Multimerization of glycosylphosphatidylinositol-anchored high density lipoprotein-binding protein 1 (GPIHBP1) and familial chylomicronemia from a serine-to-cysteine substitution in GPIHBP1 Ly6 domain

Journal of Biological Chemistry

Volumn 289, Issue 28, 2014, Pages 19491-19499

  Plengpanich, Wanee ^a   Young, Stephen G ^b,c   Khovidhunkit, Weerapan ^a   Bensadoun, André ^d   Karnman, Hirankorn ^a   Ploug, Michael ^e   Gårdsvoll, Henrik ^e   Leung, Calvin S ^b   Adeyo, Oludotun ^b   Larsson, Mikael ^f   Muanpetch, Suwanna ^a   Charoen, Supannika ^a   Fong, Loren G ^b   Niramitmahapanya, Sathit ^g   Beigneux, Anne P ^b  

^a CHULALONGKORN UNIVERSITY   (Thailand)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c UNIVERSITY OF CALIFORNIA   (United States)

^d Division of Nutritional Science Cornell University ^*  (United States)

^e University of Copenhagen   (Denmark)

^f UMEÅ UNIVERSITY   (Sweden)

^g RANGSIT UNIVERSITY   (Thailand)

Author keywords

[No Author keywords available]

Indexed keywords

CELL MEMBRANES; COVALENT BONDS; DIMERS; ENDOTHELIAL CELLS; LIPOPROTEINS;

DISULFIDE BOND FORMATION; EXPRESSION SYSTEM; HYPERTRIGLYCERIDEMIA; INTERSTITIAL SPACE; LIPOPROTEIN LIPASE; MICROVASCULAR ENDOTHELIAL CELLS; MULTIMERIZATION; POINT MUTATIONS;

AMINO ACIDS;

GLYCOSYLPHOSPHATIDYLINOSITOL ANCHORED HIGH DENSITY LIPOPROTEIN BINDING PROTEIN 1; GLYCOSYLPHOSPHATIDYLINOSITOL ANCHORED PROTEIN; LIPOPROTEIN LIPASE; POLYMER; UNCLASSIFIED DRUG;

ADULT; AGED; AMINO ACID SUBSTITUTION; ANIMAL CELL; ARTICLE; CELL SURFACE; CONTROLLED STUDY; FEMALE; HUMAN; HYPERLIPOPROTEINEMIA TYPE 1; HYPERTRIGLYCERIDEMIA; MAJOR CLINICAL STUDY; MALE; MIDDLE AGED; MISSENSE MUTATION; NONHUMAN; PEDIGREE ANALYSIS; POINT MUTATION; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN DOMAIN; PROTEIN EXPRESSION; PROTEIN MULTIMERIZATION; PROTEIN TRANSPORT; VERY ELDERLY; WILD TYPE; YOUNG ADULT;

DISULFIDE; GENETICS; HYPERTRIGLYCERIDEMIA; LIPOLYSIS; LIPOPROTEIN LIPASE; MUTATION; PROTEIN FOLDING; PROTEIN-PROTEIN INTERACTION;

ADULT; AMINO ACID SUBSTITUTION; CELL LINE; HOMOZYGOTE; HUMANS; HYPERLIPOPROTEINEMIA TYPE I; LIPOPROTEIN LIPASE; MALE; MUTATION, MISSENSE; PROTEIN BINDING; PROTEIN MULTIMERIZATION; PROTEIN STRUCTURE, TERTIARY; PROTEIN TRANSPORT; RECEPTORS, LIPOPROTEIN;

EID: 84904184110     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M114.558528     Document Type: Article

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