Extracellular matrix defects in aneurysmal Fibulin-4 mice predispose to lung emphysema

PLoS ONE

Volumn 9, Issue 9, 2014, Pages

  Ramnath, Natasja W M ^a   Van De Luijtgaarden, Koen M ^a   Van Der Pluijm, Ingrid ^a   Van Nimwegen, Menno ^a   Van Heijningen, Paula M ^a   Swagemakers, Sigrid M A ^a   Van Thiel, Bibi S ^a   Ridwan, Ruziedi Y ^a   Van Vliet, Nicole ^a   Vermeij, Marcel ^a   Hawinkels, Luuk J A C ^b   De Munck, Anne ^a   Dzyubachyk, Oleh ^a,c   Meijering, Erik ^a   Van Der Spek, Peter ^a   Rottier, Robbert ^a   Yanagisawa, Hiromi ^d   Hendriks, Rudi W ^a   Kanaar, Roland ^a   Rouwet, Ellen V ^a   Kleinjan, Alex ^a   Essers, Jeroen ^a   more..

^a ERASMUS MEDICAL CENTER   (Netherlands)

^b Centre for Biomedical Genetics   (Netherlands)

^c LEIDEN UNIVERSITY MEDICAL CENTER   (Netherlands)

^d UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

FIBULIN; FIBULIN 4; TRANSCRIPTOME; UNCLASSIFIED DRUG; ALPHA 1 ANTITRYPSIN; FIBULIN-4; LIPOPOLYSACCHARIDE; MATRIX METALLOPROTEINASE; PANCREATIC ELASTASE; SCLEROPROTEIN; SERPINA1 PROTEIN, HUMAN; TRANSFORMING GROWTH FACTOR BETA;

AGED; ANIMAL EXPERIMENT; ANIMAL MODEL; AORTA ANEURYSM; ARTICLE; CHRONIC OBSTRUCTIVE LUNG DISEASE; COHORT ANALYSIS; CONTROLLED STUDY; DISEASE ASSOCIATION; DISEASE PREDISPOSITION; EXTRACELLULAR MATRIX; FEMALE; GENE EXPRESSION; GENETIC SUSCEPTIBILITY; HUMAN; INFLAMMATION; LUNG EMPHYSEMA; MAJOR CLINICAL STUDY; MALE; MOLECULAR IMAGING; MOUSE; NONHUMAN; PERIPHERAL OCCLUSIVE ARTERY DISEASE; PREVALENCE; RISK FACTOR; SMOKING; VASCULAR DISEASE; ANIMAL; AORTA; COMPLICATION; DEFICIENCY; DOWN REGULATION; DRUG EFFECTS; ENZYMOLOGY; IMMUNOLOGY; LUNG; LUNG ALVEOLUS; METABOLISM; NEUTROPHIL; PATHOLOGY; SIGNAL TRANSDUCTION;

MUS;

AGED; ALPHA 1-ANTITRYPSIN; ANIMALS; AORTA; AORTIC ANEURYSM; COHORT STUDIES; DISEASE SUSCEPTIBILITY; DOWN-REGULATION; EXTRACELLULAR MATRIX; EXTRACELLULAR MATRIX PROTEINS; FEMALE; HUMANS; LIPOPOLYSACCHARIDES; LUNG; MALE; MATRIX METALLOPROTEINASES; MICE; NEUTROPHILS; PANCREATIC ELASTASE; PULMONARY ALVEOLI; PULMONARY EMPHYSEMA; SIGNAL TRANSDUCTION; TRANSFORMING GROWTH FACTOR BETA;

EID: 84907909005     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0106054     Document Type: Article

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