The GABA transaminase, ABAT, is essential for mitochondrial nucleoside metabolism

Cell Metabolism

Volumn 21, Issue 3, 2015, Pages 417-427

  Besse, Arnaud ^a   Wu, Ping ^a   Bruni, Francesco ^b   Donti, Taraka ^a   Graham, Brett H ^a   Craigen, William J ^a   McFarland, Robert ^b   Moretti, Paolo ^a   Lalani, Seema ^a   Scott, Kenneth L ^a   Taylor, Robert W ^b   Bonnen, Penelope E ^a  

^a BAYLOR COLLEGE OF MEDICINE   (United States)

^b NEWCASTLE UNIVERSITY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

4 AMINOBUTYRATE AMINOTRANSFERASE; ANTICONVULSIVE AGENT; MITOCHONDRIAL DNA; NUCLEOSIDE; NUCLEOSIDE DIPHOSPHATE KINASE D; VIGABATRIN; 4 AMINOBUTYRIC ACID;

3' UNTRANSLATED REGION; 4 AMINOBUTYRIC ACID METABOLISM; ALLELE; ANIMAL CELL; ARTICLE; CASE REPORT; CELLULAR DISTRIBUTION; CHILD; CONTROLLED STUDY; EMBRYO; FEMALE; GENE DOSAGE; HOMOZYGOSITY; HUMAN; HUMAN CELL; MALE; MISSENSE MUTATION; MITOCHONDRIAL DNA DEPLETION; MITOCHONDRIAL DNA REPLICATION; MITOCHONDRIAL ENCEPHALOMYOPATHY; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL RESPIRATION; MOUSE; NONHUMAN; NUCLEOTIDE SEQUENCE; OPEN READING FRAME; PHOTORECEPTOR CELL; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN PHOSPHORYLATION; SEIZURE; BRAIN; FIBROBLAST; GENETICS; METABOLISM; MITOCHONDRION;

4-AMINOBUTYRATE TRANSAMINASE; BRAIN; DNA, MITOCHONDRIAL; FIBROBLASTS; GAMMA-AMINOBUTYRIC ACID; HUMANS; MITOCHONDRIA; MUTATION, MISSENSE; NUCLEOSIDES;

EID: 84924409431     PISSN: 15504131     EISSN: 19327420     Source Type: Journal    
DOI: 10.1016/j.cmet.2015.02.008     Document Type: Article

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