ADAMTS13 secretion and residual activity among patients with congenital thrombotic thrombocytopenic purpura with and without renal impairment

Clinical Journal of the American Society of Nephrology

Volumn 10, Issue 11, 2015, Pages 2002-2012

  Rurali, Erica ^a   Banterla, Federica ^a   Donadelli, Roberta ^a   Bresin, Elena ^a   Galbusera, Miriam ^a   Gastoldi, Sara ^a   Peyvandi, Flora ^b   Underwood, Mary ^b   Remuzzi, Giuseppe ^a,b,c   Noris, Marina ^a  

^a MARIO NEGRI INST PHARMACOL RES   (Italy)

^b UNIVERSITY OF MILAN   (Italy)

^c Azienda Ospedaliera Papa Giovanni XXIII   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

COLLAGEN BINDING PROTEIN; COMPLEMENT FACTOR H; COMPLEMENT FACTOR I; MEMBRANE COFACTOR PROTEIN; MUTANT PROTEIN; VON WILLEBRAND FACTOR CLEAVING PROTEINASE; ADAM PROTEIN; ADAMTS13 PROTEIN, HUMAN;

ADOLESCENT; ADULT; ARTICLE; CHILD; CHRONIC KIDNEY DISEASE; CLINICAL ARTICLE; DISEASE ASSOCIATION; ENZYME ACTIVITY; FEMALE; FLUORESCENCE RESONANCE ENERGY TRANSFER; GENE SEQUENCE; GENETIC ASSOCIATION; HEK293 CELL LINE; HUMAN; HUMAN CELL; INFANT; KIDNEY FAILURE; MALE; PHENOTYPE; PROTEIN EXPRESSION; THROMBOTIC THROMBOCYTOPENIC PURPURA; BLOOD; COMPLICATION; GENETICS; MIDDLE AGED; MUTATION; NEWBORN; PHYSIOLOGY; PRESCHOOL CHILD; SECRETION (PROCESS); YOUNG ADULT;

ADAM PROTEINS; ADAMTS13 PROTEIN; ADOLESCENT; ADULT; CHILD; CHILD, PRESCHOOL; FEMALE; HUMANS; INFANT; INFANT, NEWBORN; MALE; MIDDLE AGED; MUTATION; PURPURA, THROMBOTIC THROMBOCYTOPENIC; RENAL INSUFFICIENCY; YOUNG ADULT;

EID: 84946723554     PISSN: 15559041     EISSN: 1555905X     Source Type: Journal    
DOI: 10.2215/CJN.01700215     Document Type: Article

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