Misfolding of vWF to pathologically disordered conformations impacts the severity of von willebrand disease

Biophysical Journal

Volumn 107, Issue 5, 2014, Pages 1185-1195

  Tischer, Alexander ^a   Madde, Pranathi ^a   Moon Tasson, Laurie ^a   Auton, Matthew ^a  

^a MAYO CLINIC   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ADHESION RECEPTOR; THROMBIN RECEPTOR; UREA; VON WILLEBRAND FACTOR;

CELL ADHESION; CIRCULAR DICHROISM; FLOW KINETICS; GENETICS; HUMAN; METABOLISM; MUTATION; PHYSIOLOGY; PROTEIN FOLDING; PROTEIN SECONDARY STRUCTURE; PROTEIN TERTIARY STRUCTURE; SEVERITY OF ILLNESS INDEX; SPECTROSCOPY; STATISTICAL MODEL; THERMODYNAMICS; THROMBOCYTE; VON WILLEBRAND DISEASE;

BLOOD PLATELETS; CELL ADHESION; CIRCULAR DICHROISM; HUMANS; LINEAR MODELS; MUTATION; PLATELET GLYCOPROTEIN GPIB-IX COMPLEX; PROTEIN FOLDING; PROTEIN STRUCTURE, SECONDARY; PROTEIN STRUCTURE, TERTIARY; RHEOLOGY; SEVERITY OF ILLNESS INDEX; SPECTRUM ANALYSIS; THERMODYNAMICS; UREA; VON WILLEBRAND DISEASES; VON WILLEBRAND FACTOR;

EID: 84937609814     PISSN: 00063495     EISSN: 15420086     Source Type: Journal    
DOI: 10.1016/j.bpj.2014.07.026     Document Type: Article

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