Familial behavioral variant frontotemporal dementia associated with astrocyte-predominant tauopathy

Journal of Neuropathology and Experimental Neurology

Volumn 74, Issue 4, 2015, Pages 370-379

  Ferrer, Isidre ^a,b   Legati, Andrea ^c   García Monco, J Carlos ^d   Gomez Beldarrain, Marian ^d   Carmona, Margarita ^a,b   Blanco, Rosa ^a,b   Seeley, William W ^e   Coppola, Giovanni ^c  

^a HOSPITAL UNIVERSITARI DE BELLVITGE   (Spain)

^b CENTRO DE INVESTIGACIÓN BIOMÉDICA EN RED SOBRE ENFERMEDADES NEURODEGENERATIVAS CIBERNED   (Spain)

^c UNIVERSITY OF CALIFORNIA   (United States)

^d HOSPITAL DE GALDAKAO   (Spain)

^e UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Astrocyte; Astrocyte predominant tauopathy; Familial tauopathy; Frontotemporal lobar dementia; FUS; MAPT; Splicing; Tau

Indexed keywords

FUSED IN SARCOMA PROTEIN; GLUTAMATE TRANSPORTER; MYELIN; TAU PROTEIN;

ADULT; ALZHEIMER DISEASE; AMYGDALOID NUCLEUS; ANTISOCIAL PERSONALITY DISORDER; ARTICLE; ASTROCYTE; ASTROCYTE PREDOMINANT TAUOPATHY; BRAIN CORTEX; CASE REPORT; CAUDATE NUCLEUS; CELL LOSS; CEREBELLUM; CHROMOSOME 9; COGNITIVE DEFECT; DELIRIUM; DENTATE NUCLEUS; DEPRESSION; DISEASE ASSOCIATION; DISORIENTATION; ENTORHINAL CORTEX; EXOME; EXON; FAMILIAL BEHAVIORAL VARIANT FRONTOTEMPORAL DEMENTIA; FAMILIAL DISEASE; FEMALE; FRONTAL CORTEX; FRONTAL VARIANT FRONTOTEMPORAL DEMENTIA; GEL ELECTROPHORESIS; GENE; GENE EXPRESSION; GENE MUTATION; GENE SEQUENCE; GENETIC ASSOCIATION; GENETIC SCREENING; HIPPOCAMPUS; HUMAN; HUMAN CELL; HUMAN TISSUE; INFERIOR OLIVE; INSULA; MAPT GENE; MIDDLE AGED; MOLECULAR WEIGHT; NERVE CELL; NUCLEAR MAGNETIC RESONANCE IMAGING; OLIGODENDROGLIA; PRIORITY JOURNAL; PURKINJE CELL; PUTAMEN; SINGLE PHOTON EMISSION COMPUTER TOMOGRAPHY; SUBICULUM; TAUOPATHY; TEMPORAL CORTEX; THALAMUS; WHITE MATTER; FRONTOTEMPORAL DEMENTIA; GENETICS; PATHOLOGY;

ASTROCYTES; FEMALE; FRONTOTEMPORAL DEMENTIA; HUMANS; MIDDLE AGED; TAUOPATHIES;

EID: 84925867784     PISSN: 00223069     EISSN: 15546578     Source Type: Journal    
DOI: 10.1097/NEN.0000000000000180     Document Type: Article

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