Cyanosis revealing hepatopulmonary syndrome in a child with dyskeratosis congenita

Pediatric Pulmonology

Volumn 45, Issue 1, 2010, Pages 99-102

  Renoux, M C ^a   Mazars, N ^a   Tichit, R ^a   Counil, F ^a  

^a HÔPITAL ARNAUD DE VILLENEUVE   (France)

Author keywords

Hypoxemia; Liver disease; Zinsser Cole Engman syndrome

Indexed keywords

CYCLOPHOSPHAMIDE; FLUDARABINE; LYMPHOCYTE ANTIBODY; MACROSALB TC 99M; TELOMERIC REPEAT BINDING FACTOR 1;

ALLOGENIC BONE MARROW TRANSPLANTATION; ARTICLE; CASE REPORT; CHILD; CHOLESTASIS; CYANOSIS; CYTOLYSIS; DYSKERATOSIS CONGENITA; DYSPNEA; EXERCISE; GENE MUTATION; HEPATOPULMONARY SYNDROME; HUMAN; HYPOXEMIA; LIVER DISEASE; LIVER FUNCTION TEST; LIVER TRANSPLANTATION; LUNG ALVEOLUS OXYGEN TENSION; MALE; OXYGEN THERAPY; PRESCHOOL CHILD; PRIORITY JOURNAL;

ANOXIA; BLOOD GAS ANALYSIS; CHILD, PRESCHOOL; CYANOSIS; DYSKERATOSIS CONGENITA; DYSPNEA; HEPATOPULMONARY SYNDROME; HUMANS; LIVER FUNCTION TESTS; LUNG; MALE; OXYGEN INHALATION THERAPY; RADIOPHARMACEUTICALS; TECHNETIUM TC 99M AGGREGATED ALBUMIN; TOMOGRAPHY, X-RAY COMPUTED;

EID: 74249122478     PISSN: 87556863     EISSN: 10990496     Source Type: Journal    
DOI: 10.1002/ppul.21128     Document Type: Article

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