Hepatopulmonary syndrome is a frequent cause of dyspnea in the short telomere disorders

Chest

Volumn 148, Issue 4, 2015, Pages 1019-1026

  Gorgy, Amany I ^a   Jonassaint, Naudia L ^a   Stanley, Susan E ^a   Koteish, Ayman ^a   DeZern, Amy E ^a   Walter, Jolan E ^b   Sopha, Sabrina C ^a   Hamilton, James P ^a   Hoover Fong, Julie ^a   Chen, Allen R ^a   Anders, Robert A ^a   Kamel, Ihab R ^a   Armanios, Mary ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b MASSACHUSETTS GENERAL HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

TELOMERASE;

ADULT; AGE; AGED; ARTICLE; CHROMOSOME DISORDER; CONGENITAL BLOOD VESSEL MALFORMATION; CONTROLLED STUDY; DYSKERATOSIS CONGENITA; DYSPNEA; EMPHYSEMA; FEMALE; GENE MUTATION; HEPATOPULMONARY SYNDROME; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; HYPERPLASIA; HYPOXIA; LIVER TRANSPLANTATION; LUNG FIBROSIS; MAJOR CLINICAL STUDY; MALE; MORTALITY; NODULAR REGENERATIVE HYPERPLASIA; PORTAL HYPERTENSION; PRIORITY JOURNAL; TELOMERE; TELOMERE SYNDROME; ADOLESCENT; COMPLICATION; GENETICS; HETEROZYGOTE; METABOLISM; MIDDLE AGED; MUTATION; RETROSPECTIVE STUDY; TELOMERE HOMEOSTASIS;

ADOLESCENT; ADULT; AGED; DYSPNEA; FEMALE; HEPATOPULMONARY SYNDROME; HETEROZYGOTE; HUMANS; MALE; MIDDLE AGED; MUTATION; RETROSPECTIVE STUDIES; TELOMERASE; TELOMERE; TELOMERE HOMEOSTASIS;

EID: 84943381247     PISSN: 00123692     EISSN: 19313543     Source Type: Journal    
DOI: 10.1378/chest.15-0825     Document Type: Article

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