Prognostic factors and long-term outcome in 52 Turkish children with hemophagocytic lymphohistiocytosis

Pediatric Critical Care Medicine

Volumn 16, Issue 6, 2015, Pages e165-e173

  Kaya, Zühre ^a   Bay, Ali ^b   Albayrak, Meryem ^c   Kocak, Ulker ^a   Yenicesu, Idil ^a   Gursel, Turkiz ^a  

^a GAZI UNIVERSITY   (Turkey)

^b GAZIANTEP UNIVERSITY   (Turkey)

^c KIRIKKALE UNIVERSITY   (Turkey)

Author keywords

children; hemophagocytic syndrome; prognosis

Indexed keywords

ANTIBIOTIC AGENT; ANTIFUNGAL AGENT; ANTIVIRUS AGENT; CORTICOSTEROID; IMMUNOGLOBULIN; PEPTIDES AND PROTEINS; PERFORIN; PRF1 PROTEIN; STX11 PROTEIN; STXBP2 PROTEIN; UNC13D PROTEIN; UNCLASSIFIED DRUG; MEMBRANE PROTEIN; MUNC18 PROTEIN; PRF1 PROTEIN, HUMAN; STX11 PROTEIN, HUMAN; STXBP2 PROTEIN, HUMAN; SYNTAXIN; UNC13D PROTEIN, HUMAN;

ALLOGENEIC STEM CELL TRANSPLANTATION; ARTICLE; CHILD; CLINICAL FEATURE; CORTICOSTEROID THERAPY; DIET THERAPY; DISSEMINATED INTRAVASCULAR CLOTTING; DRUG MEGADOSE; FEMALE; GENE MUTATION; GENETIC ANALYSIS; HEMOPHAGOCYTIC SYNDROME; HIGH RISK PATIENT; HUMAN; HYPERFERRITINEMIA; LABORATORY TEST; LYSINURIC PROTEIN INTOLERANCE; MAJOR CLINICAL STUDY; MALE; MEDICAL RECORD REVIEW; MORTALITY; OUTCOME ASSESSMENT; PRIORITY JOURNAL; PROGNOSIS; RISK ASSESSMENT; SURVIVAL RATE; THROMBOCYTOPENIA; TREATMENT RESPONSE; TURK (PEOPLE); CLINICAL TRIAL; DISSEMINATED INTRAVASCULAR COAGULATION; GENETICS; INFANT; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MICROBIOLOGY; MULTICENTER STUDY; PRESCHOOL CHILD; RETROSPECTIVE STUDY; TIME; TREATMENT OUTCOME; TURKEY;

CHILD; CHILD, PRESCHOOL; DISSEMINATED INTRAVASCULAR COAGULATION; FEMALE; HUMANS; INFANT; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MALE; MEMBRANE PROTEINS; MUNC18 PROTEINS; PERFORIN; PROGNOSIS; QA-SNARE PROTEINS; RETROSPECTIVE STUDIES; RISK ASSESSMENT; SURVIVAL RATE; TIME FACTORS; TREATMENT OUTCOME; TURKEY;

EID: 84937711821     PISSN: 15297535     EISSN: 19473893     Source Type: Journal    
DOI: 10.1097/PCC.0000000000000449     Document Type: Article

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