Advances in the understanding of skeletal muscle weakness in murine models of diseases affecting nerve-evoked muscle activity, motor neurons, synapses and myofibers

Neuromuscular Disorders

Volumn 24, Issue 11, 2014, Pages 960-972

  Ferry, Arnaud ^a,b   Joanne, Pierre ^b   Hadj Said, Wahiba ^a   Vignaud, Alban ^a   Lilienbaum, Alain ^b   Hourdé, Christophe ^a   Medja, Fadia ^a   Noirez, Philippe ^b   Charbonnier, Frederic ^b   Chatonnet, Arnaud ^c   Chevessier, Frederic ^d   Nicole, Sophie ^a   Agbulut, Onnik ^b   Butler Browne, Gillian ^a  

^a SORBONNE UNIVERSITÉ   (France)

^b UNIVERSITÉ PARIS DESCARTES   (France)

^c UNIV MONTPELLIER   (France)

^d UNIVERSITY HOSPITAL ERLANGEN   (Germany)

Author keywords

Murine models; Neuromuscular diseases; Skeletal muscle weakness

Indexed keywords

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BCL3 GENE; CONGENITAL MYASTHENIC SYNDROME; CONTROLLED STUDY; FEMALE; FN14 GENE; GADD45A GENE; GENE; GENE CONTROL; GENE EXPRESSION; HDAC4 GENE; INJURY; LC3 GENE; MALE; MOTONEURON; MOUSE; MURINE MODEL; MUSCLE ATROPHY; MUSCLE CELL; MUSCLE CONTRACTION; MUSCLE WEAKNESS; NERVE INJURY; NONHUMAN; SCHWARTZ JAMPEL SYNDROME; SIGNAL TRANSDUCTION; SYNAPSE; UPREGULATION; ANIMAL; COMPLICATION; DISEASE MODEL; ELECTROMYOGRAPHY; EVOKED MUSCLE RESPONSE; GENE EXPRESSION REGULATION; GENETICS; MUSCLE DISEASE; MUSCLE FIBRIL; MUTATION; PATHOLOGY; PATHOPHYSIOLOGY; PERIPHERAL NERVOUS SYSTEM; PHYSIOLOGY; SKELETAL MUSCLE; TRANSGENIC MOUSE;

CHOLINESTERASE; MUSK PROTEIN, MOUSE; PERLECAN; PROTEIN TYROSINE KINASE; PROTEOHEPARAN SULFATE; SOD1 G93A PROTEIN; SUPEROXIDE DISMUTASE; TUMOR NECROSIS FACTOR RECEPTOR; TWEAK RECEPTOR;

ANIMALS; CHOLINESTERASES; DISEASE MODELS, ANIMAL; ELECTROMYOGRAPHY; EVOKED POTENTIALS, MOTOR; GENE EXPRESSION REGULATION; HEPARAN SULFATE PROTEOGLYCANS; MICE; MICE, TRANSGENIC; MOTOR NEURONS; MUSCLE WEAKNESS; MUSCLE, SKELETAL; MUSCULAR DISEASES; MUTATION; MYOFIBRILS; NEUROEFFECTOR JUNCTION; RECEPTOR PROTEIN-TYROSINE KINASES; RECEPTORS, TUMOR NECROSIS FACTOR; SUPEROXIDE DISMUTASE;

EID: 84922336526     PISSN: 09608966     EISSN: 18732364     Source Type: Journal    
DOI: 10.1016/j.nmd.2014.06.001     Document Type: Article

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