.C.1
Tzagoloff, A.2
-
55
-
-
0027488803
-
Thirty years of synaptosome research
-
Whittaker V.P. Thirty years of synaptosome research. J. Neurocytol. 1993, 22:735-742.
-
(1993)
J. Neurocytol.
, vol.22
, pp. 735-742
-
-
Whittaker, V.P.1
-
56
-
-
2442555970
-
The protein import machinery of mitochondria
-
Wiedemann N., Frazier A.E., Pfanner N. The protein import machinery of mitochondria. J. Biol. Chem. 2004, 279:14473-14476.
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 14473-14476
-
-
Wiedemann, N.1
Frazier, A.E.2
Pfanner, N.3
-
59
-
-
4944260285
-
Mitochondrial disorders
-
Zeviani M., Di Donato S. Mitochondrial disorders. Brain 2004, 127:2153-2172.
-
(2004)
Brain
, vol.127
, pp. 2153-2172
-
-
Zeviani, M.1
Di Donato, S.2
|