-
1
-
-
20044362721
-
Family-based association between Alzheimer's disease and variants in UBQLN1
-
L. Bertram, M. Hiltunen, M. Parkinson, M. Ingelsson, C. Lange, K. Ramasamy, K. Mullin, R. Menon, A.J. Sampson, M.Y. Hsiao, K.J. Elliott, G. Velicelebi, T. Moscarillo, B.T. Hyman, S.L. Wagner, K.D. Becker, D. Blacker, and R.E. Tanzi Family-based association between Alzheimer's disease and variants in UBQLN1 N. Engl. J. Med. 352 2005 884 894
-
(2005)
N. Engl. J. Med.
, vol.352
, pp. 884-894
-
-
Bertram, L.1
Hiltunen, M.2
Parkinson, M.3
Ingelsson, M.4
Lange, C.5
Ramasamy, K.6
Mullin, K.7
Menon, R.8
Sampson, A.J.9
Hsiao, M.Y.10
Elliott, K.J.11
Velicelebi, G.12
Moscarillo, T.13
Hyman, B.T.14
Wagner, S.L.15
Becker, K.D.16
Blacker, D.17
Tanzi, R.E.18
-
2
-
-
0034673973
-
Molecular cloning, chromosome mapping and characterization of UBQLN3 a testis-specific gene that contains an ubiquitin-like domain
-
D. Conklin, S. Holderman, T.E. Whitmore, M. Maurer, and A.L. Feldhaus Molecular cloning, chromosome mapping and characterization of UBQLN3 a testis-specific gene that contains an ubiquitin-like domain Gene 249 2000 91 98
-
(2000)
Gene
, vol.249
, pp. 91-98
-
-
Conklin, D.1
Holderman, S.2
Whitmore, T.E.3
Maurer, M.4
Feldhaus, A.L.5
-
3
-
-
0034703397
-
Identification and characterization of an ataxin-1-interacting protein: A1Up, a ubiquitin-like nuclear protein
-
J.D. Davidson, B. Riley, E.N. Burright, L.A. Duvick, H.Y. Zoghbi, and H.T. Orr Identification and characterization of an ataxin-1-interacting protein: A1Up, a ubiquitin-like nuclear protein Hum. Mol. Genet 9 2000 2305 2312
-
(2000)
Hum. Mol. Genet
, vol.9
, pp. 2305-2312
-
-
Davidson, J.D.1
Riley, B.2
Burright, E.N.3
Duvick, L.A.4
Zoghbi, H.Y.5
Orr, H.T.6
-
4
-
-
18544410106
-
Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation
-
S.W. Davies, M. Turmaine, B.A. Cozens, M. DiFiglia, A.H. Sharp, C.A. Ross, E. Scherzinger, E.E. Wanker, L. Mangiarini, and G.P. Bates Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation Cell 90 1997 537 548
-
(1997)
Cell
, vol.90
, pp. 537-548
-
-
Davies, S.W.1
Turmaine, M.2
Cozens, B.A.3
Difiglia, M.4
Sharp, A.H.5
Ross, C.A.6
Scherzinger, E.7
Wanker, E.E.8
Mangiarini, L.9
Bates, G.P.10
-
5
-
-
80052580969
-
Mutations in UBQLN2 cause dominant X-linked juvenile and adult-onset ALS and ALS/dementia
-
H.X. Deng, W. Chen, S.T. Hong, K.M. Boycott, G.H. Gorrie, N. Siddique, Y. Yang, F. Fecto, Y. Shi, H. Zhai, H. Jiang, M. Hirano, E. Rampersaud, G.H. Jansen, S. Donkervoort, E.H. Bigio, B.R. Brooks, K. Ajroud, R.L. Sufit, J.L. Haines, E. Mugnaini, M.A. Pericak-Vance, and T. Siddique Mutations in UBQLN2 cause dominant X-linked juvenile and adult-onset ALS and ALS/dementia Nature 477 2011 211 215
-
(2011)
Nature
, vol.477
, pp. 211-215
-
-
Deng, H.X.1
Chen, W.2
Hong, S.T.3
Boycott, K.M.4
Gorrie, G.H.5
Siddique, N.6
Yang, Y.7
Fecto, F.8
Shi, Y.9
Zhai, H.10
Jiang, H.11
Hirano, M.12
Rampersaud, E.13
Jansen, G.H.14
Donkervoort, S.15
Bigio, E.H.16
Brooks, B.R.17
Ajroud, K.18
Sufit, R.L.19
Haines, J.L.20
Mugnaini, E.21
Pericak-Vance, M.A.22
Siddique, T.23
more..
-
6
-
-
3342879140
-
Identification of ubiquitin-interacting proteins in purified polyglutamine aggregates
-
H. Doi, K. Mitsui, M. Kurosawa, Y. Machida, Y. Kuroiwa, and N. Nukina Identification of ubiquitin-interacting proteins in purified polyglutamine aggregates FEBS Lett. 571 2004 171 176
-
(2004)
FEBS Lett.
, vol.571
, pp. 171-176
-
-
Doi, H.1
Mitsui, K.2
Kurosawa, M.3
Machida, Y.4
Kuroiwa, Y.5
Nukina, N.6
-
7
-
-
23144449583
-
Delivery of ubiquitinated substrates to protein-unfolding machines
-
S. Elsasser, and D. Finley Delivery of ubiquitinated substrates to protein-unfolding machines Nat. Cell Biol. 7 2005 742 749
-
(2005)
Nat. Cell Biol.
, vol.7
, pp. 742-749
-
-
Elsasser, S.1
Finley, D.2
-
8
-
-
84902172802
-
UBQLN2 mutation causing heterogeneous X-linked dominant neurodegeneration
-
A.C. Fahed, B. McDonough, C.M. Gouvion, K.L. Newell, L.S. Dure, M. Bebin, A.G. Bick, J.G. Seidman, D.H. Harter, and C.E. Seidman UBQLN2 mutation causing heterogeneous X-linked dominant neurodegeneration Ann. Neurol. 2014
-
(2014)
Ann. Neurol.
-
-
Fahed, A.C.1
McDonough, B.2
Gouvion, C.M.3
Newell, K.L.4
Dure, L.S.5
Bebin, M.6
Bick, A.G.7
Seidman, J.G.8
Harter, D.H.9
Seidman, C.E.10
-
10
-
-
33750568162
-
Dimerization of ubiquilin is dependent upon the central region of the protein: Evidence that the monomer, but not the dimer, is involved in binding presenilins
-
D.L. Ford, and M.J. Monteiro Dimerization of ubiquilin is dependent upon the central region of the protein: evidence that the monomer, but not the dimer, is involved in binding presenilins Biochem. J. 399 2006 397 404
-
(2006)
Biochem. J.
, vol.399
, pp. 397-404
-
-
Ford, D.L.1
Monteiro, M.J.2
-
11
-
-
34547640864
-
Studies of the role of ubiquitination in the interaction of ubiquilin with the loop and carboxyl terminal regions of presenilin-2
-
D.L. Ford, and M.J. Monteiro Studies of the role of ubiquitination in the interaction of ubiquilin with the loop and carboxyl terminal regions of presenilin-2 Biochemistry 46 2007 8827 8837
-
(2007)
Biochemistry
, vol.46
, pp. 8827-8837
-
-
Ford, D.L.1
Monteiro, M.J.2
-
12
-
-
37849018692
-
Ubiquilin antagonizes presenilin and promotes neurodegeneration in Drosophila
-
A. Ganguly, R.M. Feldman, and M. Guo ubiquilin antagonizes presenilin and promotes neurodegeneration in Drosophila Hum. Mol. Genet 17 2008 293 302
-
(2008)
Hum. Mol. Genet
, vol.17
, pp. 293-302
-
-
Ganguly, A.1
Feldman, R.M.2
Guo, M.3
-
13
-
-
84864929823
-
Association of UBQLN1 mutation with Brown-Vialetto-Van Laere syndrome but not typical ALS
-
P. Gonzalez-Perez, Y. Lu, R.J. Chian, P.C. Sapp, R.E. Tanzi, L. Bertram, D. McKenna-Yasek, F.B. Gao, and R.H. Brown Jr. Association of UBQLN1 mutation with Brown-Vialetto-Van Laere syndrome but not typical ALS Neurobiol. Dis. 48 2012 391 398
-
(2012)
Neurobiol. Dis.
, vol.48
, pp. 391-398
-
-
Gonzalez-Perez, P.1
Lu, Y.2
Chian, R.J.3
Sapp, P.C.4
Tanzi, R.E.5
Bertram, L.6
McKenna-Yasek, D.7
Gao, F.B.8
Brown, Jr.R.H.9
-
14
-
-
3242695184
-
Progressive decrease in chaperone protein levels in a mouse model of Huntington's disease and induction of stress proteins as a therapeutic approach
-
D.G. Hay, K. Sathasivam, S. Tobaben, B. Stahl, M. Marber, R. Mestril, A. Mahal, D.L. Smith, B. Woodman, and G.P. Bates Progressive decrease in chaperone protein levels in a mouse model of Huntington's disease and induction of stress proteins as a therapeutic approach Hum. Mol. Genet 13 2004 1389 1405
-
(2004)
Hum. Mol. Genet
, vol.13
, pp. 1389-1405
-
-
Hay, D.G.1
Sathasivam, K.2
Tobaben, S.3
Stahl, B.4
Marber, M.5
Mestril, R.6
Mahal, A.7
Smith, D.L.8
Woodman, B.9
Bates, G.P.10
-
15
-
-
0141678246
-
Standardization and statistical approaches to therapeutic trials in the R6/2 mouse
-
E. Hockly, B. Woodman, A. Mahal, C.M. Lewis, and G. Bates Standardization and statistical approaches to therapeutic trials in the R6/2 mouse Brain Res. Bull. 61 2003 469 479
-
(2003)
Brain Res. Bull.
, vol.61
, pp. 469-479
-
-
Hockly, E.1
Woodman, B.2
Mahal, A.3
Lewis, C.M.4
Bates, G.5
-
16
-
-
0033962442
-
A family of ubiquitin-like proteins binds the ATPase domain of Hsp70-like Stch
-
F.J. Kaye, S. Modi, I. Ivanovska, E.V. Koonin, K. Thress, A. Kubo, S. Kornbluth, and M.D. Rose A family of ubiquitin-like proteins binds the ATPase domain of Hsp70-like Stch FEBS Lett. 467 2000 348 355
-
(2000)
FEBS Lett.
, vol.467
, pp. 348-355
-
-
Kaye, F.J.1
Modi, S.2
Ivanovska, I.3
Koonin, E.V.4
Thress, K.5
Kubo, A.6
Kornbluth, S.7
Rose, M.D.8
-
17
-
-
0141632772
-
The ubiquitin-associated domain of hPLIC-2 interacts with the proteasome
-
M.F. Kleijnen, R.M. Alarcon, and P.M. Howley The ubiquitin-associated domain of hPLIC-2 interacts with the proteasome Mol. Biol. Cell. 14 2003 3868 3875
-
(2003)
Mol. Biol. Cell.
, vol.14
, pp. 3868-3875
-
-
Kleijnen, M.F.1
Alarcon, R.M.2
Howley, P.M.3
-
18
-
-
0033636785
-
The hPLIC proteins may provide a link between the ubiquitination machinery and the proteasome
-
M.F. Kleijnen, A.H. Shih, P. Zhou, S. Kumar, R.E. Soccio, N.L. Kedersha, G. Gill, and P.M. Howley The hPLIC proteins may provide a link between the ubiquitination machinery and the proteasome Mol. Cell 6 2000 409 419
-
(2000)
Mol. Cell
, vol.6
, pp. 409-419
-
-
Kleijnen, M.F.1
Shih, A.H.2
Zhou, P.3
Kumar, S.4
Soccio, R.E.5
Kedersha, N.L.6
Gill, G.7
Howley, P.M.8
-
19
-
-
2442520399
-
Ubiquilin interacts with ubiquitylated proteins and proteasome through its ubiquitin-associated and ubiquitin-like domains
-
H.S. Ko, T. Uehara, K. Tsuruma, and Y. Nomura Ubiquilin interacts with ubiquitylated proteins and proteasome through its ubiquitin-associated and ubiquitin-like domains FEBS Lett. 566 2004 110 114
-
(2004)
FEBS Lett.
, vol.566
, pp. 110-114
-
-
Ko, H.S.1
Uehara, T.2
Tsuruma, K.3
Nomura, Y.4
-
20
-
-
41949131052
-
A novel connexin43-interacting protein, CIP75, which belongs to the UbL-UBA protein family, regulates the turnover of connexin43
-
X. Li, V. Su, W.E. Kurata, C. Jin, and A.F. Lau A novel connexin43-interacting protein, CIP75, which belongs to the UbL-UBA protein family, regulates the turnover of connexin43 J. Biol. Chem. 283 2008 5748 5759
-
(2008)
J. Biol. Chem.
, vol.283
, pp. 5748-5759
-
-
Li, X.1
Su, V.2
Kurata, W.E.3
Jin, C.4
Lau, A.F.5
-
21
-
-
70449723717
-
Ubiquilin and p97/VCP bind erasin, forming a complex involved in ERAD
-
P.J. Lim, R. Danner, J. Liang, H. Doong, C. Harman, D. Srinivasan, C. Rothenberg, H. Wang, Y. Ye, S. Fang, and M.J. Monteiro Ubiquilin and p97/VCP bind erasin, forming a complex involved in ERAD J. Cell Biol. 187 2009 201 217
-
(2009)
J. Cell Biol.
, vol.187
, pp. 201-217
-
-
Lim, P.J.1
Danner, R.2
Liang, J.3
Doong, H.4
Harman, C.5
Srinivasan, D.6
Rothenberg, C.7
Wang, H.8
Ye, Y.9
Fang, S.10
Monteiro, M.J.11
-
22
-
-
0034645063
-
Identification of ubiquilin, a novel presenilin interactor that increases presenilin protein accumulation
-
A.L. Mah, G. Perry, M.A. Smith, and M.J. Monteiro Identification of ubiquilin, a novel presenilin interactor that increases presenilin protein accumulation J. Cell Biol. 151 2000 847 862
-
(2000)
J. Cell Biol.
, vol.151
, pp. 847-862
-
-
Mah, A.L.1
Perry, G.2
Smith, M.A.3
Monteiro, M.J.4
-
23
-
-
16044373842
-
Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice
-
L. Mangiarini, K. Sathasivam, M. Seller, B. Cozens, A. Harper, C. Hetherington, M. Lawton, Y. Trottier, H. Lehrach, S.W. Davies, and G.P. Bates Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice Cell 87 1996 493 506
-
(1996)
Cell
, vol.87
, pp. 493-506
-
-
Mangiarini, L.1
Sathasivam, K.2
Seller, M.3
Cozens, B.4
Harper, A.5
Hetherington, C.6
Lawton, M.7
Trottier, Y.8
Lehrach, H.9
Davies, S.W.10
Bates, G.P.11
-
24
-
-
1842532263
-
Overexpression of ubiquilin decreases ubiquitination and degradation of presenilin proteins
-
L.K. Massey, A.L. Mah, D.L. Ford, J. Miller, J. Liang, H. Doong, and M.J. Monteiro Overexpression of ubiquilin decreases ubiquitination and degradation of presenilin proteins J. Alzheimer's Dis. 6 2004 79 92
-
(2004)
J. Alzheimer's Dis.
, vol.6
, pp. 79-92
-
-
Massey, L.K.1
Mah, A.L.2
Ford, D.L.3
Miller, J.4
Liang, J.5
Doong, H.6
Monteiro, M.J.7
-
25
-
-
27744468749
-
Ubiquilin regulates presenilin endoproteolysis and modulates gamma-secretase components, Pen-2 and nicastrin
-
L.K. Massey, A.L. Mah, and M.J. Monteiro Ubiquilin regulates presenilin endoproteolysis and modulates gamma-secretase components, Pen-2 and nicastrin Biochem. J. 391 2005 513 525
-
(2005)
Biochem. J.
, vol.391
, pp. 513-525
-
-
Massey, L.K.1
Mah, A.L.2
Monteiro, M.J.3
-
26
-
-
84862765926
-
Ubiquilin immunoreactivity in cytoplasmic and nuclear inclusions in synucleinopathies, polyglutamine diseases and intranuclear inclusion body disease
-
F. Mori, K. Tanji, S. Odagiri, Y. Toyoshima, M. Yoshida, T. Ikeda, H. Sasaki, A. Kakita, H. Takahashi, and K. Wakabayashi Ubiquilin immunoreactivity in cytoplasmic and nuclear inclusions in synucleinopathies, polyglutamine diseases and intranuclear inclusion body disease Acta Neuropathol. 2012
-
(2012)
Acta Neuropathol.
-
-
Mori, F.1
Tanji, K.2
Odagiri, S.3
Toyoshima, Y.4
Yoshida, M.5
Ikeda, T.6
Sasaki, H.7
Kakita, A.8
Takahashi, H.9
Wakabayashi, K.10
-
27
-
-
59649110865
-
PLIC proteins or ubiquilins regulate autophagy-dependent cell survival during nutrient starvation
-
E.N. N'Diaye, K.K. Kajihara, I. Hsieh, H. Morisaki, J. Debnath, and E.J. Brown PLIC proteins or ubiquilins regulate autophagy-dependent cell survival during nutrient starvation EMBO Rep. 10 2009 173 179
-
(2009)
EMBO Rep.
, vol.10
, pp. 173-179
-
-
N'Diaye, E.N.1
Kajihara, K.K.2
Hsieh, I.3
Morisaki, H.4
Debnath, J.5
Brown, E.J.6
-
28
-
-
0027164698
-
Expansion of an unstable trinucleotide CAG repeat in spinocerebellar ataxia type 1
-
H.T. Orr, M.Y. Chung, S. Banfi, T.J. Kwiatkowski Jr.; A. Servadio, A.L. Beaudet, A.E. McCall, L.A. Duvick, L.P. Ranum, and H.Y. Zoghbi Expansion of an unstable trinucleotide CAG repeat in spinocerebellar ataxia type 1 Nat. Genet. 4 1993 221 226
-
(1993)
Nat. Genet.
, vol.4
, pp. 221-226
-
-
Orr, H.T.1
Chung, M.Y.2
Banfi, S.3
Kwiatkowski, Jr.T.J.4
Servadio, A.5
Beaudet, A.L.6
McCall, A.E.7
Duvick, L.A.8
Ranum, L.P.9
Zoghbi, H.Y.10
-
29
-
-
26944465404
-
Diverse polyubiquitin interaction properties of ubiquitin-associated domains
-
S. Raasi, R. Varadan, D. Fushman, and C.M. Pickart Diverse polyubiquitin interaction properties of ubiquitin-associated domains Nat. Struct. Mol. Biol. 12 2005 708 714
-
(2005)
Nat. Struct. Mol. Biol.
, vol.12
, pp. 708-714
-
-
Raasi, S.1
Varadan, R.2
Fushman, D.3
Pickart, C.M.4
-
30
-
-
77957674939
-
Ubiquilin at a crossroads in protein degradation pathways
-
C. Rothenberg, and M.J. Monteiro Ubiquilin at a crossroads in protein degradation pathways Autophagy 6 2010 979 980
-
(2010)
Autophagy
, vol.6
, pp. 979-980
-
-
Rothenberg, C.1
Monteiro, M.J.2
-
31
-
-
77955023765
-
Ubiquilin functions in autophagy and is degraded by chaperone-mediated autophagy
-
C. Rothenberg, D. Srinivasan, L. Mah, S. Kaushik, C.M. Peterhoff, J. Ugolino, S. Fang, A.M. Cuervo, R.A. Nixon, and M.J. Monteiro Ubiquilin functions in autophagy and is degraded by chaperone-mediated autophagy Hum. Mol. Genet 19 2010 3219 3232
-
(2010)
Hum. Mol. Genet
, vol.19
, pp. 3219-3232
-
-
Rothenberg, C.1
Srinivasan, D.2
Mah, L.3
Kaushik, S.4
Peterhoff, C.M.5
Ugolino, J.6
Fang, S.7
Cuervo, A.M.8
Nixon, R.A.9
Monteiro, M.J.10
-
32
-
-
84880325702
-
Unbiased screen reveals ubiquilin-1 and -2 highly associated with Huntingtin inclusions
-
N.J. Rutherford, J. Lewis, A.K. Clippinger, M.A. Thomas, J. Adamson, P.E. Cruz, A. Cannon, G. Xu, T.E. Golde, G. Shaw, D.R. Borchelt, and B.I. Giasson Unbiased screen reveals ubiquilin-1 and -2 highly associated with Huntingtin inclusions Brain Res. 2013
-
(2013)
Brain Res.
-
-
Rutherford, N.J.1
Lewis, J.2
Clippinger, A.K.3
Thomas, M.A.4
Adamson, J.5
Cruz, P.E.6
Cannon, A.7
Xu, G.8
Golde, T.E.9
Shaw, G.10
Borchelt, D.R.11
Giasson, B.I.12
-
33
-
-
84898728074
-
Ubiquilin-1 overexpression increases the lifespan and delays accumulation of Huntingtin aggregates in the R6/2 mouse model of Huntington's disease
-
N. Safren, A. El Ayadi, L. Chang, C.E. Terrillion, T.D. Gould, D.F. Boehning, and M.J. Monteiro Ubiquilin-1 overexpression increases the lifespan and delays accumulation of Huntingtin aggregates in the R6/2 mouse model of Huntington's disease PLoS One 9 2014 e87513
-
(2014)
PLoS One
, vol.9
, pp. e87513
-
-
Safren, N.1
El Ayadi, A.2
Chang, L.3
Terrillion, C.E.4
Gould, T.D.5
Boehning, D.F.6
Monteiro, M.J.7
-
34
-
-
0037059042
-
Molecular chaperones as modulators of polyglutamine protein aggregation and toxicity
-
H. Sakahira, P. Breuer, M.K. Hayer-Hartl, and F.U. Hartl Molecular chaperones as modulators of polyglutamine protein aggregation and toxicity Proc. Natl. Acad. Sci. U.S.A. 99 Suppl. 4 2002 16412 16418
-
(2002)
Proc. Natl. Acad. Sci. U.S.A.
, vol.99
, pp. 16412-16418
-
-
Sakahira, H.1
Breuer, P.2
Hayer-Hartl, M.K.3
Hartl, F.U.4
-
35
-
-
80053927521
-
Ubiquilin-1 is a molecular chaperone for the amyloid precursor protein
-
E.S. Stieren, A. El Ayadi, Y. Xiao, E. Siller, M.L. Landsverk, A.F. Oberhauser, J.M. Barral, and D. Boehning Ubiquilin-1 is a molecular chaperone for the amyloid precursor protein J. Biol. Chem. 286 2011 35689 35698
-
(2011)
J. Biol. Chem.
, vol.286
, pp. 35689-35698
-
-
Stieren, E.S.1
El Ayadi, A.2
Xiao, Y.3
Siller, E.4
Landsverk, M.L.5
Oberhauser, A.F.6
Barral, J.M.7
Boehning, D.8
-
36
-
-
79751480230
-
Alzheimer's disease-associated ubiquilin-1 regulates presenilin-1 accumulation and aggresome formation
-
J. Viswanathan, A. Haapasalo, C. Bottcher, R. Miettinen, K.M. Kurkinen, A. Lu, A. Thomas, C.J. Maynard, D. Romano, B.T. Hyman, O. Berezovska, L. Bertram, H. Soininen, N.P. Dantuma, R.E. Tanzi, and M. Hiltunen Alzheimer's disease-associated ubiquilin-1 regulates presenilin-1 accumulation and aggresome formation Traffic 2011
-
(2011)
Traffic
-
-
Viswanathan, J.1
Haapasalo, A.2
Bottcher, C.3
Miettinen, R.4
Kurkinen, K.M.5
Lu, A.6
Thomas, A.7
Maynard, C.J.8
Romano, D.9
Hyman, B.T.10
Berezovska, O.11
Bertram, L.12
Soininen, H.13
Dantuma, N.P.14
Tanzi, R.E.15
Hiltunen, M.16
-
37
-
-
33846225133
-
Huntington's disease
-
F.O. Walker Huntington's disease Lancet 369 2007 218 228
-
(2007)
Lancet
, vol.369
, pp. 218-228
-
-
Walker, F.O.1
-
38
-
-
33644771265
-
Suppression of polyglutamine-induced toxicity in cell and animal models of Huntington's disease by ubiquilin
-
H. Wang, P.J. Lim, C. Yin, M. Rieckher, B.E. Vogel, and M.J. Monteiro Suppression of polyglutamine-induced toxicity in cell and animal models of Huntington's disease by ubiquilin Hum. Mol. Genet 15 2006 1025 1041
-
(2006)
Hum. Mol. Genet
, vol.15
, pp. 1025-1041
-
-
Wang, H.1
Lim, P.J.2
Yin, C.3
Rieckher, M.4
Vogel, B.E.5
Monteiro, M.J.6
-
39
-
-
34447095637
-
Ubiquilin interacts and enhances the degradation of expanded-polyglutamine proteins
-
H. Wang, and M.J. Monteiro Ubiquilin interacts and enhances the degradation of expanded-polyglutamine proteins Biochem. Biophys. Res. Commun. 360 2007 423 427
-
(2007)
Biochem. Biophys. Res. Commun.
, vol.360
, pp. 423-427
-
-
Wang, H.1
Monteiro, M.J.2
-
40
-
-
84864380051
-
UBQLN2/ubiquilin 2 mutation and pathology in familial amyotrophic lateral sclerosis
-
K.L. Williams, S.T. Warraich, S. Yang, J.A. Solski, R. Fernando, G.A. Rouleau, G.A. Nicholson, and I.P. Blair UBQLN2/ubiquilin 2 mutation and pathology in familial amyotrophic lateral sclerosis Neurobiol. Aging 33 2527 2012 e3 10
-
(2012)
Neurobiol. Aging
, vol.33
, Issue.2527
, pp. e3-10
-
-
Williams, K.L.1
Warraich, S.T.2
Yang, S.3
Solski, J.A.4
Fernando, R.5
Rouleau, G.A.6
Nicholson, G.A.7
Blair, I.P.8
-
41
-
-
0033213325
-
Ubiquitin-related proteins regulate interaction of vimentin intermediate filaments with the plasma membrane
-
A.L. Wu, J. Wang, A. Zheleznyak, and E.J. Brown Ubiquitin-related proteins regulate interaction of vimentin intermediate filaments with the plasma membrane Mol. Cell 4 1999 619 625
-
(1999)
Mol. Cell
, vol.4
, pp. 619-625
-
-
Wu, A.L.1
Wang, J.2
Zheleznyak, A.3
Brown, E.J.4
-
42
-
-
0037196550
-
Characterization of ubiquilin 1, an mTOR-interacting protein
-
S. Wu, A. Mikhailov, H. Kallo-Hosein, K. Hara, K. Yonezawa, and J. Avruch Characterization of ubiquilin 1, an mTOR-interacting protein Biochim. Biophys. Acta 1542 2002 41 56
-
(2002)
Biochim. Biophys. Acta
, vol.1542
, pp. 41-56
-
-
Wu, S.1
Mikhailov, A.2
Kallo-Hosein, H.3
Hara, K.4
Yonezawa, K.5
Avruch, J.6
-
43
-
-
0028208253
-
Identification and characterization of a novel (115 kDa) neurofilament-associated kinase
-
J. Xiao, and M.J. Monteiro Identification and characterization of a novel (115 kDa) neurofilament-associated kinase J. Neurosci. 14 1994 1820 1833
-
(1994)
J. Neurosci.
, vol.14
, pp. 1820-1833
-
-
Xiao, J.1
Monteiro, M.J.2
-
44
-
-
84900307676
-
A new mutation in ubiquilin gene family and its effect on protein degradation
-
J. Yan, K. Ajroud, F. Fecto, Y. Shi, N. Siddique, H.-X. Deng, and T. Siddique A new mutation in ubiquilin gene family and its effect on protein degradation Neurology 80 P02 2013 168
-
(2013)
Neurology
, vol.80
, Issue.P02
, pp. 168
-
-
Yan, J.1
Ajroud, K.2
Fecto, F.3
Shi, Y.4
Siddique, N.5
Deng, H.-X.6
Siddique, T.7
-
45
-
-
0029175420
-
Spinocerebellar ataxia type 1
-
H.Y. Zoghbi Spinocerebellar ataxia type 1 Clin. Neurosci. 3 1995 5 11
-
(1995)
Clin. Neurosci.
, vol.3
, pp. 5-11
-
-
Zoghbi, H.Y.1
|