Defects in mitochondrial ATP synthesis in dystrophin-deficient Mdx skeletal muscles may be caused by complex I insufficiency

PLoS ONE

Volumn 9, Issue 12, 2014, Pages

  Rybalka, Emma ^a,b   Timpani, Cara A ^a   Cooke, Matthew B ^a,b   Williams, Andrew D ^c   Hayes, Alan ^a,b  

^a VICTORIA UNIVERSITY   (Australia)

^b Australian Institute for Musculoskeletal Science   (Australia)

^c UNIVERSITY OF TASMANIA   (Australia)

Author keywords

[No Author keywords available]

Indexed keywords

2 OXOGLUTARIC ACID; ADENOSINE TRIPHOSPHATE; CALCIUM ION; CARNITINE; CITRATE SYNTHASE; CITRIC ACID; DYSTROPHIN; MALIC ACID; MITOCHONDRIAL PROTEIN; PALMITOYLCARNITINE; PYRUVIC ACID; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); ROTENONE; SUCCINATE DEHYDROGENASE (UBIQUINONE); SUCCINIC ACID; CALCIUM;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CITRIC ACID CYCLE; CONTROLLED STUDY; DIAPHRAGM MUSCLE; DISEASE EXACERBATION; DUCHENNE MUSCULAR DYSTROPHY; ENZYME DEFICIENCY; ENZYME INHIBITION; MITOCHONDRION; MITOCHONDRION SWELLING; MOUSE; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PATHOGENESIS; PROTEIN DEFICIENCY; SKELETAL MUSCLE; TIBIALIS ANTERIOR MUSCLE; ANIMAL; BASAL METABOLIC RATE; BIOSYNTHESIS; COMPLICATION; DEFICIENCY; DIAPHRAGM; METABOLISM; PATHOLOGY;

MUS;

ADENOSINE TRIPHOSPHATE; ANIMALS; BASAL METABOLISM; CALCIUM; CITRATE (SI)-SYNTHASE; CITRIC ACID CYCLE; DIAPHRAGM; DYSTROPHIN; ELECTRON TRANSPORT COMPLEX I; MICE; MITOCHONDRIA; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, DUCHENNE;

EID: 84919934339     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0115763     Document Type: Article

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