Anakinra for flares of pyogenic arthritis in PAPA syndrome [5]

Rheumatology

Volumn 44, Issue 3, 2005, Pages 406-408

  Dierselhuis, M P ^a   Frenkel, J ^a   Wulffraat, N M ^a   Boelens, J J ^a  

^a UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

BINDING PROTEIN; CD2 ANTIGEN; INTERLEUKIN 1BETA; RECOMBINANT INTERLEUKIN 1 RECEPTOR BLOCKING AGENT; STEROID; TRIAMCINOLONE HEXACETONIDE;

ACNE; ADOLESCENT; ARTHRITIS; AUTOSOMAL DOMINANT DISORDER; BACTERIAL ARTHRITIS; CASE REPORT; CLINICAL FEATURE; DISEASE COURSE; DISEASE EXACERBATION; DRUG EFFICACY; GENE MUTATION; HUMAN; LABORATORY TEST; LETTER; MALE; PATIENT REFERRAL; PHYSICAL EXAMINATION; PRIORITY JOURNAL; PYODERMA GANGRENOSUM; TREATMENT OUTCOME;

ACNE VULGARIS; ADOLESCENT; ANTIRHEUMATIC AGENTS; ARTHRITIS, INFECTIOUS; HUMANS; INTERLEUKIN 1 RECEPTOR ANTAGONIST PROTEIN; MALE; PYODERMA GANGRENOSUM; RECEPTORS, INTERLEUKIN-1; SIALOGLYCOPROTEINS; SYNDROME;

EID: 14944380059     PISSN: 14620324     EISSN: None     Source Type: Journal    
DOI: 10.1093/rheumatology/keh479     Document Type: Letter

References (9)

1. Wise CA, Gillum JD, Seidman CE et al. Mutations in CD2BP1 disrupt binding to PTP PEST and are responsible for PAPA syndrome, an autoinflammatory disorder. Human Mol Gen 2002;11: 961-9.
2. Jacobs JC, Goetzl EJ. 'Streaking leukocyte factor', arthritis and pyoderma gangrenosum. Paediatrics 1975;56:570-8.
3. Lindor NM, Arsenault TM, Solomon H, Seidman CE, McEvoy MT. A new autosomal dominant disorder of pyogenic sterile arthritis, pyoderma gangrenosum, and acne: PAPA syndrome. Mayo Clin Proc 1997;72:611-5.
4. Shoham NG, Centola M, Mansfield E et al. Pyrin binds the PSTPIP1/CD2BP1 protein, defining familial Mediterranean fever and PAPA syndrome as disorders in the same pathway. Proc Natl Acad Sci USA 2003;100:13501-6.
5. McDermott MF. A common pathway in periodic fever syndromes. Trends Immunol 2004;9:457-60.
6. Galon J, Aksentijevich I, McDermott MF et al. TNFRSFIA mutations and autoinflammatory syndromes. Curr Opin Immunol 2000;12:479-86.
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8. Hoffman HM, Patel DD. Genomic-based therapy: targeting interleukin-1 for autoinflammatory diseases. Arthritis Rheum 2004;50:345-9.
9. Hawkins PN, Lachmann HJ, Aganna E, McDermott MF. Spectrum of clinical features in Muckle-Wells Syndrome and response to anakinra. Arthritis Rheum 2004;50:607-12.