Liver failure due to hepatic angiosarcoma in an adolescent with dyskeratosis congenita

Journal of Pediatric Hematology/Oncology

Volumn 36, Issue 4, 2014, Pages 312-315

  Olson, Timothy S ^a,b,d   Chan, Elaine S ^d   Paessler, Michele E ^d   Sullivan, Kathleen E ^c   Frantz, Christopher N ^e   Russo, Piere ^d   Bessler, Monica ^a,f  

^a Division of Hematology   (United States)

^b Division of Oncology   (United States)

^c Dept of Pathol   (United States)

^d CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

^e UNIVERSITY OF PENNSYLVANIA   (United States)

^f NEMOURS ALFRED I DUPONT HOSPITAL FOR CHILDREN   (United States)

Author keywords

angiosarcoma; bone marrow failure; dyskeratosis congenita; liver failure; pediatric

Indexed keywords

ALKALINE PHOSPHATASE; BILIRUBIN; GAMMA GLUTAMYLTRANSFERASE; INFLIXIMAB; STEROID;

ADOLESCENT; ANASARCA; ANGIOSARCOMA; ARTICLE; BILE DUCT DILATATION; BLEEDING; BLOOD CLOTTING DISORDER; CASE REPORT; CD8+ T LYMPHOCYTE; CHOLESTASIS; DKC1 GENE; DYSKERATOSIS CONGENITA; ECHOGRAPHY; ENTEROCOLITIS; GENE MUTATION; HEMOSIDEROSIS; HEPATORENAL SYNDROME; HERPES SIMPLEX; HUMAN; HUMAN TISSUE; HYPERBILIRUBINEMIA; IMMUNOGLOBULIN DEFICIENCY; IMMUNOTHERAPY; LIVER CIRRHOSIS; LIVER FAILURE; LIVER HEMANGIOSARCOMA; LIVER TOXICITY; LUNG INFECTION; LYMPHOCYTE COUNT; MALE; MUCOSAL BLEEDING; MULTIPLE ORGAN FAILURE; MUTATOR GENE; NEUTROPHIL COUNT; OROPHARYNGEAL BLEEDING; PORTAL VEIN BLOOD PRESSURE; PRIORITY JOURNAL; RESPIRATION CONTROL; RESPIRATORY FAILURE; ROTAVIRUS INFECTION; SUBSTITUTION THERAPY; THROMBOCYTE TRANSFUSION; TRACHEOSTOMY; TRISMUS;

ADOLESCENT; DYSKERATOSIS CONGENITA; HEMANGIOSARCOMA; HUMANS; LIVER FAILURE; LIVER NEOPLASMS; MALE;

EID: 84899935655     PISSN: 10774114     EISSN: 15363678     Source Type: Journal    
DOI: 10.1097/MPH.0b013e318286d4d4     Document Type: Article

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