Inherited thrombotic thrombocytopenic purpura in children

Seminars in Thrombosis and Hemostasis

Volumn 40, Issue 4, 2014, Pages 487-492

  Hassenpflug, Wolf Achim ^a   Budde, Ulrich ^b   Schneppenheim, Sonja ^b   Schneppenheim, Reinhard ^a  

^a UNIVERSITY MEDICAL CENTER HAMBURG EPPENDORF   (Germany)

^b Coagulation Laboratory   (Germany)

Author keywords

ADAMTS 13; molecular genetics; thrombotic thrombocytopenic purpura; Upshaw Schulman syndrome; von Willebrand factor

Indexed keywords

VON WILLEBRAND FACTOR CLEAVING PROTEINASE; ADAM PROTEIN; ADAMTS13 PROTEIN, HUMAN;

ARTICLE; AUTOIMMUNE HEMOLYTIC ANEMIA; CENTRAL NERVOUS SYSTEM; CHILD; CHILDHOOD DISEASE; CHRONIC KIDNEY DISEASE; CLINICAL ARTICLE; EARLY DIAGNOSIS; ENZYME ACTIVITY; ERYTHROCYTE TRANSFUSION; FEMALE; GENOTYPE; GERMANY; HEMOLYTIC ANEMIA; HEMOLYTIC UREMIC SYNDROME; HUMAN; HYPERBILIRUBINEMIA; KIDNEY FUNCTION; MALE; MOLECULAR GENETICS; NEONATAL THROMBOCYTOPENIA; PHENOTYPE; PLASMA TRANSFUSION; PRIORITY JOURNAL; THROMBOCYTE COUNT; THROMBOTIC THROMBOCYTOPENIC PURPURA; ADOLESCENT; ADULT; CENTRAL NERVOUS SYSTEM DISEASE; DEFICIENCY; GENETIC ASSOCIATION; GENETICS; INFANT; INFLAMMATION; MUTATION; NEWBORN; PRESCHOOL CHILD; PURPURA, THROMBOTIC THROMBOCYTOPENIC; YOUNG ADULT;

ADAM PROTEINS; ADOLESCENT; ADULT; CENTRAL NERVOUS SYSTEM DISEASES; CHILD; CHILD, PRESCHOOL; FEMALE; GENETIC ASSOCIATION STUDIES; HUMANS; INFANT; INFANT, NEWBORN; INFLAMMATION; MALE; MUTATION; PURPURA, THROMBOTIC THROMBOCYTOPENIC; YOUNG ADULT;

EID: 84902277744     PISSN: 00946176     EISSN: 10989064     Source Type: Journal    
DOI: 10.1055/s-0034-1376152     Document Type: Article

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