Neutrophilic dermatoses and autoinflammatory diseases with skin involvement—innate immune disorders

Seminars in Immunopathology

Volumn 38, Issue 1, 2016, Pages 45-56

  Navarini, Alexander A ^a   Satoh, Takashi K ^a   French, Lars E ^a  

^a UNIVERSITY HOSPITAL ZURICH   (Switzerland)

Author keywords

Autoinflammatory; Classification; Granulocyte; IL 1; Innate immune disorders; Merging; Neutrophil; Pustular; Skin

Indexed keywords

CRYOPYRIN; IMMUNOGLOBULIN ENHANCER BINDING PROTEIN; INTERFERON; INTERLEUKIN 1;

ACUTE FEBRILE NEUTROPHILIC DERMATOSIS; AICARDI GOUTIERES SYNDROME; AUTOIMMUNE DISEASE; AUTOINFLAMMATORY DISEASE; BLAU SYNDROME; CARD ASSOCIATED PUSTULAR PSORIASIS; CHRONIC ATYPICAL NEUTROPHILIC DERMATOSIS WITH LIPODYSTROPHYAND ELEVATED TEMPERATURE SYNDROME; CINCA SYNDROME; CLINICAL FEATURE; DEFICIENCY OF ADENOSINE DEAMINASE 2; DEFICIENCY OF INTERFERON 1 RECEPTOR ANTAGONIST; DEFICIENCY OF INTERLEUKIN 36 RECEPTOR ANTAGONIST; DEFICIENCY OF X LINKED INHIBITOR OF APOPTOSIS; DISEASE ASSOCIATION; DISEASE CLASSIFICATION; DISEASE PREDISPOSITION; EARLY ONSET INFLAMMATORY BOWEL DISEASE; ERYTHEMA ELEVATUM DIUTINUM; FAMILIAL MEDITERRANEAN FEVER; FIBROUS DYSPLASIA; GAMMOPATHY; GENE MUTATION; HUMAN; HYPERIMMUNOGLOBULINEMIA D AND PERIODIC FEVER SYNDROME; IMMUNOPATHOGENESIS; IMMUNOPATHOLOGY; INFLAMMATORY BOWEL DISEASE; INNATE IMMUNITY; LYN ASSOCIATED AUTOINFLAMMATORY DISEASE; MACROPHAGE ACTIVATION SYNDROME; MAJEED SYNDROME; MEVALONATE KINASE DEFICIENCY; NEUTROPHILIC DERMATOSIS; PAPA SYNDROME; PEDIATRIC GRANULOMATOUS ARTHRITIS; PLCGAMMA2 ASSOCIATED ANTIBODY DEFICIENCY AND IMMUNE DYSREGULATION AND AUTOINFLAMMATION; PRIORITY JOURNAL; PROTEASOME ASSOCIATED AUTOINFLAMMATORY SYNDROME; PYODERMA GANGRENOSUM; REVIEW; SCHNITZLER SYNDROME; SIDEROBLASTIC ANEMIA IMMUNODEFICIENCY FEVER AND DEVELOPMENTAL DELAY; SKIN DISEASE; SPONDYLOENCHONDROPLASIA WITH IMMUNE DYSREGULATION; STING ASSOCIATED VASCULOPATHY WITH ONSET IN INFANCY; SUBCORNEAL PUSTULAR DERMATOSIS; TUMOR NECROSIS FACTOR RECEPTOR ASSOCIATED PERIODIC SYNDROME; WALDENSTROEM MACROGLOBULINEMIA; ANIMAL; AUTOIMMUNE DISEASES; AUTOIMMUNITY; DERMATITIS; IMMUNOLOGY; MACROPHAGE; MACROPHAGE ACTIVATION; METABOLISM; NEUTROPHIL; SIGNAL TRANSDUCTION; SWEET SYNDROME;

ANIMALS; AUTOIMMUNE DISEASES; AUTOIMMUNITY; DERMATITIS; DISEASE SUSCEPTIBILITY; HUMANS; IMMUNITY, INNATE; INTERFERONS; INTERLEUKIN-1; MACROPHAGE ACTIVATION; MACROPHAGES; NEUTROPHILS; NF-KAPPA B; SIGNAL TRANSDUCTION; SWEET SYNDROME;

EID: 84953638825     PISSN: 18632297     EISSN: 18632300     Source Type: Journal    
DOI: 10.1007/s00281-015-0549-6     Document Type: Review

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