Increased fragmentation of von Willebrand factor, due to abnormal cleavage of the subunit, parallels disease activity in recurrent hemolytic uremic syndrome and thrombotic thrombocytopenic purpura and discloses predisposition in families

Blood

Volumn 94, Issue 2, 1999, Pages 610-620

  Galbusera, Miriam ^b   Noris, Marina ^b   Rossi, Chiara ^b   Orisio, Silvia ^b   Caprioli, Jessica ^b   Ruggeri, Zaverio M ^b   Amadei, Barbara ^b   Ruggenenti, Piero ^b   Vasile, Beatrice ^b   Casari, Giorgio ^b   Remuzzi, Giuseppe ^a  

^a MARIO NEGRI INST PHARMACOL RES   (Italy)

^b NONE

Author keywords

[No Author keywords available]

Indexed keywords

DNA; VON WILLEBRAND FACTOR;

ADOLESCENT; ADULT; ARTICLE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; DISEASE PREDISPOSITION; DNA DETERMINATION; FAMILIAL DISEASE; FEMALE; GENETIC LINKAGE; HEMOLYTIC UREMIC SYNDROME; HUMAN; HUMAN CELL; HUMAN TISSUE; MALE; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN POLYMERIZATION; RECURRENT DISEASE; THROMBOSIS; THROMBOTIC THROMBOCYTOPENIC PURPURA;

EID: 0033566356     PISSN: 00064971     EISSN: None     Source Type: Journal    
DOI: 10.1182/blood.v94.2.610     Document Type: Article

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