Loss of raf-1 kinase inhibitory protein delays early-onset severe retinal ciliopathy in cep290rd16 mouse

Investigative Ophthalmology and Visual Science

Volumn 55, Issue 9, 2014, Pages 5788-5794

  Subramanian, Balajikarthick ^a   Anand, Manisha ^a   Khan, Naheed W ^b   Khanna, Hemant ^a  

^a UNIVERSITY OF MASSACHUSETTS MEDICAL SCHOOL   (United States)

^b UNIVERSITY OF MICHIGAN MEDICAL SCHOOL   (United States)

Author keywords

Blindness; CEP290; Photoreceptor degeneration; Retina; RKIP

Indexed keywords

PHOSPHATIDYLETHANOLAMINE BINDING PROTEIN; PROTEIN P18; RAF PROTEIN; CEP290 PROTEIN, MOUSE; NUCLEAR PROTEIN; OPSIN; PEBP1 PROTEIN, HUMAN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; BLINDNESS; CELL DEATH; CONTROLLED STUDY; ELECTRORETINOGRAPHY; GENE MUTATION; GENETIC DISORDER; IMMUNOBLOTTING; IMMUNOFLUORESCENCE MICROSCOPY; LEBER CONGENITAL AMAUROSIS; MOUSE; NICK END LABELING; NONHUMAN; PHENOTYPE; PHOTORECEPTOR CELL; POLYMERASE CHAIN REACTION; PROTEIN EXPRESSION; PROTEIN TRANSPORT; RETINA DEGENERATION; RETINAL CILIOPATHY; RETINOPATHY; TRANSMISSION ELECTRON MICROSCOPY; ANALYSIS OF VARIANCE; ANIMAL; CEP290; CILIARY BODY; DISEASE MODEL; KNOCKOUT MOUSE; METABOLISM; PATHOLOGY; PATHOPHYSIOLOGY; PHOTORECEPTOR DEGENERATION; PHYSIOLOGY; RETINA;

BLINDNESS; CEP290; PHOTORECEPTOR DEGENERATION; RETINA; RKIP;

ANALYSIS OF VARIANCE; ANIMALS; APOPTOSIS; CILIARY BODY; DISEASE MODELS, ANIMAL; ELECTRORETINOGRAPHY; MICE; MICE, KNOCKOUT; NUCLEAR PROTEINS; OPSINS; PHOSPHATIDYLETHANOLAMINE BINDING PROTEIN; PHOTORECEPTOR CELLS, VERTEBRATE; RETINAL DEGENERATION;

EID: 84908110239     PISSN: 01460404     EISSN: 15525783     Source Type: Journal    
DOI: 10.1167/iovs.14-14954     Document Type: Article

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