Mutation in dystrophin-encoding gene affects energy metabolism in mouse myoblasts

Biochemical and Biophysical Research Communications

Volumn 386, Issue 3, 2009, Pages 463-466

  Onopiuk, Marta ^a   Brutkowski, Wojciech ^a   Wierzbicka, Katarzyna ^a   Wojciechowska, Sylwia ^a   Szczepanowska, Joanna ^a   Fronk, Jan ^b   Lochmüller, Hanns ^c   Górecki, Dariusz C ^d   Zabłocki, Krzysztof ^a  

^a NENCKI INSTITUTE OF EXPERIMENTAL BIOLOGY   (Poland)

^b UNIVERSITY OF WARSAW   (Poland)

^c NEWCASTLE UNIVERSITY   (United Kingdom)

^d UNIVERSITY OF PORTSMOUTH   (United Kingdom)

Author keywords

mdx myoblast; Mitochondrial organization; Mitochondrial potential; Reactive oxygen species; Respiration

Indexed keywords

ADENOSINE TRIPHOSPHATE; DYSTROPHIN; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; REACTIVE OXYGEN METABOLITE;

ANIMAL CELL; ARTICLE; DUCHENNE MUSCULAR DYSTROPHY; ENERGY METABOLISM; GENE MUTATION; GLYCOLYSIS; INBRED STRAIN; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL RESPIRATION; MOUSE; MOUSE STRAIN; MYOBLAST; NONHUMAN; OXYGEN CONSUMPTION; PATHOGENESIS; PHENOTYPE; POINT MUTATION; PRIORITY JOURNAL; X CHROMOSOME LINKED MUSCULAR DYSTROPHIC MOUSE;

ADENOSINE TRIPHOSPHATE; ANIMALS; DYSTROPHIN; ENERGY METABOLISM; GLYCOLYSIS; MICE; MICE, INBRED MDX; MITOCHONDRIAL PROTON-TRANSLOCATING ATPASES; MUSCULAR DYSTROPHY, DUCHENNE; MYOBLASTS; OXYGEN CONSUMPTION; POINT MUTATION;

EID: 67650090495     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2009.06.053     Document Type: Article

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