p53 suppression partially rescues the mutant phenotype in mouse models of DiGeorge syndrome

Proceedings of the National Academy of Sciences of the United States of America

Volumn 111, Issue 37, 2014, Pages 13385-13390

  Caprio, Cinzia ^a,b   Baldini, Antonio ^b,c  

^a PhD Program   (Italy)

^b INSTITUTE OF GENETICS AND BIOPHYSICS ADRIANO BUZZATI TRAVERSO   (Italy)

^c UNIVERSITY OF NAPLES FEDERICO II   (Italy)

Author keywords

Pharyngeal arch artery development; Tbx1 and second heart field

Indexed keywords

BENZOTHIAZOLE DERIVATIVE; CHROMATIN; GBX2 PROTEIN, MOUSE; HOMEODOMAIN PROTEIN; PIFITHRIN; PROTEIN BINDING; PROTEIN P53; T BOX TRANSCRIPTION FACTOR; TBX1 PROTEIN, MOUSE; TOLUENE;

ANALOGS AND DERIVATIVES; ANIMAL; ANIMAL EMBRYO; ARTERY; BRANCHIAL ARCH; CHROMATIN; CONGENITAL MALFORMATION; CROSS BREEDING; DIGEORGE SYNDROME; DISEASE MODEL; DOWN REGULATION; DRUG EFFECTS; EMBRYOLOGY; EPISTASIS; FEMALE; GENE DELETION; GENE EXPRESSION REGULATION; GENETICS; MALE; METABOLISM; MOUSE; MUTANT MOUSE STRAIN; MUTATION; PATHOLOGY; PHENOTYPE;

ANIMALS; ARTERIES; BENZOTHIAZOLES; BRANCHIAL REGION; CHROMATIN; CROSSES, GENETIC; DIGEORGE SYNDROME; DISEASE MODELS, ANIMAL; DOWN-REGULATION; EMBRYO, MAMMALIAN; EPISTASIS, GENETIC; FEMALE; GENE DELETION; GENE EXPRESSION REGULATION, DEVELOPMENTAL; HOMEODOMAIN PROTEINS; MALE; MICE; MICE, MUTANT STRAINS; MUTATION; PHENOTYPE; PROTEIN BINDING; T-BOX DOMAIN PROTEINS; TOLUENE; TUMOR SUPPRESSOR PROTEIN P53;

EID: 84907202751     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.1401923111     Document Type: Article

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