메뉴 건너뛰기




Volumn 108, Issue 1, 2015, Pages 1-10

When to consider transfusion therapy for patients with non-transfusion-dependent thalassaemia

Author keywords

Haemoglobin E thalassaemia; Haemoglobin H disease; Iron chelation; Non transfusion dependent thalassaemia; Red cell transfusion; thalassaemia intermedia

Indexed keywords

HEMOGLOBIN;

EID: 84919674531     PISSN: 00429007     EISSN: 14230410     Source Type: Journal    
DOI: 10.1111/vox.12201     Document Type: Review
Times cited : (41)

References (95)
  • 1
    • 0023112573 scopus 로고
    • Hemoglobinopathies in Southeast Asia
    • Fucharoen S, Winichagoon P: Hemoglobinopathies in Southeast Asia. Hemoglobin 1987; 11:65-88
    • (1987) Hemoglobin , vol.11 , pp. 65-88
    • Fucharoen, S.1    Winichagoon, P.2
  • 2
    • 0034324016 scopus 로고    scopus 로고
    • Clinical manifestation of beta-thalassemia/hemoglobin E disease
    • Fucharoen S, Ketvichit P, Pootrakul P, et al.: Clinical manifestation of beta-thalassemia/hemoglobin E disease. J Pediatr Hematol Oncol 2000; 22:552-557
    • (2000) J Pediatr Hematol Oncol , vol.22 , pp. 552-557
    • Fucharoen, S.1    Ketvichit, P.2    Pootrakul, P.3
  • 3
    • 84873314430 scopus 로고    scopus 로고
    • New updating into hemoglobinopathies
    • [Epub ahead of print]
    • Fucharoen S, Winichagoon P: New updating into hemoglobinopathies. Int J Lab Hematol 2012; doi: 10.1111/j.1751-553X.2012.01446.x [Epub ahead of print].
    • (2012) Int J Lab Hematol
    • Fucharoen, S.1    Winichagoon, P.2
  • 4
    • 0033536288 scopus 로고    scopus 로고
    • The beta-thalassemias
    • Olivieri NF: The beta-thalassemias. N Engl J Med 1999; 341:99-109
    • (1999) N Engl J Med , vol.341 , pp. 99-109
    • Olivieri, N.F.1
  • 5
    • 44349122895 scopus 로고    scopus 로고
    • A scoring system for the classification of beta-thalassemia/Hb E disease severity
    • Sripichai O, Makarasara W, Munkongdee T, et al.: A scoring system for the classification of beta-thalassemia/Hb E disease severity. Am J Hematol 2008; 83:482-484
    • (2008) Am J Hematol , vol.83 , pp. 482-484
    • Sripichai, O.1    Makarasara, W.2    Munkongdee, T.3
  • 7
    • 44949128064 scopus 로고    scopus 로고
    • Global epidemiology of haemoglobin disorders and derived service indicators
    • Modell B, Darlison M: Global epidemiology of haemoglobin disorders and derived service indicators. Bull World Health Organ 2008; 86:480-487
    • (2008) Bull World Health Organ , vol.86 , pp. 480-487
    • Modell, B.1    Darlison, M.2
  • 8
    • 77953952024 scopus 로고    scopus 로고
    • The inherited diseases of hemoglobin are an emerging global health burden
    • Weatherall DJ: The inherited diseases of hemoglobin are an emerging global health burden. Blood 2010; 115:4331-4336
    • (2010) Blood , vol.115 , pp. 4331-4336
    • Weatherall, D.J.1
  • 11
    • 79951979504 scopus 로고    scopus 로고
    • Heterogeneity of hemoglobin H disease in childhood
    • Lal A, Goldrich ML, Haines DA, et al.: Heterogeneity of hemoglobin H disease in childhood. N Engl J Med 2011; 364:710-718
    • (2011) N Engl J Med , vol.364 , pp. 710-718
    • Lal, A.1    Goldrich, M.L.2    Haines, D.A.3
  • 13
    • 0036180261 scopus 로고    scopus 로고
    • Clinical phenotypes and molecular characterization of Hb H-Pakse disease
    • Viprakasit V, Tanphaichitr VS, Pung-Amritt P, et al.: Clinical phenotypes and molecular characterization of Hb H-Pakse disease. Haematologica 2002; 87:117-125
    • (2002) Haematologica , vol.87 , pp. 117-125
    • Viprakasit, V.1    Tanphaichitr, V.S.2    Pung-Amritt, P.3
  • 14
    • 84861381296 scopus 로고    scopus 로고
    • The definition and epidemiology of non-transfusion-dependent thalassemia
    • Weatherall DJ: The definition and epidemiology of non-transfusion-dependent thalassemia. Blood Rev 2012; 26(Suppl 1):S3-S6
    • (2012) Blood Rev , vol.26 , pp. S3-S6
    • Weatherall, D.J.1
  • 15
    • 0034875759 scopus 로고    scopus 로고
    • Universal newborn screening for Hb H disease in California
    • Lorey F, Cunningham G, Vichinsky EP, et al.: Universal newborn screening for Hb H disease in California. Genet Test 2001; 5:93-100
    • (2001) Genet Test , vol.5 , pp. 93-100
    • Lorey, F.1    Cunningham, G.2    Vichinsky, E.P.3
  • 16
    • 62449272809 scopus 로고    scopus 로고
    • Newborn screening for hemoglobinopathies in California
    • Michlitsch J, Azimi M, Hoppe C, et al.: Newborn screening for hemoglobinopathies in California. Pediatr Blood Cancer 2009; 52:486-490
    • (2009) Pediatr Blood Cancer , vol.52 , pp. 486-490
    • Michlitsch, J.1    Azimi, M.2    Hoppe, C.3
  • 17
    • 84897518205 scopus 로고    scopus 로고
    • Variable genotype-phenotype correlations in patients with a rare non-deletional α-thalassemia; Hb Pak Num Po (HBA1:c.396_397insT)
    • Sanpakit K, Viprakasit V: Variable genotype-phenotype correlations in patients with a rare non-deletional α-thalassemia; Hb Pak Num Po (HBA1:c.396_397insT). J Pediatr Hematol Oncol 2014; 36:e185-e189.
    • (2014) J Pediatr Hematol Oncol , vol.36 , pp. e185-e189
    • Sanpakit, K.1    Viprakasit, V.2
  • 18
    • 85032559388 scopus 로고    scopus 로고
    • Alpha thalassemia syndromes: from clinical and molecular diagnosis to bedside management
    • EHA 18 Education Book
    • Viprakasit V: Alpha thalassemia syndromes: from clinical and molecular diagnosis to bedside management. EHA 18 Education Book 2013
    • (2013)
    • Viprakasit, V.1
  • 19
    • 84896113701 scopus 로고    scopus 로고
    • Clinical presentation and molecular identification of four uncommon α-globin variants in Thailand: initiation codon mutation of α2-globin gene (HBA2:c.1delA), donor splice site mutation of α1-globin gene (IVSI-1, HBA1:c.95+1G>A), Hemoglobin Queens Park/Chao Pra Ya (HBA1:c.98T>A) and Hemoglobin Westmead (HBA2:c.369C>G)
    • Viprakasit V, Ekwattanakit S, Chalaow N, et al.: Clinical presentation and molecular identification of four uncommon α-globin variants in Thailand: initiation codon mutation of α2-globin gene (HBA2:c.1delA), donor splice site mutation of α1-globin gene (IVSI-1, HBA1:c.95+1G>A), Hemoglobin Queens Park/Chao Pra Ya (HBA1:c.98T>A) and Hemoglobin Westmead (HBA2:c.369C>G). Acta Haematol 2013; 131:88-94
    • (2013) Acta Haematol , vol.131 , pp. 88-94
    • Viprakasit, V.1    Ekwattanakit, S.2    Chalaow, N.3
  • 20
    • 0034889014 scopus 로고    scopus 로고
    • Inherited haemoglobin disorders: an increasing global health problem
    • Weatherall DJ, Clegg JB: Inherited haemoglobin disorders: an increasing global health problem. Bull World Health Organ 2001; 79:704-712
    • (2001) Bull World Health Organ , vol.79 , pp. 704-712
    • Weatherall, D.J.1    Clegg, J.B.2
  • 21
    • 70350287853 scopus 로고    scopus 로고
    • Clinical features and molecular analysis in Thai patients with HbH disease
    • Laosombat V, Viprakasit V, Chotsampancharoen T, et al.: Clinical features and molecular analysis in Thai patients with HbH disease. Ann Hematol 2009; 88:1185-1192
    • (2009) Ann Hematol , vol.88 , pp. 1185-1192
    • Laosombat, V.1    Viprakasit, V.2    Chotsampancharoen, T.3
  • 22
    • 79951553407 scopus 로고    scopus 로고
    • Optimal management of beta thalassaemia intermedia
    • Taher AT, Musallam KM, Cappellini MD, et al.: Optimal management of beta thalassaemia intermedia. Br J Haematol 2011; 152:512-523
    • (2011) Br J Haematol , vol.152 , pp. 512-523
    • Taher, A.T.1    Musallam, K.M.2    Cappellini, M.D.3
  • 23
    • 77950420281 scopus 로고    scopus 로고
    • Overview on practices in thalassemia intermedia management aiming for lowering complication rates across a region of endemicity: the OPTIMAL CARE study
    • Taher AT, Musallam KM, Karimi M, et al.: Overview on practices in thalassemia intermedia management aiming for lowering complication rates across a region of endemicity: the OPTIMAL CARE study. Blood 2010; 115:1886-1892
    • (2010) Blood , vol.115 , pp. 1886-1892
    • Taher, A.T.1    Musallam, K.M.2    Karimi, M.3
  • 24
    • 78649339507 scopus 로고    scopus 로고
    • Splenectomy and thrombosis: the case of thalassemia intermedia
    • Taher AT, Musallam KM, Karimi M, et al.: Splenectomy and thrombosis: the case of thalassemia intermedia. J Thromb Haemost 2010; 8:2152-2158
    • (2010) J Thromb Haemost , vol.8 , pp. 2152-2158
    • Taher, A.T.1    Musallam, K.M.2    Karimi, M.3
  • 26
    • 79959520305 scopus 로고    scopus 로고
    • Health-related quality of life in adults with transfusion-independent thalassaemia intermedia compared to regularly transfused thalassaemia major: new insights
    • Musallam KM, Khoury B, Abi-Habib R, et al.: Health-related quality of life in adults with transfusion-independent thalassaemia intermedia compared to regularly transfused thalassaemia major: new insights. Eur J Haematol 2011; 87:73-79
    • (2011) Eur J Haematol , vol.87 , pp. 73-79
    • Musallam, K.M.1    Khoury, B.2    Abi-Habib, R.3
  • 27
    • 84861362043 scopus 로고    scopus 로고
    • Contemporary approaches to treatment of beta-thalassemia intermedia
    • Taher AT, Musallam KM, Karimi M, et al.: Contemporary approaches to treatment of beta-thalassemia intermedia. Blood Rev 2012; 26(Suppl. 1):S24-S27
    • (2012) Blood Rev , vol.26 , pp. S24-S27
    • Taher, A.T.1    Musallam, K.M.2    Karimi, M.3
  • 28
    • 84861406341 scopus 로고    scopus 로고
    • Recent advances and treatment challenges in patients with non-transfusion-dependent thalassemia
    • Taher AT, Cappellini MD, Musallam KM: Recent advances and treatment challenges in patients with non-transfusion-dependent thalassemia. Blood Rev 2012; 26(Suppl. 1):S1-S2
    • (2012) Blood Rev , vol.26 , pp. S1-S2
    • Taher, A.T.1    Cappellini, M.D.2    Musallam, K.M.3
  • 30
    • 78650072153 scopus 로고    scopus 로고
    • Adaptation to anemia in hemoglobin E-ss thalassemia
    • Allen A, Fisher C, Premawardhena A, et al.: Adaptation to anemia in hemoglobin E-ss thalassemia. Blood 2010; 116:5368-5370
    • (2010) Blood , vol.116 , pp. 5368-5370
    • Allen, A.1    Fisher, C.2    Premawardhena, A.3
  • 31
    • 34547218007 scopus 로고    scopus 로고
    • Age-related changes in adaptation to severe anemia in childhood in developing countries
    • O'Donnell A, Premawardhena A, Arambepola M, et al.: Age-related changes in adaptation to severe anemia in childhood in developing countries. Proc Natl Acad Sci USA 2007; 104:9440-9444
    • (2007) Proc Natl Acad Sci USA , vol.104 , pp. 9440-9444
    • O'Donnell, A.1    Premawardhena, A.2    Arambepola, M.3
  • 33
    • 26944485129 scopus 로고    scopus 로고
    • Haemoglobin E beta thalassaemia in Sri Lanka
    • Premawardhena A, Fisher CA, Olivieri NF, et al.: Haemoglobin E beta thalassaemia in Sri Lanka. Lancet 2005; 366:1467-1470
    • (2005) Lancet , vol.366 , pp. 1467-1470
    • Premawardhena, A.1    Fisher, C.A.2    Olivieri, N.F.3
  • 34
    • 1942425504 scopus 로고    scopus 로고
    • Evaluation of alpha hemoglobin stabilizing protein (AHSP) as a genetic modifier in patients with beta thalassemia
    • Viprakasit V, Tanphaichitr VS, Chinchang W, et al.: Evaluation of alpha hemoglobin stabilizing protein (AHSP) as a genetic modifier in patients with beta thalassemia. Blood 2004; 103:3296-3299
    • (2004) Blood , vol.103 , pp. 3296-3299
    • Viprakasit, V.1    Tanphaichitr, V.S.2    Chinchang, W.3
  • 36
    • 34248147571 scopus 로고    scopus 로고
    • Noninfectious complications of blood transfusion
    • Eder AF, Chambers LA: Noninfectious complications of blood transfusion. Arch Pathol Lab Med 2007; 131:708-718
    • (2007) Arch Pathol Lab Med , vol.131 , pp. 708-718
    • Eder, A.F.1    Chambers, L.A.2
  • 37
    • 84861357425 scopus 로고    scopus 로고
    • The role of ineffective erythropoiesis in non-transfusion-dependent thalassemia
    • Rivella S: The role of ineffective erythropoiesis in non-transfusion-dependent thalassemia. Blood Rev 2012; 26(Suppl. 1):S12-S15
    • (2012) Blood Rev , vol.26 , pp. S12-S15
    • Rivella, S.1
  • 39
    • 77954533701 scopus 로고    scopus 로고
    • Paraspinal extramedullary hematopoiesis in patients with thalassemia intermedia
    • Haidar R, Mhaidli H, Taher AT: Paraspinal extramedullary hematopoiesis in patients with thalassemia intermedia. Eur Spine J 2010; 19:871-878
    • (2010) Eur Spine J , vol.19 , pp. 871-878
    • Haidar, R.1    Mhaidli, H.2    Taher, A.T.3
  • 40
    • 0023100003 scopus 로고
    • Erythroid marrow function in anemic patients
    • Cazzola M, Pootrakul P, Huebers HA, et al.: Erythroid marrow function in anemic patients. Blood 1987; 69:296-301
    • (1987) Blood , vol.69 , pp. 296-301
    • Cazzola, M.1    Pootrakul, P.2    Huebers, H.A.3
  • 41
    • 0023272594 scopus 로고
    • Evaluation of erythroid marrow function in anemic patients
    • Cazzola M, Finch CA: Evaluation of erythroid marrow function in anemic patients. Haematologica 1987; 72:195-200
    • (1987) Haematologica , vol.72 , pp. 195-200
    • Cazzola, M.1    Finch, C.A.2
  • 42
    • 0028937612 scopus 로고
    • Relationship between transfusion regimen and suppression of erythropoiesis in beta-thalassaemia major
    • Cazzola M, De Stefano P, Ponchio L, et al.: Relationship between transfusion regimen and suppression of erythropoiesis in beta-thalassaemia major. Br J Haematol 1995; 89:473-478
    • (1995) Br J Haematol , vol.89 , pp. 473-478
    • Cazzola, M.1    De Stefano, P.2    Ponchio, L.3
  • 43
    • 84857366913 scopus 로고    scopus 로고
    • Brain positron emission tomography in splenectomized adults with beta-thalassemia intermedia: uncovering yet another covert abnormality
    • Musallam KM, Nasreddine W, Beydoun A, et al.: Brain positron emission tomography in splenectomized adults with beta-thalassemia intermedia: uncovering yet another covert abnormality. Ann Hematol 2012; 91:235-241
    • (2012) Ann Hematol , vol.91 , pp. 235-241
    • Musallam, K.M.1    Nasreddine, W.2    Beydoun, A.3
  • 44
    • 33749872392 scopus 로고    scopus 로고
    • Prevalence of thromboembolic events among 8,860 patients with thalassaemia major and intermedia in the Mediterranean area and Iran
    • Taher A, Isma'eel H, Mehio G, et al.: Prevalence of thromboembolic events among 8, 860 patients with thalassaemia major and intermedia in the Mediterranean area and Iran. Thromb Haemost 2006; 96:488-491
    • (2006) Thromb Haemost , vol.96 , pp. 488-491
    • Taher, A.1    Isma'eel, H.2    Mehio, G.3
  • 45
    • 84861397221 scopus 로고    scopus 로고
    • Advances in the treatment of alpha-thalassemia
    • Vichinsky E: Advances in the treatment of alpha-thalassemia. Blood Rev 2012; 26(Suppl 1):S31-S34
    • (2012) Blood Rev , vol.26 , pp. S31-S34
    • Vichinsky, E.1
  • 46
    • 0021368961 scopus 로고
    • Non-transferrin plasma iron in beta-thalassaemia/Hb E and haemoglobin H diseases
    • Anuwatanakulchai M, Pootrakul P, Thuvasethakul P, et al.: Non-transferrin plasma iron in beta-thalassaemia/Hb E and haemoglobin H diseases. Scand J Haematol 1984; 32:153-158
    • (1984) Scand J Haematol , vol.32 , pp. 153-158
    • Anuwatanakulchai, M.1    Pootrakul, P.2    Thuvasethakul, P.3
  • 47
    • 0019311766 scopus 로고
    • Increased transferrin iron saturation in splenectomized thalassaemic patients
    • Pootrakul P, Rugkiatsakul R, Wasi P: Increased transferrin iron saturation in splenectomized thalassaemic patients. Br J Haematol 1980; 46:143-145
    • (1980) Br J Haematol , vol.46 , pp. 143-145
    • Pootrakul, P.1    Rugkiatsakul, R.2    Wasi, P.3
  • 48
    • 0019814079 scopus 로고
    • Serum ferritin levels in thalassemias and the effect of splenectomy
    • Pootrakul P, Vongsmasa V, La-ongpanich P, et al.: Serum ferritin levels in thalassemias and the effect of splenectomy. Acta Haematol 1981; 66:244-250
    • (1981) Acta Haematol , vol.66 , pp. 244-250
    • Pootrakul, P.1    Vongsmasa, V.2    La-ongpanich, P.3
  • 49
    • 70449368579 scopus 로고    scopus 로고
    • Iron overload in thalassaemia intermedia: reassessment of iron chelation strategies
    • Taher A, Hershko C, Cappellini MD: Iron overload in thalassaemia intermedia: reassessment of iron chelation strategies. Br J Haematol 2009; 147:634-640
    • (2009) Br J Haematol , vol.147 , pp. 634-640
    • Taher, A.1    Hershko, C.2    Cappellini, M.D.3
  • 50
    • 84861399953 scopus 로고    scopus 로고
    • Iron overload in non-transfusion-dependent thalassemia: a clinical perspective
    • Musallam KM, Cappellini MD, Wood JC, et al.: Iron overload in non-transfusion-dependent thalassemia: a clinical perspective. Blood Rev 2012; 26(Suppl 1):S16-S19
    • (2012) Blood Rev , vol.26 , pp. S16-S19
    • Musallam, K.M.1    Cappellini, M.D.2    Wood, J.C.3
  • 51
    • 80455143324 scopus 로고    scopus 로고
    • Elevated liver iron concentration is a marker of increased morbidity in patients with beta thalassemia intermedia
    • Musallam KM, Cappellini MD, Wood JC, et al.: Elevated liver iron concentration is a marker of increased morbidity in patients with beta thalassemia intermedia. Haematologica 2011; 96:1605-1612
    • (2011) Haematologica , vol.96 , pp. 1605-1612
    • Musallam, K.M.1    Cappellini, M.D.2    Wood, J.C.3
  • 52
    • 77954319602 scopus 로고    scopus 로고
    • Hepatocellular carcinoma in patients with thalassaemia syndromes: clinical characteristics and outcome in a long term single centre experience
    • Restivo Pantalone G, Renda D, Valenza F, et al.: Hepatocellular carcinoma in patients with thalassaemia syndromes: clinical characteristics and outcome in a long term single centre experience. Br J Haematol 2010; 150:245-247
    • (2010) Br J Haematol , vol.150 , pp. 245-247
    • Restivo Pantalone, G.1    Renda, D.2    Valenza, F.3
  • 53
    • 84861366756 scopus 로고    scopus 로고
    • Hypercoagulability in non-transfusion-dependent thalassemia
    • Cappellini MD, Musallam KM, Poggiali E, et al.: Hypercoagulability in non-transfusion-dependent thalassemia. Blood Rev 2012; 26(Suppl. 1):S20-S23
    • (2012) Blood Rev , vol.26 , pp. S20-S23
    • Cappellini, M.D.1    Musallam, K.M.2    Poggiali, E.3
  • 54
    • 73049084139 scopus 로고    scopus 로고
    • Asymptomatic brain magnetic resonance imaging abnormalities in splenectomized adults with thalassemia intermedia
    • Taher AT, Musallam KM, Nasreddine W, et al.: Asymptomatic brain magnetic resonance imaging abnormalities in splenectomized adults with thalassemia intermedia. J Thromb Haemost 2010; 8:54-59
    • (2010) J Thromb Haemost , vol.8 , pp. 54-59
    • Taher, A.T.1    Musallam, K.M.2    Nasreddine, W.3
  • 55
    • 33750828453 scopus 로고    scopus 로고
    • Enhanced aggregability of red blood cells of beta-thalassemia major patients
    • Chen S, Eldor A, Barshtein G, et al.: Enhanced aggregability of red blood cells of beta-thalassemia major patients. Am J Physiol 1996; 270:H1951-H1956
    • (1996) Am J Physiol , vol.270 , pp. H1951-H1956
    • Chen, S.1    Eldor, A.2    Barshtein, G.3
  • 57
  • 59
    • 0035383809 scopus 로고    scopus 로고
    • Cardiac involvement in thalassemia intermedia: a multicenter study
    • Aessopos A, Farmakis D, Karagiorga M, et al.: Cardiac involvement in thalassemia intermedia: a multicenter study. Blood 2001; 97:3411-3416
    • (2001) Blood , vol.97 , pp. 3411-3416
    • Aessopos, A.1    Farmakis, D.2    Karagiorga, M.3
  • 60
    • 84919620138 scopus 로고    scopus 로고
    • Effect of genotype on pulmonary hypertension in patients with thalassemia
    • abst 3456
    • Teawtrakul N, Ungprasert P, Pussadhamma B, et al.: Effect of genotype on pulmonary hypertension in patients with thalassemia. Blood 2013; 122:abst 3456
    • (2013) Blood , vol.122
    • Teawtrakul, N.1    Ungprasert, P.2    Pussadhamma, B.3
  • 61
    • 84919620137 scopus 로고    scopus 로고
    • Features associated with pulmonary hypertension in splenectomized patients with hemoglobin E/β-thalassemia disease
    • abst 3457
    • Chuncharunee S, Atichartakarn V, Udomsubpayakul U, et al.: Features associated with pulmonary hypertension in splenectomized patients with hemoglobin E/β-thalassemia disease. Blood 2013; 122:abst 3457
    • (2013) Blood , vol.122
    • Chuncharunee, S.1    Atichartakarn, V.2    Udomsubpayakul, U.3
  • 62
    • 84856870900 scopus 로고    scopus 로고
    • Clinical indicators for pulmonary arterial hypertension in thalassemia
    • Chueamuangphan N, Wongtheptien W, Nawarawong W, et al.: Clinical indicators for pulmonary arterial hypertension in thalassemia. J Med Assoc Thai 2012; 95:16-21
    • (2012) J Med Assoc Thai , vol.95 , pp. 16-21
    • Chueamuangphan, N.1    Wongtheptien, W.2    Nawarawong, W.3
  • 63
    • 84878097741 scopus 로고    scopus 로고
    • Pulmonary hypertension risk in patients with haemoglobin H disease: low incidence and absence of correlation with splenectomy
    • Yin X, Zhang X, Wu Z, et al.: Pulmonary hypertension risk in patients with haemoglobin H disease: low incidence and absence of correlation with splenectomy. Acta Haematol 2013; 130:153-159
    • (2013) Acta Haematol , vol.130 , pp. 153-159
    • Yin, X.1    Zhang, X.2    Wu, Z.3
  • 64
    • 51749090631 scopus 로고    scopus 로고
    • Relation between iron-overload indices, cardiac echo-Doppler, and biochemical markers in thalassemia intermedia
    • Isma'eel H, Chafic AH, Rassi FE, et al.: Relation between iron-overload indices, cardiac echo-Doppler, and biochemical markers in thalassemia intermedia. Am J Cardiol 2008; 102:363-367
    • (2008) Am J Cardiol , vol.102 , pp. 363-367
    • Isma'eel, H.1    Chafic, A.H.2    Rassi, F.E.3
  • 65
    • 77955907561 scopus 로고    scopus 로고
    • Pulmonary hypertension in thalassemia
    • Morris CR, Vichinsky EP: Pulmonary hypertension in thalassemia. Ann N Y Acad Sci 2010; 1202:205-213
    • (2010) Ann N Y Acad Sci , vol.1202 , pp. 205-213
    • Morris, C.R.1    Vichinsky, E.P.2
  • 66
    • 33750089012 scopus 로고    scopus 로고
    • Splenectomy: a strong risk factor for pulmonary hypertension in patients with thalassaemia
    • Phrommintikul A, Sukonthasarn A, Kanjanavanit R, et al.: Splenectomy: a strong risk factor for pulmonary hypertension in patients with thalassaemia. Heart 2006; 92:1467-1472
    • (2006) Heart , vol.92 , pp. 1467-1472
    • Phrommintikul, A.1    Sukonthasarn, A.2    Kanjanavanit, R.3
  • 67
    • 33748102660 scopus 로고    scopus 로고
    • Pulmonary hypertension in thalassemia: association with platelet activation and hypercoagulable state
    • Singer ST, Kuypers FA, Styles L, et al.: Pulmonary hypertension in thalassemia: association with platelet activation and hypercoagulable state. Am J Hematol 2006; 81:670-675
    • (2006) Am J Hematol , vol.81 , pp. 670-675
    • Singer, S.T.1    Kuypers, F.A.2    Styles, L.3
  • 68
    • 0028887358 scopus 로고
    • Pulmonary hypertension and right heart failure in patients with beta-thalassemia intermedia
    • Aessopos A, Stamatelos G, Skoumas V, et al.: Pulmonary hypertension and right heart failure in patients with beta-thalassemia intermedia. Chest 1995; 107:50-53
    • (1995) Chest , vol.107 , pp. 50-53
    • Aessopos, A.1    Stamatelos, G.2    Skoumas, V.3
  • 69
    • 0034868447 scopus 로고    scopus 로고
    • Recommendations on the management of pulmonary hypertension in clinical practice
    • Gibbs JSR, Higenbottam TW: Recommendations on the management of pulmonary hypertension in clinical practice. Heart 2001; 86:i1-i13
    • (2001) Heart , vol.86 , pp. i1-i13
    • Gibbs, J.S.R.1    Higenbottam, T.W.2
  • 70
    • 0013106093 scopus 로고    scopus 로고
    • Treatment of pulmonary hypertension in sickle cell disease with transfusion
    • abst 420a
    • Claster S, Hammer M, Hagar W, et al.: Treatment of pulmonary hypertension in sickle cell disease with transfusion. Blood 1999; 94(Suppl 1):abst 420a
    • (1999) Blood , vol.94
    • Claster, S.1    Hammer, M.2    Hagar, W.3
  • 71
    • 1642327238 scopus 로고    scopus 로고
    • Correction of hypercoagulability and amelioration of pulmonary arterial hypertension by chronic blood transfusion in an asplenic hemoglobin E/beta-thalassemia patient
    • Atichartakarn V, Chuncharunee S, Chandanamattha P, et al.: Correction of hypercoagulability and amelioration of pulmonary arterial hypertension by chronic blood transfusion in an asplenic hemoglobin E/beta-thalassemia patient. Blood 2004; 103:2844-2846
    • (2004) Blood , vol.103 , pp. 2844-2846
    • Atichartakarn, V.1    Chuncharunee, S.2    Chandanamattha, P.3
  • 72
    • 77955160429 scopus 로고    scopus 로고
    • Age-related complications in treatment-naive patients with thalassaemia intermedia
    • Taher AT, Musallam KM, El-Beshlawy A, et al.: Age-related complications in treatment-naive patients with thalassaemia intermedia. Br J Haematol 2010; 150:486-489
    • (2010) Br J Haematol , vol.150 , pp. 486-489
    • Taher, A.T.1    Musallam, K.M.2    El-Beshlawy, A.3
  • 73
    • 79957652924 scopus 로고    scopus 로고
    • Healing of refractory leg ulcer in a patient with thalassemia intermedia and hypercoagulability after 14 years of unresponsive therapy
    • Levin C, Koren A: Healing of refractory leg ulcer in a patient with thalassemia intermedia and hypercoagulability after 14 years of unresponsive therapy. Isr Med Assoc J 2011; 13:316-318
    • (2011) Isr Med Assoc J , vol.13 , pp. 316-318
    • Levin, C.1    Koren, A.2
  • 74
    • 0037929823 scopus 로고    scopus 로고
    • Phenotype score to grade the severity of thalassemia intermedia
    • Phadke SR, Agarwal S: Phenotype score to grade the severity of thalassemia intermedia. Indian J Pediatr 2003; 70:477-481
    • (2003) Indian J Pediatr , vol.70 , pp. 477-481
    • Phadke, S.R.1    Agarwal, S.2
  • 76
    • 0035409398 scopus 로고    scopus 로고
    • Linear growth in homozygous beta-thalassemia and beta-thalassemia/hemoglobin E patients under different treatment regimens
    • Viprakasit V, Tanphaichitr VS, Mahasandana C, et al.: Linear growth in homozygous beta-thalassemia and beta-thalassemia/hemoglobin E patients under different treatment regimens. J Med Assoc Thai 2001; 84:929-941
    • (2001) J Med Assoc Thai , vol.84 , pp. 929-941
    • Viprakasit, V.1    Tanphaichitr, V.S.2    Mahasandana, C.3
  • 77
    • 84887465313 scopus 로고    scopus 로고
    • Adrenal insufficiency is prevalent in HbE/beta-thalassaemia paediatric patients irrespective of their clinical severity and transfusion requirement
    • Nakavachara P, Viprakasit V: Adrenal insufficiency is prevalent in HbE/beta-thalassaemia paediatric patients irrespective of their clinical severity and transfusion requirement. Clin Endocrinol (Oxf) 2013; 79:776-783.
    • (2013) Clin Endocrinol (Oxf) , vol.79 , pp. 776-783
    • Nakavachara, P.1    Viprakasit, V.2
  • 78
    • 84881533685 scopus 로고    scopus 로고
    • Children with hemoglobin E/beta-thalassemia have a high risk of being vitamin D deficient even if they get abundant sun exposure: a study from Thailand
    • Nakavachara P, Viprakasit V: Children with hemoglobin E/beta-thalassemia have a high risk of being vitamin D deficient even if they get abundant sun exposure: a study from Thailand. Pediatr Blood Cancer 2013; 60:1683-1688
    • (2013) Pediatr Blood Cancer , vol.60 , pp. 1683-1688
    • Nakavachara, P.1    Viprakasit, V.2
  • 79
    • 33749343758 scopus 로고    scopus 로고
    • Low serum levels of 25-hydroxy vitamin D in adults affected by thalassemia major or intermedia
    • Napoli N, Carmina E, Bucchieri S, et al.: Low serum levels of 25-hydroxy vitamin D in adults affected by thalassemia major or intermedia. Bone 2006; 38:888-892
    • (2006) Bone , vol.38 , pp. 888-892
    • Napoli, N.1    Carmina, E.2    Bucchieri, S.3
  • 80
    • 84907977691 scopus 로고    scopus 로고
    • Osteopenia is commonly present in prepubertal children with severe HbE/βthalassemia despite adequate transfusion and iron chelation therapy
    • abst 3830
    • Viprakasit V, Sawathiparnich P, Sangpraypanm T, et al.: Osteopenia is commonly present in prepubertal children with severe HbE/βthalassemia despite adequate transfusion and iron chelation therapy. Blood 2007; 110:abst 3830
    • (2007) Blood , vol.110
    • Viprakasit, V.1    Sawathiparnich, P.2    Sangpraypanm, T.3
  • 81
    • 0025124580 scopus 로고
    • Red cell alloantibodies in patients with thalassemia
    • Spanos T, Karageorga M, Ladis V, et al.: Red cell alloantibodies in patients with thalassemia. Vox Sang 1990; 58:50-55
    • (1990) Vox Sang , vol.58 , pp. 50-55
    • Spanos, T.1    Karageorga, M.2    Ladis, V.3
  • 82
    • 0021809144 scopus 로고
    • Red cell alloantibodies in thalassemia major. Results of an Italian cooperative study
    • Sirchia G, Zanella A, Parravicini A, et al.: Red cell alloantibodies in thalassemia major. Results of an Italian cooperative study. Transfusion 1985; 25:110-112
    • (1985) Transfusion , vol.25 , pp. 110-112
    • Sirchia, G.1    Zanella, A.2    Parravicini, A.3
  • 83
    • 0034669984 scopus 로고    scopus 로고
    • Alloimmunization and erythrocyte autoimmunization in transfusion-dependent thalassemia patients of predominantly asian descent
    • Singer ST, Wu V, Mignacca R, et al.: Alloimmunization and erythrocyte autoimmunization in transfusion-dependent thalassemia patients of predominantly asian descent. Blood 2000; 96:3369-3373
    • (2000) Blood , vol.96 , pp. 3369-3373
    • Singer, S.T.1    Wu, V.2    Mignacca, R.3
  • 84
    • 84868213735 scopus 로고    scopus 로고
    • Challenges of alloimmunization in patients with haemoglobinopathies
    • Chou ST, Liem RI, Thompson AA: Challenges of alloimmunization in patients with haemoglobinopathies. Br J Haematol 2012; 159:394-404
    • (2012) Br J Haematol , vol.159 , pp. 394-404
    • Chou, S.T.1    Liem, R.I.2    Thompson, A.A.3
  • 85
    • 84865159173 scopus 로고    scopus 로고
    • Prevalence of alloimmunisation in patients with beta thalassaemia major
    • Kosaryan M, Mahdavi MR, Roshan P, et al.: Prevalence of alloimmunisation in patients with beta thalassaemia major. Blood Transfus 2012; 10:396-397
    • (2012) Blood Transfus , vol.10 , pp. 396-397
    • Kosaryan, M.1    Mahdavi, M.R.2    Roshan, P.3
  • 86
    • 84898633977 scopus 로고    scopus 로고
    • Transfusion complications in thalassemia patients: a report from the Centers for Disease Control and Prevention
    • Vichinsky E, Neumayr L, Trimble S, et al.: Transfusion complications in thalassemia patients: a report from the Centers for Disease Control and Prevention. Transfusion 2014; 54:972-981
    • (2014) Transfusion , vol.54 , pp. 972-981
    • Vichinsky, E.1    Neumayr, L.2    Trimble, S.3
  • 87
    • 79952607066 scopus 로고    scopus 로고
    • Red cell alloimmunization in a diverse population of transfused patients with thalassaemia
    • Thompson AA, Cunningham MJ, Singer ST, et al.: Red cell alloimmunization in a diverse population of transfused patients with thalassaemia. Br J Haematol 2011; 153:121-128
    • (2011) Br J Haematol , vol.153 , pp. 121-128
    • Thompson, A.A.1    Cunningham, M.J.2    Singer, S.T.3
  • 88
    • 84930041196 scopus 로고    scopus 로고
    • Transfusion therapy and alloimmunization in thalassemia intermedia: a 10 year experience at a tertiary care university hospital
    • (Epub ahead of print)
    • Al-Riyami AZ, Al-Mahrooqi S, Al-Hinai S, et al.: Transfusion therapy and alloimmunization in thalassemia intermedia: a 10 year experience at a tertiary care university hospital. Transfus Apher Sci 2014, http://dx.doi.org/10.1016/j.transci.2014.04.009 (Epub ahead of print)
    • (2014) Transfus Apher Sci
    • Al-Riyami, A.Z.1    Al-Mahrooqi, S.2    Al-Hinai, S.3
  • 89
    • 54349095611 scopus 로고    scopus 로고
    • Correlation of liver iron concentration determined by R2 magnetic resonance imaging with serum ferritin in patients with thalassemia intermedia
    • Taher A, El RF, Isma'eel H, et al.: Correlation of liver iron concentration determined by R2 magnetic resonance imaging with serum ferritin in patients with thalassemia intermedia. Haematologica 2008; 93:1584-1586
    • (2008) Haematologica , vol.93 , pp. 1584-1586
    • Taher, A.1    El, R.F.2    Isma'eel, H.3
  • 90
    • 77950377763 scopus 로고    scopus 로고
    • Magnetic resonance evaluation of hepatic and myocardial iron deposition in transfusion-independent thalassemia intermedia compared to regularly transfused thalassemia major patients
    • Taher AT, Musallam KM, Wood JC, et al.: Magnetic resonance evaluation of hepatic and myocardial iron deposition in transfusion-independent thalassemia intermedia compared to regularly transfused thalassemia major patients. Am J Hematol 2010; 85:288-290
    • (2010) Am J Hematol , vol.85 , pp. 288-290
    • Taher, A.T.1    Musallam, K.M.2    Wood, J.C.3
  • 91
    • 84876713390 scopus 로고    scopus 로고
    • Treating iron overload in patients with non-transfusion-dependent thalassemia
    • Taher AT, Viprakasit V, Musallam KM, et al.: Treating iron overload in patients with non-transfusion-dependent thalassemia. Am J Hematol 2013; 88:409-415
    • (2013) Am J Hematol , vol.88 , pp. 409-415
    • Taher, A.T.1    Viprakasit, V.2    Musallam, K.M.3
  • 92
    • 84865346929 scopus 로고    scopus 로고
    • T2* MRI in regularly transfused children with thalassemia intermedia: serum ferritin does not reflect liver iron stores
    • Tony S, Daar S, Elshinawy M, et al.: T2* MRI in regularly transfused children with thalassemia intermedia: serum ferritin does not reflect liver iron stores. Pediatr Hematol Oncol 2012; 29:579-584
    • (2012) Pediatr Hematol Oncol , vol.29 , pp. 579-584
    • Tony, S.1    Daar, S.2    Elshinawy, M.3
  • 93
    • 84864530218 scopus 로고    scopus 로고
    • Deferasirox reduces iron overload significantly in nontransfusion-dependent thalassemia: 1-year results from a prospective, randomized, double-blind, placebo-controlled study
    • Taher AT, Porter J, Viprakasit V, et al.: Deferasirox reduces iron overload significantly in nontransfusion-dependent thalassemia: 1-year results from a prospective, randomized, double-blind, placebo-controlled study. Blood 2012; 120:970-977
    • (2012) Blood , vol.120 , pp. 970-977
    • Taher, A.T.1    Porter, J.2    Viprakasit, V.3
  • 95
    • 33845878540 scopus 로고    scopus 로고
    • Clinical and molecular analysis of haemoglobin H disease in Sardinia: haematological, obstetric and cardiac aspects in patients with different genotypes
    • Origa R, Sollaino MC, Giagu N, et al.: Clinical and molecular analysis of haemoglobin H disease in Sardinia: haematological, obstetric and cardiac aspects in patients with different genotypes. Br J Haematol 2007; 136:326-332
    • (2007) Br J Haematol , vol.136 , pp. 326-332
    • Origa, R.1    Sollaino, M.C.2    Giagu, N.3


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.