The role of bronchial epithelial cells in the pathogenesis of COPD in Z-alpha-1 antitrypsin deficiency

Respiratory Research

Volumn 15, Issue 1, 2014, Pages 1-10

  Pini, Laura ^a   Tiberio, Laura ^a   Venkatesan, Narayanan ^b   Bezzi, Michela ^c   Corda, Luciano ^c   Luisetti, Maurizio ^d   Ferrarotti, Ilaria ^d   Malerba, Mario ^c   Lomas, David A ^e   Janciauskiene, Sabina ^f   Vizzardi, Enrico ^a   Modina, Denise ^a   Schiaffonati, Luisa ^a   Tantucci, Claudio ^a  

^a UNIVERSITY OF BRESCIA   (Italy)

^b MCGILL UNIVERSITY   (Canada)

^c SPEDALI CIVILI   (Italy)

^d UNIVERSITY OF PAVIA   (Italy)

^e UNIVERSITY COLLEGE LONDON   (United Kingdom)

^f HANNOVER MEDICAL SCHOOL   (Germany)

Author keywords

Bronchial epithelial cell dysfunction; Bronchial epithelial cells; Pathogenesis of COPD; Z AAT polymers

Indexed keywords

ALPHA 1 ANTITRYPSIN; ANTIBODY; ARANIDIPINE; M ALPHA 1 ANTITRYPSIN; ONCOSTATIN M; POLYMER; PROTEIN VARIANT; UNCLASSIFIED DRUG; Z ALPHA 1 ANTITRYPSIN; Z ALPHA 1 ANTITRYPSIN POLYMER;

ADULT; ALPHA 1 ANTITRYPSIN DEFICIENCY; ARTICLE; BIOACCUMULATION; BRONCHIAL EPITHELIAL CELL; BRONCHUS BIOPSY; BRONCHUS MUCOSA; CELL CULTURE; CELL STIMULATION; CELLULAR SECRETION; CHRONIC OBSTRUCTIVE LUNG DISEASE; CLINICAL ARTICLE; COMPARATIVE STUDY; CONTROLLED STUDY; CULTURE MEDIUM; EPITHELIUM CELL; EX VIVO STUDY; FEMALE; GENE EXPRESSION; GENETIC TRANSFECTION; HOMOZYGOTE; HUMAN; HUMAN TISSUE; MALE; PATHOGENESIS; PROTEIN SECRETION; SUBMUCOSA; Z ALPHA 1 ANTITRYPSIN DEFICIENCY;

EID: 84908087357     PISSN: 14659921     EISSN: 1465993X     Source Type: Journal    
DOI: 10.1186/s12931-014-0112-3     Document Type: Article

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