Dysregulated iron metabolism in the choroid plexus in fragile X-associated tremor/ataxia syndrome

Brain Research

Volumn 1598, Issue , 2015, Pages 88-96

  Ariza, Jeanelle ^a,b   Steward, Craig ^a   Rueckert, Flora ^a   Widdison, Matt ^a   Coffman, Robert ^a   Afjei, Atiyeh ^a   Noctor, Stephen C ^a,c   Hagerman, Randi ^b,c   Hagerman, Paul ^b,c   Martínez Cerdeño, Verónica ^a,b,c  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Autism; CGG repeat; Choroid plexus; FMR1; Fragile X; FXTAS; Iron; Neurodegeneration; Premutation

Indexed keywords

CD71 ANTIGEN; CERULOPLASMIN; FERROPORTIN; IRON; TRANSFERRIN; CATION TRANSPORT PROTEIN; LEUKOCYTE ANTIGEN; METAL TRANSPORTING PROTEIN 1; TRANSFERRIN RECEPTOR;

ARTICLE; ATAXIA; BASOLATERAL MEMBRANE; CHOROID PLEXUS; CONTROLLED STUDY; EPITHELIUM CELL; FEMALE; FRAGILE X ASSOCIATED TREMOR ATAXIA SYNDROME; FRAGILE X SYNDROME; HUMAN; HUMAN TISSUE; IRON METABOLISM; MALE; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN LOCALIZATION; STROMA; TISSUE LEVEL; TREMOR; AGED; DEFICIENCY; EPITHELIUM; INTRACELLULAR SPACE; METABOLISM; MIDDLE AGED; PATHOLOGY; VERY ELDERLY;

AGED; AGED, 80 AND OVER; ANTIGENS, CD; ATAXIA; CATION TRANSPORT PROTEINS; CERULOPLASMIN; CHOROID PLEXUS; EPITHELIUM; FEMALE; FRAGILE X SYNDROME; HUMANS; INTRACELLULAR SPACE; IRON; MALE; MIDDLE AGED; RECEPTORS, TRANSFERRIN; TRANSFERRIN; TREMOR;

EID: 84924126806     PISSN: 00068993     EISSN: 18726240     Source Type: Journal    
DOI: 10.1016/j.brainres.2014.11.058     Document Type: Article

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