메뉴 건너뛰기




Volumn 100, Issue 1, 2015, Pages 48-53

Sickle cell disease: A neglected chronic disease of increasing global health importance

Author keywords

[No Author keywords available]

Indexed keywords

HAEMOPHILUS VACCINE; HEMOGLOBIN S; HYDROXYUREA; LEAD; PNEUMOCOCCUS VACCINE; VANILLOID RECEPTOR 1;

EID: 84919344025     PISSN: 00039888     EISSN: 14682044     Source Type: Journal    
DOI: 10.1136/archdischild-2013-303773     Document Type: Article
Times cited : (122)

References (86)
  • 1
    • 0014102102 scopus 로고
    • Structure of sickle cell hemoglobin and molecular mechanism of the sickling phenomenon
    • Murayama M. Structure of sickle cell hemoglobin and molecular mechanism of the sickling phenomenon. Clin Chem 1967;13:578-88.
    • (1967) Clin Chem , vol.13 , pp. 578-588
    • Murayama, M.1
  • 2
    • 44949128064 scopus 로고    scopus 로고
    • Global epidemiology of haemoglobin disorders and derived service indicators
    • Modell B, Darlison M. Global epidemiology of haemoglobin disorders and derived service indicators. Bull World Health Organ 2008;86:480-7.
    • (2008) Bull World Health Organ , vol.86 , pp. 480-487
    • Modell, B.1    Darlison, M.2
  • 4
    • 79952138729 scopus 로고    scopus 로고
    • Hb S-beta-thalassemia: Molecular, hematological and clinical comparisons
    • Serjeant GR, Serjeant BE, Fraser RA, et al. Hb S-beta-thalassemia: molecular, hematological and clinical comparisons. Hemoglobin 2011;35:1-12.
    • (2011) Hemoglobin , vol.35 , pp. 1-12
    • Serjeant, G.R.1    Serjeant, B.E.2    Fraser, R.A.3
  • 5
    • 0034897892 scopus 로고    scopus 로고
    • Peculiar elongated and sickle-shaped red blood corpuscles in a case of severe anemia. 1910
    • Herrick JB. Peculiar elongated and sickle-shaped red blood corpuscles in a case of severe anemia. 1910. Yale J Biol Med 2001;74:179-84.
    • (2001) Yale J Biol Med , vol.74 , pp. 179-184
    • Herrick, J.B.1
  • 6
    • 0000192486 scopus 로고
    • Sickle cell anemia a molecular disease
    • Pauling L, Itano HA, Singer SJ, et al. Sickle cell anemia a molecular disease. Science 1949;110:543-8.
    • (1949) Science , vol.110 , pp. 543-548
    • Pauling, L.1    Itano, H.A.2    Singer, S.J.3
  • 7
    • 0000420850 scopus 로고
    • A specific chemical difference between the globins of normal human and sickle-cell anaemia haemoglobin
    • Ingram VM. A specific chemical difference between the globins of normal human and sickle-cell anaemia haemoglobin. Nature 1956;178:792-4.
    • (1956) Nature , vol.178 , pp. 792-794
    • Ingram, V.M.1
  • 8
    • 0000294402 scopus 로고
    • Detection of sickle cell beta S-globin allele by hybridization with synthetic oligonucleotides
    • Conner BJ, Reyes AA, Morin C, et al. Detection of sickle cell beta S-globin allele by hybridization with synthetic oligonucleotides. Proc Natl Acad Sci USA 1983;80:278-82.
    • (1983) Proc Natl Acad Sci USA , vol.80 , pp. 278-282
    • Conner, B.J.1    Reyes, A.A.2    Morin, C.3
  • 9
    • 0015495945 scopus 로고
    • Detection of the sickle gene in the human fetus. Potential for intrauterine diagnosis of sickle-cell anemia
    • Kan YW, Dozy AM, Alter BP, et al. Detection of the sickle gene in the human fetus. Potential for intrauterine diagnosis of sickle-cell anemia. N Engl J Med 1972;287:1-5.
    • (1972) N Engl J Med , vol.287 , pp. 1-5
    • Kan, Y.W.1    Dozy, A.M.2    Alter, B.P.3
  • 11
    • 0014963910 scopus 로고
    • Health care priority and sickle cell anemia
    • Scott RB. Health care priority and sickle cell anemia. JAMA 1970;214:731-4.
    • (1970) JAMA , vol.214 , pp. 731-734
    • Scott, R.B.1
  • 12
    • 0028291736 scopus 로고
    • Mortality in sickle cell disease. Life expectancy and risk factors for early death
    • Platt OS, Brambilla DJ, Rosse WF, et al. Mortality in sickle cell disease. Life expectancy and risk factors for early death. N Engl J Med 1994;330:1639-44.
    • (1994) N Engl J Med , vol.330 , pp. 1639-1644
    • Platt, O.S.1    Brambilla, D.J.2    Rosse, W.F.3
  • 13
    • 0024446352 scopus 로고
    • Mortality in children and adolescents with sickle cell disease. Cooperative Study of Sickle Cell Disease
    • Leikin SL, Gallagher D, Kinney TR, et al. Mortality in children and adolescents with sickle cell disease. Cooperative Study of Sickle Cell Disease. Pediatrics 1989;84:500-8.
    • (1989) Pediatrics , vol.84 , pp. 500-508
    • Leikin, S.L.1    Gallagher, D.2    Kinney, T.R.3
  • 14
    • 2542455639 scopus 로고    scopus 로고
    • Survival of children with sickle cell disease
    • Quinn CT, Rogers ZR, Buchanan GR. Survival of children with sickle cell disease. Blood 2004;103:4023-7.
    • (2004) Blood , vol.103 , pp. 4023-4027
    • Quinn, C.T.1    Rogers, Z.R.2    Buchanan, G.R.3
  • 15
    • 0035799111 scopus 로고    scopus 로고
    • Survival estimates for patients with homozygous sickle-cell disease in Jamaica: A clinic-based population study
    • Wierenga KJ, Hambleton IR, Lewis NA. Survival estimates for patients with homozygous sickle-cell disease in Jamaica: a clinic-based population study. Lancet 2001;357:680-3.
    • (2001) Lancet , vol.357 , pp. 680-683
    • Wierenga, K.J.1    Hambleton, I.R.2    Lewis, N.A.3
  • 16
    • 34548753905 scopus 로고    scopus 로고
    • Clinical outcomes in children with sickle cell disease living in England: A neonatal cohort in East London
    • Telfer P, Coen P, Chakravorty S, et al. Clinical outcomes in children with sickle cell disease living in England: a neonatal cohort in East London. Haematologica 2007;92:905-12.
    • (2007) Haematologica , vol.92 , pp. 905-912
    • Telfer, P.1    Coen, P.2    Chakravorty, S.3
  • 17
    • 77951712618 scopus 로고    scopus 로고
    • Improved survival of children and adolescents with sickle cell disease
    • Quinn CT, Rogers ZR, McCavit TL, et al. Improved survival of children and adolescents with sickle cell disease. Blood 2010;115:3447-52.
    • (2010) Blood , vol.115 , pp. 3447-3452
    • Quinn, C.T.1    Rogers, Z.R.2    McCavit, T.L.3
  • 18
    • 84880360759 scopus 로고    scopus 로고
    • Sickle Cell Disease Related Mortality in the United States (1999-2009)
    • Hamideh D, Alvarez O. Sickle Cell Disease Related Mortality in the United States (1999-2009). Pediatr Blood Cancer 2013;60:1482-6.
    • (2013) Pediatr Blood Cancer , vol.60 , pp. 1482-1486
    • Hamideh, D.1    Alvarez, O.2
  • 19
    • 77049164783 scopus 로고
    • Protection afforded by sickle-cell trait against subtertian malareal infection
    • Allison AC. Protection afforded by sickle-cell trait against subtertian malareal infection. Br Med J 1954;1:290-4.
    • (1954) Br Med J , vol.1 , pp. 290-294
    • Allison, A.C.1
  • 20
    • 84878481415 scopus 로고    scopus 로고
    • Hemoglobinopathies: Slicing the Gordian knot of Plasmodium falciparum malaria pathogenesis
    • Taylor SM, Cerami C, Fairhurst RM. Hemoglobinopathies: slicing the Gordian knot of Plasmodium falciparum malaria pathogenesis. PLoS Pathog 2013;9:e1003327.
    • (2013) PLoS Pathog , vol.9 , pp. e1003327
    • Taylor, S.M.1    Cerami, C.2    Fairhurst, R.M.3
  • 21
    • 78650101852 scopus 로고    scopus 로고
    • Global distribution of the sickle cell gene and geographical confirmation of the malaria hypothesis
    • Piel FB, Patil AP, Howes RE, et al. Global distribution of the sickle cell gene and geographical confirmation of the malaria hypothesis. Nat Commun 2010;1:104.
    • (2010) Nat Commun , vol.1 , pp. 104
    • Piel, F.B.1    Patil, A.P.2    Howes, R.E.3
  • 22
    • 81355163446 scopus 로고    scopus 로고
    • Sickle cell disease in Africa: A neglected cause of early childhood mortality
    • Grosse SD, Odame I, Atrash HK, et al. Sickle cell disease in Africa: a neglected cause of early childhood mortality. Am J Prev Med 2011;41:S398-405.
    • (2011) Am J Prev Med , vol.41 , pp. S398-405
    • Grosse, S.D.1    Odame, I.2    Atrash, H.K.3
  • 23
    • 84892951517 scopus 로고    scopus 로고
    • Global migration and the changing distribution of sickle haemoglobin: A quantitative study of temporal trends between 1960 and 2000
    • Piel FB, Tatem AJ, Huang Z, et al. Global migration and the changing distribution of sickle haemoglobin: a quantitative study of temporal trends between 1960 and 2000. Lancet Glob Health 2014;2:e80-9.
    • (2014) Lancet Glob Health , vol.2 , pp. e80-e89
    • Piel, F.B.1    Tatem, A.J.2    Huang, Z.3
  • 24
    • 84872062977 scopus 로고    scopus 로고
    • Global epidemiology of sickle haemoglobin in neonates: A contemporary geostatistical model-based map and population estimates
    • Piel FB, Patil AP, Howes RE, et al. Global epidemiology of sickle haemoglobin in neonates: a contemporary geostatistical model-based map and population estimates. Lancet 2013;381:142-51.
    • (2013) Lancet , vol.381 , pp. 142-151
    • Piel, F.B.1    Patil, A.P.2    Howes, R.E.3
  • 25
    • 70349869344 scopus 로고    scopus 로고
    • Bacteraemia in Kenyan children with sickle-cell anaemia: A retrospective cohort and case-control study
    • Williams TN, Uyoga S, Macharia A, et al. Bacteraemia in Kenyan children with sickle-cell anaemia: a retrospective cohort and case-control study. Lancet 2009;374:1364-70.
    • (2009) Lancet , vol.374 , pp. 1364-1370
    • Williams, T.N.1    Uyoga, S.2    MacHaria, A.3
  • 26
    • 77956576772 scopus 로고    scopus 로고
    • High mortality from Plasmodium falciparum malaria in children living with sickle cell anemia on the coast of Kenya
    • McAuley CF, Webb C, Makani J, et al. High mortality from Plasmodium falciparum malaria in children living with sickle cell anemia on the coast of Kenya. Blood 2010;116:1663-8.
    • (2010) Blood , vol.116 , pp. 1663-1668
    • McAuley, C.F.1    Webb, C.2    Makani, J.3
  • 27
    • 84899982011 scopus 로고    scopus 로고
    • Verbal autopsy as a tool for identifying children dying of sickle cell disease: A validation study conducted in Kilifi district, Kenya
    • Ndila C, Bauni E, Nyirongo V, et al. Verbal autopsy as a tool for identifying children dying of sickle cell disease: a validation study conducted in Kilifi district, Kenya. BMC Med 2014;12:65.
    • (2014) BMC Med , vol.12 , pp. 65
    • Ndila, C.1    Bauni, E.2    Nyirongo, V.3
  • 28
    • 77949357012 scopus 로고    scopus 로고
    • Significant haemoglobinopathies: Guidelines for screening and diagnosis
    • Ryan K, Bain BJ, Worthington D, et al. Significant haemoglobinopathies: guidelines for screening and diagnosis. Br J Haematol 2010;149:35-49.
    • (2010) Br J Haematol , vol.149 , pp. 35-49
    • Ryan, K.1    Bain, B.J.2    Worthington, D.3
  • 30
    • 38549131853 scopus 로고    scopus 로고
    • Coagulation activation and inflammation in sickle cell disease-associated pulmonary hypertension
    • Ataga KI, Moore CG, Hillery CA, et al. Coagulation activation and inflammation in sickle cell disease-associated pulmonary hypertension. Haematologica 2008;93:20-6.
    • (2008) Haematologica , vol.93 , pp. 20-26
    • Ataga, K.I.1    Moore, C.G.2    Hillery, C.A.3
  • 31
    • 33644775612 scopus 로고    scopus 로고
    • Lactate dehydrogenase as a biomarker of hemolysis-associated nitric oxide resistance, priapism, leg ulceration, pulmonary hypertension, and death in patients with sickle cell disease
    • Kato GJ, McGowan V, Machado RF, et al. Lactate dehydrogenase as a biomarker of hemolysis-associated nitric oxide resistance, priapism, leg ulceration, pulmonary hypertension, and death in patients with sickle cell disease. Blood 2006;107:2279-85.
    • (2006) Blood , vol.107 , pp. 2279-2285
    • Kato, G.J.1    McGowan, V.2    MacHado, R.F.3
  • 32
    • 10744233940 scopus 로고    scopus 로고
    • Pulmonary hypertension as a risk factor for death in patients with sickle cell disease
    • Gladwin MT, Sachdev V, Jison ML, et al. Pulmonary hypertension as a risk factor for death in patients with sickle cell disease. N Engl J Med 2004;350:886-95.
    • (2004) N Engl J Med , vol.350 , pp. 886-895
    • Gladwin, M.T.1    Sachdev, V.2    Jison, M.L.3
  • 33
    • 33745699067 scopus 로고    scopus 로고
    • Cerebrovascular disease associated with sickle cell pulmonary hypertension
    • Kato GJ, Hsieh M, Machado R, et al. Cerebrovascular disease associated with sickle cell pulmonary hypertension. Am J Hematol 2006;81:503-10.
    • (2006) Am J Hematol , vol.81 , pp. 503-510
    • Kato, G.J.1    Hsieh, M.2    MacHado, R.3
  • 34
    • 84876284584 scopus 로고    scopus 로고
    • New insights into sickle cell disease: A disease of hypoxia
    • Sun K, Xia Y. New insights into sickle cell disease: a disease of hypoxia. Curr Opin Hematol 2013;20:215-21.
    • (2013) Curr Opin Hematol , vol.20 , pp. 215-221
    • Sun, K.1    Xia, Y.2
  • 35
    • 84868582399 scopus 로고    scopus 로고
    • Sickle cell pain: A critical reappraisal
    • Ballas SK, Gupta K, Adams-Graves P. Sickle cell pain: a critical reappraisal. Blood 2012;120:3647-56.
    • (2012) Blood , vol.120 , pp. 3647-3656
    • Ballas, S.K.1    Gupta, K.2    Adams-Graves, P.3
  • 36
    • 80053217106 scopus 로고    scopus 로고
    • Transient receptor potential vanilloid 1 mediates pain in mice with severe sickle cell disease
    • Hillery CA, Kerstein PC, Vilceanu D, et al. Transient receptor potential vanilloid 1 mediates pain in mice with severe sickle cell disease. Blood 2011;118:3376-83.
    • (2011) Blood , vol.118 , pp. 3376-3383
    • Hillery, C.A.1    Kerstein, P.C.2    Vilceanu, D.3
  • 37
    • 61449132474 scopus 로고    scopus 로고
    • Sickle cell disease in children: Differentiating osteomyelitis from vaso-occlusive crisis
    • Berger E, Saunders N, Wang L, et al. Sickle cell disease in children: differentiating osteomyelitis from vaso-occlusive crisis. Arch Pediatr Adolesc Med 2009;163: 251-5.
    • (2009) Arch Pediatr Adolesc Med , vol.163 , pp. 251-255
    • Berger, E.1    Saunders, N.2    Wang, L.3
  • 38
    • 20044374216 scopus 로고    scopus 로고
    • Bone involvement in sickle cell disease
    • Almeida A, Roberts I. Bone involvement in sickle cell disease. Br J Haematol 2005;129:482-90.
    • (2005) Br J Haematol , vol.129 , pp. 482-490
    • Almeida, A.1    Roberts, I.2
  • 39
    • 80051762413 scopus 로고    scopus 로고
    • Increased prevalence of osteonecrosis of the femoral head in children and adolescents with sickle-cell disease
    • Mahadeo KM, Oyeku S, Taragin B, et al. Increased prevalence of osteonecrosis of the femoral head in children and adolescents with sickle-cell disease. Am J Hematol 2011;86:806-8.
    • (2011) Am J Hematol , vol.86 , pp. 806-808
    • Mahadeo, K.M.1    Oyeku, S.2    Taragin, B.3
  • 40
    • 0026076686 scopus 로고
    • Sickle cell disease as a cause of osteonecrosis of the femoral head
    • Milner PF, Kraus AP, Sebes JI, et al. Sickle cell disease as a cause of osteonecrosis of the femoral head. N Engl J Med 1991;325:1476-81.
    • (1991) N Engl J Med , vol.325 , pp. 1476-1481
    • Milner, P.F.1    Kraus, A.P.2    Sebes, J.I.3
  • 41
    • 0035023308 scopus 로고    scopus 로고
    • Avascular necrosis of the hip in children with sickle cell disease and high Hb F: Magnetic resonance imaging findings and influence of alpha-thalassemia trait
    • Adekile AD, Gupta R, Yacoub F, et al. Avascular necrosis of the hip in children with sickle cell disease and high Hb F: magnetic resonance imaging findings and influence of alpha-thalassemia trait. Acta Haematol 2001;105:27-31.
    • (2001) Acta Haematol , vol.105 , pp. 27-31
    • Adekile, A.D.1    Gupta, R.2    Yacoub, F.3
  • 42
    • 0031933359 scopus 로고    scopus 로고
    • Etiology of osteomyelitis complicating sickle cell disease
    • Burnett MW, Bass JW, Cook BA. Etiology of osteomyelitis complicating sickle cell disease. Pediatrics 1998;101:296-7.
    • (1998) Pediatrics , vol.101 , pp. 296-297
    • Burnett, M.W.1    Bass, J.W.2    Cook, B.A.3
  • 43
    • 0033857950 scopus 로고    scopus 로고
    • Acute clinical events in 299 homozygous sickle cell patients living in France. French Study Group on Sickle Cell Disease
    • Neonato MG, Guilloud-Bataille M, Beauvais P, et al. Acute clinical events in 299 homozygous sickle cell patients living in France. French Study Group on Sickle Cell Disease. Eur J Haematol 2000;65:155-64.
    • (2000) Eur J Haematol , vol.65 , pp. 155-164
    • Neonato, M.G.1    Guilloud-Bataille, M.2    Beauvais, P.3
  • 44
    • 84861768705 scopus 로고    scopus 로고
    • Pulmonary complications of sickle cell disease
    • Miller AC, Gladwin MT. Pulmonary complications of sickle cell disease. Am J Respir Crit Care Med 2012;185:1154-65.
    • (2012) Am J Respir Crit Care Med , vol.185 , pp. 1154-1165
    • Miller, A.C.1    Gladwin, M.T.2
  • 45
    • 33747479576 scopus 로고    scopus 로고
    • Asthma is associated with acute chest syndrome and pain in children with sickle cell anemia
    • Boyd JH, Macklin EA, Strunk RC, et al. Asthma is associated with acute chest syndrome and pain in children with sickle cell anemia. Blood 2006;108:2923-7.
    • (2006) Blood , vol.108 , pp. 2923-2927
    • Boyd, J.H.1    MacKlin, E.A.2    Strunk, R.C.3
  • 46
    • 84879459386 scopus 로고    scopus 로고
    • Clinical correlates of acute pulmonary events in children and adolescents with sickle cell disease
    • Paul R, Minniti CP, Nouraie M, et al. Clinical correlates of acute pulmonary events in children and adolescents with sickle cell disease. Eur J Haematol 2013;91:62-8.
    • (2013) Eur J Haematol , vol.91 , pp. 62-68
    • Paul, R.1    Minniti, C.P.2    Nouraie, M.3
  • 47
    • 78650970723 scopus 로고    scopus 로고
    • Elevated tricuspid regurgitation velocity and decline in exercise capacity over 22 months of follow up in children and adolescents with sickle cell anemia
    • Gordeuk VR, Minniti CP, Nouraie M, et al. Elevated tricuspid regurgitation velocity and decline in exercise capacity over 22 months of follow up in children and adolescents with sickle cell anemia. Haematologica 2011;96:33-40.
    • (2011) Haematologica , vol.96 , pp. 33-40
    • Gordeuk, V.R.1    Minniti, C.P.2    Nouraie, M.3
  • 49
    • 34247182608 scopus 로고    scopus 로고
    • Hyposplenism: A comprehensive review. Part II: Clinical manifestations, diagnosis, and management
    • William BM, Thawani N, Sae-Tia S, et al. Hyposplenism: a comprehensive review. Part II: clinical manifestations, diagnosis, and management. Hematology 2007;12:89-98.
    • (2007) Hematology , vol.12 , pp. 89-98
    • William, B.M.1    Thawani, N.2    Sae-Tia, S.3
  • 50
  • 51
    • 74649086995 scopus 로고    scopus 로고
    • Infection in sickle cell disease: A review
    • Booth C, Inusa B, Obaro SK. Infection in sickle cell disease: a review. Int J Infect Dis 2010;14:e2-12.
    • (2010) Int J Infect Dis , vol.14 , pp. e2-12
    • Booth, C.1    Inusa, B.2    Obaro, S.K.3
  • 52
    • 85027918973 scopus 로고    scopus 로고
    • Epidemiology of Bloodstream Infections in Children with Sickle Cell Disease
    • Ellison AM, Ota KV, McGowan KL, et al. Epidemiology of Bloodstream Infections in Children with Sickle Cell Disease. Pediatr Infect Dis J 2013;32:560-3.
    • (2013) Pediatr Infect Dis J , vol.32 , pp. 560-563
    • Ellison, A.M.1    Ota, K.V.2    McGowan, K.L.3
  • 53
    • 0019830766 scopus 로고
    • Acute splenic sequestration and hypersplenism in the first five years in homozygous sickle cell disease
    • Topley JM, Rogers DW, Stevens MC, et al. Acute splenic sequestration and hypersplenism in the first five years in homozygous sickle cell disease. Arch Dis Child 1981;56:765-9.
    • (1981) Arch Dis Child , vol.56 , pp. 765-769
    • Topley, J.M.1    Rogers, D.W.2    Stevens, M.C.3
  • 54
    • 84903597894 scopus 로고    scopus 로고
    • The spleen and sickle cell disease: The sick(led) spleen
    • Brousse V, Buffet P, Rees D. The spleen and sickle cell disease: the sick(led) spleen. Br J Haematol 2014;166:165-76.
    • (2014) Br J Haematol , vol.166 , pp. 165-176
    • Brousse, V.1    Buffet, P.2    Rees, D.3
  • 55
    • 0021930572 scopus 로고
    • Acute splenic sequestration in homozygous sickle cell disease: Natural history and management
    • Emond AM, Collis R, Darvill D, et al. Acute splenic sequestration in homozygous sickle cell disease: natural history and management. J Pediatr 1985;107:201-6.
    • (1985) J Pediatr , vol.107 , pp. 201-206
    • Emond, A.M.1    Collis, R.2    Darvill, D.3
  • 56
    • 4544260562 scopus 로고    scopus 로고
    • Acute hepatic sequestration in sickle cell disease
    • Norris WE. Acute hepatic sequestration in sickle cell disease. J Natl Med Assoc 2004;96:1235-9.
    • (2004) J Natl Med Assoc , vol.96 , pp. 1235-1239
    • Norris, W.E.1
  • 57
    • 84899075176 scopus 로고    scopus 로고
    • How we treat sickle hepatopathy and liver transplantation in adults
    • Gardner K, Suddle A, Kane P, et al. How we treat sickle hepatopathy and liver transplantation in adults. Blood 2014;123:2302-7.
    • (2014) Blood , vol.123 , pp. 2302-2307
    • Gardner, K.1    Suddle, A.2    Kane, P.3
  • 58
    • 0031965089 scopus 로고    scopus 로고
    • Cerebrovascular accidents in sickle cell disease: Rates and risk factors
    • Ohene-Frempong K, Weiner SJ, Sleeper LA, et al. Cerebrovascular accidents in sickle cell disease: rates and risk factors. Blood 1998;91:288-94.
    • (1998) Blood , vol.91 , pp. 288-294
    • Ohene-Frempong, K.1    Weiner, S.J.2    Sleeper, L.A.3
  • 59
    • 81055147549 scopus 로고    scopus 로고
    • Cerebral infarction in children with sickle cell disease: A concise overview
    • Musallam KM, Khoury RA, Abboud MR. Cerebral infarction in children with sickle cell disease: a concise overview. Hemoglobin 2011;35:618-24.
    • (2011) Hemoglobin , vol.35 , pp. 618-624
    • Musallam, K.M.1    Khoury, R.A.2    Abboud, M.R.3
  • 60
    • 0032474692 scopus 로고    scopus 로고
    • Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography
    • Adams RJ, McKie VC, Hsu L, et al. Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography. N Engl J Med 1998;339:5-11.
    • (1998) N Engl J Med , vol.339 , pp. 5-11
    • Adams, R.J.1    McKie, V.C.2    Hsu, L.3
  • 61
    • 29544444495 scopus 로고    scopus 로고
    • Optimizing Primary Stroke Prevention in Sickle Cell Anemia Trial I. Discontinuing prophylactic transfusions used to prevent stroke in sickle cell disease
    • Adams RJ, Brambilla D, Optimizing Primary Stroke Prevention in Sickle Cell Anemia Trial I. Discontinuing prophylactic transfusions used to prevent stroke in sickle cell disease. N Engl J Med 2005;353:2769-78.
    • (2005) N Engl J Med , vol.353 , pp. 2769-2778
    • Adams, R.J.1    Brambilla, D.2
  • 62
    • 84860348352 scopus 로고    scopus 로고
    • Stroke with Transfusions Changing to Hydroxyurea (SWiTCH)
    • Ware RE, Helms RW, Investigators SW. Stroke With Transfusions Changing to Hydroxyurea (SWiTCH). Blood 2012;119:3925-32.
    • (2012) Blood , vol.119 , pp. 3925-3932
    • Ware, R.E.1    Helms, R.W.2
  • 63
    • 84907010836 scopus 로고    scopus 로고
    • Controlled trial of transfusions for silent cerebral infarcts in sickle cell anemia
    • DeBaun MR, Gordon M, McKinstry RC, et al. Controlled trial of transfusions for silent cerebral infarcts in sickle cell anemia. N Engl J Med 2014;371:699-710.
    • (2014) N Engl J Med , vol.371 , pp. 699-710
    • Debaun, M.R.1    Gordon, M.2    McKinstry, R.C.3
  • 64
    • 84861211196 scopus 로고    scopus 로고
    • Silent cerebral infarcts: A review on a prevalent and progressive cause of neurologic injury in sickle cell anemia
    • DeBaun MR, Armstrong FD, McKinstry RC, et al. Silent cerebral infarcts: a review on a prevalent and progressive cause of neurologic injury in sickle cell anemia. Blood 2012;119:4587-96.
    • (2012) Blood , vol.119 , pp. 4587-4596
    • Debaun, M.R.1    Armstrong, F.D.2    McKinstry, R.C.3
  • 65
    • 33645059719 scopus 로고    scopus 로고
    • Sickle cell 'girdle syndrome' progressing to ischaemic colitis and colonic perforation
    • Qureshi A, Lang N, Bevan DH. Sickle cell 'girdle syndrome' progressing to ischaemic colitis and colonic perforation. Clin Lab Haematol 2006;28:60-2.
    • (2006) Clin Lab Haematol , vol.28 , pp. 60-62
    • Qureshi, A.1    Lang, N.2    Bevan, D.H.3
  • 66
    • 84894066556 scopus 로고    scopus 로고
    • Priapism in children: A comprehensive review and clinical guideline
    • Donaldson JF, Rees RW, Steinbrecher HA. Priapism in children: a comprehensive review and clinical guideline. J Pediatr Urol 2014;10:11-24.
    • (2014) J Pediatr Urol , vol.10 , pp. 11-24
    • Donaldson, J.F.1    Rees, R.W.2    Steinbrecher, H.A.3
  • 67
    • 84903141313 scopus 로고    scopus 로고
    • Randomized controlled trial of sildenafil for preventing recurrent ischemic priapism in sickle cell disease
    • Burnett AL, Anele UA, Trueheart IN, et al. Randomized controlled trial of sildenafil for preventing recurrent ischemic priapism in sickle cell disease. Am J Med 2014;127:664-8.
    • (2014) Am J Med , vol.127 , pp. 664-668
    • Burnett, A.L.1    Anele, U.A.2    Trueheart, I.N.3
  • 69
    • 58349102500 scopus 로고    scopus 로고
    • Implementation of universal newborn bloodspot screening for sickle cell disease and other clinically significant haemoglobinopathies in England: Screening results for 2005-7
    • Streetly A, Latinovic R, Hall K, et al. Implementation of universal newborn bloodspot screening for sickle cell disease and other clinically significant haemoglobinopathies in England: screening results for 2005-7. J Clin Pathol 2009;62:26-30.
    • (2009) J Clin Pathol , vol.62 , pp. 26-30
    • Streetly, A.1    Latinovic, R.2    Hall, K.3
  • 71
    • 0029025475 scopus 로고
    • Effect of hydroxyurea on the frequency of painful crises in sickle cell anemia. Investigators of the Multicenter Study of Hydroxyurea in Sickle Cell Anemia
    • Charache S, Terrin ML, Moore RD, et al. Effect of hydroxyurea on the frequency of painful crises in sickle cell anemia. Investigators of the Multicenter Study of Hydroxyurea in Sickle Cell Anemia. N Engl J Med 1995;332:1317-22.
    • (1995) N Engl J Med , vol.332 , pp. 1317-1322
    • Charache, S.1    Terrin, M.L.2    Moore, R.D.3
  • 72
    • 13044277572 scopus 로고    scopus 로고
    • Safety of hydroxyurea in children with sickle cell anemia: Results of the HUG-KIDS study, a phase I/II trial
    • Kinney TR, Helms RW, O'Branski EE, et al. Safety of hydroxyurea in children with sickle cell anemia: results of the HUG-KIDS study, a phase I/II trial. Pediatric Hydroxyurea Group. Blood 1999;94:1550-4.
    • (1999) Pediatric Hydroxyurea Group. Blood , vol.94 , pp. 1550-1554
    • Kinney, T.R.1    Helms, R.W.2    O'Branski, E.E.3
  • 73
    • 79955909191 scopus 로고    scopus 로고
    • Hydroxycarbamide in very young children with sickle-cell anaemia: A multicentre, randomised, controlled trial (BABY HUG)
    • Wang WC, Ware RE, Miller ST, et al. Hydroxycarbamide in very young children with sickle-cell anaemia: a multicentre, randomised, controlled trial (BABY HUG). Lancet 2011;377:1663-72.
    • (2011) Lancet , vol.377 , pp. 1663-1672
    • Wang, W.C.1    Ware, R.E.2    Miller, S.T.3
  • 74
    • 77953057530 scopus 로고    scopus 로고
    • The risks and benefits of long-term use of hydroxyurea in sickle cell anemia: A 17.5 year follow-up
    • Steinberg MH, McCarthy WF, Castro O, et al. The risks and benefits of long-term use of hydroxyurea in sickle cell anemia: a 17.5 year follow-up. Am J Hematol 2010;85:403-8.
    • (2010) Am J Hematol , vol.85 , pp. 403-408
    • Steinberg, M.H.1    McCarthy, W.F.2    Castro, O.3
  • 75
    • 77955490414 scopus 로고    scopus 로고
    • Hydroxyurea in children with sickle cell disease: Practice patterns and barriers to utilization
    • Brandow AM, Jirovec DL, Panepinto JA. Hydroxyurea in children with sickle cell disease: practice patterns and barriers to utilization. Am J Hematol 2010;85:611-13.
    • (2010) Am J Hematol , vol.85 , pp. 611-613
    • Brandow, A.M.1    Jirovec, D.L.2    Panepinto, J.A.3
  • 76
    • 0034702282 scopus 로고    scopus 로고
    • Causes and outcomes of the acute chest syndrome in sickle cell disease. National Acute Chest Syndrome Study Group
    • Vichinsky EP, Neumayr LD, Earles AN, et al. Causes and outcomes of the acute chest syndrome in sickle cell disease. National Acute Chest Syndrome Study Group. N Engl J Med 2000;342:1855-65.
    • (2000) N Engl J Med , vol.342 , pp. 1855-1865
    • Vichinsky, E.P.1    Neumayr, L.D.2    Earles, A.N.3
  • 77
    • 0035659821 scopus 로고    scopus 로고
    • Impact of chronic transfusion on incidence of pain and acute chest syndrome during the Stroke Prevention Trial (STOP) in sickle-cell anemia
    • Miller ST, Wright E, Abboud M, et al. Impact of chronic transfusion on incidence of pain and acute chest syndrome during the Stroke Prevention Trial (STOP) in sickle-cell anemia. J Pediatr 2001;139:785-9.
    • (2001) J Pediatr , vol.139 , pp. 785-789
    • Miller, S.T.1    Wright, E.2    Abboud, M.3
  • 78
    • 84886292309 scopus 로고    scopus 로고
    • Pain and other non-neurological adverse events in children with sickle cell anemia and previous stroke who received hydroxyurea and phlebotomy or chronic transfusions and chelation: Results from the SWiTCH clinical trial
    • Alvarez O, Yovetich NA, Scott JP, et al. Pain and other non-neurological adverse events in children with sickle cell anemia and previous stroke who received hydroxyurea and phlebotomy or chronic transfusions and chelation: results from the SWiTCH clinical trial. Am J Hematol 2013;88:932-8.
    • (2013) Am J Hematol , vol.88 , pp. 932-938
    • Alvarez, O.1    Yovetich, N.A.2    Scott, J.P.3
  • 79
    • 84904522204 scopus 로고    scopus 로고
    • Transfusion therapy for sickle cell disease: A balancing act
    • Chou ST. Transfusion therapy for sickle cell disease: a balancing act. Hematol Am Soc Hematol Educ Program 2013;2013:439-46.
    • (2013) Hematol Am Soc Hematol Educ Program , vol.2013 , pp. 439-446
    • Chou, S.T.1
  • 80
    • 0034307369 scopus 로고    scopus 로고
    • Financial analysis of chronic transfusion for stroke prevention in sickle cell disease
    • Wayne AS, Schoenike SE, Pegelow CH. Financial analysis of chronic transfusion for stroke prevention in sickle cell disease. Blood 2000;96:2369-72.
    • (2000) Blood , vol.96 , pp. 2369-2372
    • Wayne, A.S.1    Schoenike, S.E.2    Pegelow, C.H.3
  • 81
    • 84885158071 scopus 로고    scopus 로고
    • Hydroxyurea is associated with lower costs of care of young children with sickle cell anemia
    • Wang WC, Oyeku SO, Luo Z, et al. Hydroxyurea is associated with lower costs of care of young children with sickle cell anemia. Pediatrics 2013;132:677-83.
    • (2013) Pediatrics , vol.132 , pp. 677-683
    • Wang, W.C.1    Oyeku, S.O.2    Luo, Z.3
  • 82
    • 84862268473 scopus 로고    scopus 로고
    • Allogeneic hematopoietic stem cell transplantation in children with sickle cell disease
    • Locatelli F, Pagliara D. Allogeneic hematopoietic stem cell transplantation in children with sickle cell disease. Pediatr Blood Cancer 2012;59:372-6.
    • (2012) Pediatr Blood Cancer , vol.59 , pp. 372-376
    • Locatelli, F.1    Pagliara, D.2
  • 83
    • 84876333389 scopus 로고    scopus 로고
    • Long-term outcome and evaluation of organ function in pediatric patients undergoing haploidentical and matched related hematopoietic cell transplantation for sickle cell disease
    • Dallas MH, Triplett B, Shook DR, et al. Long-term outcome and evaluation of organ function in pediatric patients undergoing haploidentical and matched related hematopoietic cell transplantation for sickle cell disease. Biol Blood Marrow Transplant 2013;19:820-30.
    • (2013) Biol Blood Marrow Transplant , vol.19 , pp. 820-830
    • Dallas, M.H.1    Triplett, B.2    Shook, D.R.3
  • 84
    • 84875155964 scopus 로고    scopus 로고
    • Gene therapy for hemoglobinopathies: Progress and challenges
    • Dong A, Rivella S, Breda L. Gene therapy for hemoglobinopathies: progress and challenges. Transl Res 2013;161:293-306.
    • (2013) Transl Res , vol.161 , pp. 293-306
    • Dong, A.1    Rivella, S.2    Breda, L.3
  • 85
    • 84896806692 scopus 로고    scopus 로고
    • Gene therapy for hemoglobinopathies: The state of the field and the future
    • Chandrakasan S, Malik P. Gene therapy for hemoglobinopathies: the state of the field and the future. Hematol Oncol Clin North Am 2014;28:199-216.
    • (2014) Hematol Oncol Clin North Am , vol.28 , pp. 199-216
    • Chandrakasan, S.1    Malik, P.2
  • 86
    • 84862243355 scopus 로고    scopus 로고
    • Future directions of sickle cell disease research: The NIH perspective
    • Hoots WK, Shurin SB. Future directions of sickle cell disease research: the NIH perspective. Pediatr Blood Cancer 2012;59:353-7.
    • (2012) Pediatr Blood Cancer , vol.59 , pp. 353-357
    • Hoots, W.K.1    Shurin, S.B.2


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.