Opa1 overexpression ameliorates the phenotype of two mitochondrial disease mouse models

Cell Metabolism

Volumn 21, Issue 6, 2015, Pages 845-854

  Civiletto, Gabriele ^a,b   Varanita, Tatiana ^c   Cerutti, Raffaele ^b   Gorletta, Tatiana ^a   Barbaro, Serena ^a   Marchet, Silvia ^a   Lamperti, Costanza ^a   Viscomi, Carlo ^a,b   Scorrano, Luca ^c,d   Zeviani, Massimo ^a,b  

^a DEPARTMENT OF NEUROSURGERY   (Italy)

^b UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^c VENETIAN INSTITUTE OF MOLECULAR MEDICINE   (Italy)

^d UNIVERSITY OF PADOVA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOCHROME C OXIDASE; MITOCHONDRIAL PROTEIN; OPA1 PROTEIN; UNCLASSIFIED DRUG; GUANOSINE TRIPHOSPHATASE; NDUFS4 PROTEIN, MOUSE; OPA1 PROTEIN (GTPASE), MOUSE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE);

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FEMALE; GASTROCNEMIUS MUSCLE; MALE; MITOCHONDRIAL RESPIRATION; MOTOR PERFORMANCE; MOUSE; MUSCLE FUNCTION; MUSCLE MITOCHONDRION; NONHUMAN; OXYGEN CONSUMPTION; PHENOTYPE; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRIORITY JOURNAL; RESPIRATORY CHAIN; WESTERN BLOTTING; ANIMAL; BIOSYNTHESIS; ENZYMOLOGY; GENE EXPRESSION REGULATION; GENETICS; KNOCKOUT MOUSE; METABOLISM; MITOCHONDRION; PATHOLOGY;

MUS;

ANIMALS; ELECTRON TRANSPORT COMPLEX I; ELECTRON TRANSPORT COMPLEX IV; GENE EXPRESSION REGULATION, ENZYMOLOGIC; GTP PHOSPHOHYDROLASES; MICE; MICE, KNOCKOUT; MITOCHONDRIA; MITOCHONDRIAL DISEASES; OXYGEN CONSUMPTION;

EID: 84930588143     PISSN: 15504131     EISSN: 19327420     Source Type: Journal    
DOI: 10.1016/j.cmet.2015.04.016     Document Type: Article

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