Abnormal intermediate filament organization alters mitochondrial motility in giant axonal neuropathy fibroblasts

Molecular Biology of the Cell

Volumn 27, Issue 4, 2016, Pages 608-616

  Lowery, Jason ^a   Jain, Nikhil ^a   Kuczmarski, Edward R ^a   Mahammad, Saleemulla ^b   Goldman, Anne ^a   Gelfand, Vladimir I ^a   Opal, Puneet ^c   Goldman, Robert D ^a  

^a ETH ZURICH   (Switzerland)

^b MCMASTER UNIVERSITY   (Canada)

^c NORTHWESTERN UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

GIGAXONIN; UBIQUITIN PROTEIN LIGASE E3; UNCLASSIFIED DRUG; VIMENTIN; CYTOSKELETON PROTEIN; GAN PROTEIN, HUMAN; SMALL INTERFERING RNA;

ACTIN FILAMENT; ARTICLE; BRAIN MITOCHONDRION; CELL ORGANELLE; CONTROLLED STUDY; FIBROBLAST; GIANT AXONAL NEUROPATHY; HUMAN; HUMAN CELL; INTERMEDIATE FILAMENT; LYSOSOME; MICROTUBULE; MITOCHONDRIAL DYNAMICS; PRIORITY JOURNAL; PROTEIN AGGREGATION; TRANSIENT EXPRESSION; WILD TYPE; CELL LINE; GENETICS; METABOLISM; MITOCHONDRION; MUTATION; PATHOPHYSIOLOGY; PRIMARY CELL CULTURE; RNA INTERFERENCE;

CELL LINE; CYTOSKELETAL PROTEINS; FIBROBLASTS; GIANT AXONAL NEUROPATHY; HUMANS; INTERMEDIATE FILAMENTS; LYSOSOMES; MICROTUBULES; MITOCHONDRIA; MITOCHONDRIAL DYNAMICS; MUTATION; PRIMARY CELL CULTURE; RNA INTERFERENCE; RNA, SMALL INTERFERING; VIMENTIN;

EID: 84958626040     PISSN: 10591524     EISSN: 19394586     Source Type: Journal    
DOI: 10.1091/mbc.E15-09-0627     Document Type: Article

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